{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,12,30]],"date-time":"2025-12-30T23:16:22Z","timestamp":1767136582288,"version":"build-2238731810"},"update-to":[{"DOI":"10.1002\/14651858.cd013610","type":"new_version","label":"New version","source":"publisher","updated":{"date-parts":[[2023,7,18]],"date-time":"2023-07-18T00:00:00Z","timestamp":1689638400000}}],"reference-count":100,"publisher":"Wiley","issue":"7","content-domain":{"domain":["wiley.com","cochranelibrary.com"],"crossmark-restriction":true},"short-container-title":[],"DOI":"10.1002\/14651858.cd013610.pub2","type":"journal-article","created":{"date-parts":[[2023,7,18]],"date-time":"2023-07-18T07:50:40Z","timestamp":1689666640000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":5,"title":["Interventions for improving adherence to airway clearance treatment and exercise in people with cystic fibrosis"],"prefix":"10.1002","volume":"2023","author":[{"given":"Mandy","family":"Jones","sequence":"additional","affiliation":[{"name":"c\/o Cochrane Cystic Fibrosis; University of Nottingham; Nottingham UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Fiona","family":"Moffatt","sequence":"additional","affiliation":[{"name":"School of Health Sciences; University of Nottingham; Nottingham UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Alex","family":"Harvey","sequence":"additional","affiliation":[{"name":"School of Health Sciences and Social Care; Brunel University London; Uxbridge UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jennifer M","family":"Ryan","sequence":"additional","affiliation":[{"name":"Institute of Environment, Health and Societies; Brunel University London; Uxbridge UK"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2023,7,18]]},"reference":[{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0001|cit1","doi-asserted-by":"crossref","first-page":"81","DOI":"10.4187\/respcare.02578","article-title":"Effects of an educational intervention of physical activity for children and adolescents with cystic fibrosis: a randomized controlled trial","volume":"60","author":"Hommerding","year":"2015","journal-title":"Respiratory Care"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0002|cit2","doi-asserted-by":"crossref","first-page":"S36","DOI":"10.1016\/S1569-1993(12)60114-3","article-title":"Efficacy of an educational intervention of physical activity for children and adolescents with cystic fibrosis","volume":"11 Suppl 1","author":"Marostica","year":"2012","journal-title":"Journal of Cystic Fibrosis"},{"issue":"3","key":"10.1002\/14651858.CD013610.pub2-BIB0003|cit3","doi-asserted-by":"crossref","first-page":"710","DOI":"10.1016\/j.jpeds.2014.12.001","article-title":"Physical exercise recommendations improve postural changes found in children and adolescents with cystic fibrosis: a randomized controlled trial","volume":"166","author":"Schindel","year":"2015","journal-title":"Journal of Pediatrics"},{"issue":"Suppl 62","key":"10.1002\/14651858.CD013610.pub2-BIB0004|cit4","first-page":"PA4626","article-title":"A music therapy intervention as an adjunct to chest physiotherapy in children with cystic fibrosis","volume":"52","author":"Frias","year":"2018","journal-title":"European Respiratory Journal"},{"issue":"10","key":"10.1002\/14651858.CD013610.pub2-BIB0005|cit5","doi-asserted-by":"crossref","first-page":"e0241334","DOI":"10.1371\/journal.pone.0241334","article-title":"Effects of music therapy as an adjunct to chest physiotherapy in children with cystic fibrosis: a randomized controlled trial","volume":"15","author":"Montero-Ruiz","year":"2020","journal-title":"PloS One"},{"issue":"4","key":"10.1002\/14651858.CD013610.pub2-BIB0006|cit6","doi-asserted-by":"crossref","first-page":"337","DOI":"10.1177\/0009922809348022","article-title":"A breath biofeedback computer game for children with cystic fibrosis","volume":"49","author":"Bingham","year":"2010","journal-title":"Clinical Pediatrics"},{"issue":"8","key":"10.1002\/14651858.CD013610.pub2-BIB0007|cit7","doi-asserted-by":"crossref","first-page":"1278","DOI":"10.4187\/respcare.01263","article-title":"Pilot trial of spirometer games for airway clearance practice in cystic fibrosis","volume":"57","author":"Bingham","year":"2012","journal-title":"Respiratory Care"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0008|cit8","unstructured":"Video game exercise effectiveness of a domiciliary pulmonary rehabilitation program in cystic fibrosis patients clinicaltrials.gov\/show\/NCT02552043"},{"issue":"2","key":"10.1002\/14651858.CD013610.pub2-BIB0009|cit9","doi-asserted-by":"crossref","first-page":"87","DOI":"10.1159\/000481264","article-title":"Effectiveness of a home-based active game programme in young cystic fibrosis patients","volume":"95","author":"Corral","year":"2018","journal-title":"Respiration"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0010|cit10","doi-asserted-by":"crossref","first-page":"S28","DOI":"10.1016\/S1569-1993(17)30249-7","article-title":"Effectiveness of a psychomotor intervention in a group of paediatric patients with cystic fibrosis hospitalized for pulmonary exacerbation: a randomized controlled study","volume":"16 Suppl 1","author":"De Marchis","year":"2017","journal-title":"Journal of Cystic Fibrosis"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0011|cit11","first-page":"21","article-title":"Steps Ahead: optimising physical activity in adults with cystic fibrosis: study Protocol for a pilot randomised trial using wearable technology, goal setting and text message feedback","volume":"3","author":"Curran","year":"2020","journal-title":"HRB Open Research"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0012|cit12","unstructured":"Steps Ahead: optimising physical activity and health in adults with cystic fibrosis clinicaltrials.gov\/show\/NCT03672058"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0013|cit13","unstructured":"CyFiT Telerehabilitation: technology based physiotherapy for peer driven participation in therapy, and quality of life trialsearch.who.int\/Trial2.aspx?TrialID=ACTRN12617001035314"},{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0014|cit14","doi-asserted-by":"crossref","first-page":"21","DOI":"10.1186\/s12890-019-0784-z","article-title":"CyFiT telehealth: protocol for a randomised controlled trial of an online outpatient physiotherapy service for children with cystic fibrosis","volume":"19","author":"Lang","year":"2019","journal-title":"BMC Pulmonary Medicine"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0015|cit15","unstructured":"ActivOnline: physical Activity in Cystic Fibrosis Trial UK clinicaltrials.gov\/show\/NCT04249999"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0016|cit16","unstructured":"Feasibility of home-based exercise program for adults with cystic fibrosis clinicaltrials.gov\/show\/NCT05239611"},{"issue":"2","key":"10.1002\/14651858.CD013610.pub2-BIB0017|cit17","doi-asserted-by":"crossref","first-page":"115","DOI":"10.1136\/thx.49.2.115","article-title":"Treatment compliance in adults with cystic fibrosis","volume":"49","author":"Abbott","year":"1994","journal-title":"Thorax"},{"issue":"4","key":"10.1002\/14651858.CD013610.pub2-BIB0018|cit18","doi-asserted-by":"crossref","first-page":"389","DOI":"10.1093\/aje\/kwi054","article-title":"The effect of social desirability and social approval on self-reports of physical activity","volume":"161","author":"Adams","year":"2005","journal-title":"American Journal of Epidemiology"},{"issue":"5","key":"10.1002\/14651858.CD013610.pub2-BIB0019|cit19","doi-asserted-by":"crossref","first-page":"359","DOI":"10.1016\/j.jcf.2008.01.003","article-title":"Treatment compliance in children and adults with cystic fibrosis","volume":"7","author":"Aria Llorente","year":"2008","journal-title":"Journal of Cystic Fibrosis"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0020|cit20","doi-asserted-by":"crossref","first-page":"326","DOI":"10.1136\/bjsports-2017-098742","article-title":"Defining adherence to therapeutic exercise for musculoskeletal pain: a systematic review","volume":"54","author":"Bailey","year":"2018","journal-title":"British Journal of Sports Medicine"},{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0021|cit21","doi-asserted-by":"crossref","first-page":"8","DOI":"10.1002\/ppul.10397","article-title":"Increasing adherence to cystic fibrosis treatment; a systematic review of behavioural techniques","volume":"37","author":"Bernard","year":"2004","journal-title":"Pediatric Pulmonology"},{"issue":"8","key":"10.1002\/14651858.CD013610.pub2-BIB0022|cit22","doi-asserted-by":"crossref","first-page":"1278","DOI":"10.4187\/respcare.01263","article-title":"Pilot study of spirometer games for airway clearance practice in cystic fibrosis","volume":"57","author":"Bingham","year":"2012","journal-title":"Respiratory Care"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0023|cit23","doi-asserted-by":"crossref","first-page":"117","DOI":"10.2147\/AHMT.S95637","article-title":"Strategies to optimise treatment adherence in adolescent patients with cystic fibrosis","volume":"7","author":"Bishay","year":"2016","journal-title":"Adolescent Health, Medicine and Therapeutics"},{"issue":"Supp 1","key":"10.1002\/14651858.CD013610.pub2-BIB0024|cit24","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1136\/thx.2008.110726","article-title":"Guidelines for the physiotherapy management of the adult, medical, spontaneously breathing patient","volume":"64","author":"Bott","year":"2009","journal-title":"Thorax"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0025|cit25","doi-asserted-by":"publisher","first-page":"507","DOI":"10.2147\/PPA.S25308","article-title":"Barriers to adherence in adolescents and young adults with CF: a questionnaire study in young patients and their parents","volume":"5","author":"Bregnballe","year":"2011","journal-title":"Patient Preference and Adherence"},{"issue":"2","key":"10.1002\/14651858.CD013610.pub2-BIB0026|cit26","doi-asserted-by":"crossref","first-page":"165","DOI":"10.1002\/ppul.10436","article-title":"Differences between adolescents' and parents' reports of health-related quality of life in cystic fibrosis","volume":"37","author":"Britto","year":"2004","journal-title":"Pediatric Pulmonology"},{"issue":"12","key":"10.1002\/14651858.CD013610.pub2-BIB0027|cit27","doi-asserted-by":"publisher","DOI":"10.1002\/14651858.CD009595.pub3","article-title":"Autogenic drainage for airway clearance in cystic fibrosis","author":"Burnham","year":"2021","journal-title":"Cochrane Database of Systematic Reviews"},{"issue":"4","key":"10.1002\/14651858.CD013610.pub2-BIB0028|cit28","doi-asserted-by":"crossref","first-page":"656","DOI":"10.1111\/resp.12764","article-title":"Physiotherapy for cystic fibrosis in Australia and New Zealand: a clinical practice guideline","volume":"21","author":"Button","year":"2016","journal-title":"Respirology"},{"issue":"2","key":"10.1002\/14651858.CD013610.pub2-BIB0029|cit29","first-page":"126","article-title":"Physical activity, exercise, and physical fitness: definitions and distinctions for health-related research","volume":"100","author":"Caspersen","year":"1985","journal-title":"Public Health Reports"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0030|cit30","unstructured":"Standards of Care and Good Clinical Practice for the Physiotherapy Management of Cystic Fibrosis (4th Edition) Available from www.cysticfibrosis.org.uk\/the-work-we-do\/resources-for-cf-professionals\/consensus-documents 2020"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0031|cit31","unstructured":"UK Cystic Fibrosis Registry Annual Data Report www.cysticfibrosis.org.uk\/sites\/default\/files\/2022-10\/CFT_2021-Annual-Data-Report-WEB.pdf 2022"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0032|cit32","unstructured":"Cystic Fibrosis Foundation Highlights of the 2014 patient registry data Available at www.cff.org\/Research\/Researcher-Resources\/Patient-Registry\/Highlights-of-the-2014-Patient-Registry-Data\/ 2014"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0033|cit33","unstructured":"CF Foundation 2020 Annual report www.cff.org\/About-Us\/Assets\/2020-Annual-Report.pdf 2021"},{"issue":"6","key":"10.1002\/14651858.CD013610.pub2-BIB0034|cit34","doi-asserted-by":"crossref","first-page":"316","DOI":"10.5603\/ARM.2016.0041","article-title":"Contemporary national trends of cystic fibrosis hospitalizations and co-morbidities in the United States","volume":"84","author":"Chatterjee","year":"2016","journal-title":"Advances in Respiratory Medicine"},{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0035|cit35","doi-asserted-by":"crossref","first-page":"29","DOI":"10.1136\/thx.51.1.29","article-title":"Compliance with treatment in adult patients with cystic fibrosis","volume":"51","author":"Conway","year":"1996","journal-title":"Thorax"},{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0036|cit36","doi-asserted-by":"publisher","first-page":"e016982","DOI":"10.1136\/bmjopen-2017-016982","article-title":"Economic impact of medication non-adherence by disease groups: a systematic review","volume":"8","author":"Cutler","year":"2018","journal-title":"BMJ Open"},{"issue":"4","key":"10.1002\/14651858.CD013610.pub2-BIB0037|cit37","doi-asserted-by":"publisher","DOI":"10.1002\/14651858.CD007639.pub2","article-title":"Nebuliser systems for drug delivery in cystic fibrosis","author":"Daniels","year":"2013","journal-title":"Cochrane Database of Systematic Reviews"},{"issue":"3","key":"10.1002\/14651858.CD013610.pub2-BIB0038|cit38","doi-asserted-by":"crossref","first-page":"499","DOI":"10.1016\/j.jcf.2019.10.025","article-title":"Characterising burden of treatment in cystic fibrosis to identify priority areas for clinical trials","volume":"19","author":"Davies","year":"2020","journal-title":"Journal of Cystic Fibrosis"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0039|cit39","unstructured":"Deeks JJ Higgins JPT Altman DG Chapter 10: Analysing data and undertaking meta-analyses. In: Higgins JP, Thomas J, Chandler J, Cumpston M, Li T, Page MJ, Welch VA, editor(s). Cochrane Handbook for Systematic Reviews of Interventions version 6.3 (updated February 2022). Cochrane, 2022 Available from www.training.cochrane.org\/handbook"},{"issue":"11","key":"10.1002\/14651858.CD013610.pub2-BIB0040|cit40","doi-asserted-by":"crossref","first-page":"2063","DOI":"10.1093\/ptj\/pzaa136","article-title":"Development and validation of the AdT-Physio Scale: a tool to assess adherence and perception of physical therapist intervention in patients with cystic fibrosis","volume":"100","author":"Corral","year":"2020","journal-title":"Physical Therapy"},{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0041|cit41","doi-asserted-by":"crossref","first-page":"99","DOI":"10.1164\/rccm.200409-1244OC","article-title":"The effect of infective exacerbations on sleep and neurobehavioral function in cystic fibrosis","volume":"170","author":"Dobbin","year":"2005","journal-title":"American Journal of Respiratory and Critical Care Medicine"},{"issue":"Suppl 38","key":"10.1002\/14651858.CD013610.pub2-BIB0042|cit42","first-page":"2","article-title":"Understanding non-compliance with treatment in adults with cystic fibrosis","volume":"93","author":"Dodd","year":"2000","journal-title":"Journal of the Royal Society of Medicine"},{"issue":"3","key":"10.1002\/14651858.CD013610.pub2-BIB0043|cit43","doi-asserted-by":"crossref","first-page":"211","DOI":"10.1002\/ppul.21103","article-title":"Motivational interviewing for adherence problems in cystic fibrosis","volume":"45","author":"Duff","year":"2010","journal-title":"Pediatric Pulmonology"},{"issue":"4","key":"10.1002\/14651858.CD013610.pub2-BIB0044|cit44","doi-asserted-by":"crossref","first-page":"258","DOI":"10.1016\/j.jcf.2011.03.005","article-title":"Longitudinal association between medication adherence and lung health in people with cystic fibrosis","volume":"10","author":"Eakin","year":"2011","journal-title":"Journal of Cystic Fibrosis"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0045|cit45","doi-asserted-by":"publisher","first-page":"629","DOI":"10.1136\/bmj.315.7109.629","article-title":"Bias in meta-analysis detected by a simple, graphical test","volume":"315","author":"Egger","year":"1997","journal-title":"BMJ"},{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0046|cit46","doi-asserted-by":"crossref","first-page":"99","DOI":"10.1002\/1097-4679(199201)48:1<99::AID-JCLP2270480114>3.0.CO;2-5","article-title":"Psychological factors related to perceived compliance with cystic fibrosis treatment","volume":"48","author":"Geiss","year":"1992","journal-title":"Journal of Clinical Psychology"},{"issue":"6","key":"10.1002\/14651858.CD013610.pub2-BIB0047|cit47","doi-asserted-by":"crossref","first-page":"425","DOI":"10.1016\/j.jcf.2010.08.016","article-title":"Perceptions of barriers and facilitators: self-management decisions by older adolescents and adults with CF","volume":"9","author":"George","year":"2010","journal-title":"Journal of Cystic Fibrosis"},{"issue":"6","key":"10.1002\/14651858.CD013610.pub2-BIB0048|cit48","doi-asserted-by":"publisher","DOI":"10.1002\/14651858.CD003148.pub3","article-title":"Psychological interventions for individuals with cystic fibrosis and their families","author":"Goldbeck","year":"2014","journal-title":"Cochrane Database of Systematic Reviews"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0049|cit49","doi-asserted-by":"publisher","first-page":"43","DOI":"10.1186\/s12890-015-0038-7","article-title":"Adherence to treatment in children and adolescents with cystic fibrosis: a cross-sectional, multi-method study investigating the influence of beliefs about treatment and parental depressive symptoms","volume":"15","author":"Goodfellow","year":"2015","journal-title":"BMC Pulmonary Medicine"},{"issue":"6","key":"10.1002\/14651858.CD013610.pub2-BIB0050|cit50","doi-asserted-by":"publisher","DOI":"10.1002\/14651858.CD013285.pub2","article-title":"Exercise versus airway clearance techniques for people with cystic fibrosis","author":"Heinz","year":"2022","journal-title":"Cochrane Database of Systematic Reviews"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0051|cit51","unstructured":"Higgins JP Altman DG Sterne JA Chapter 8: Assessing risk of bias in included studies. In: Higgins JP, Churchill R, Chandler J, Cumpston MS, editor(s), Cochrane Handbook for Systematic Reviews of Interventions version 5.2.0 (updated June 2017). The Cochrane Collaboration, 2017 Available from training.cochrane.org\/handbook\/archive\/v5.2"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0052|cit52","doi-asserted-by":"crossref","first-page":"S30","DOI":"10.1016\/S1569-1993(14)60093-X","article-title":"Feasibility study to objectively measure airway clearance technique in cystic fibrosis","volume":"13 (Suppl 2)","author":"Hoo","year":"2014","journal-title":"Journal of Cystic Fibrosis"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0053|cit53","doi-asserted-by":"publisher","first-page":"113","DOI":"10.1186\/s12890-021-01482-x","article-title":"Factors influencing physical activity in adults with cystic fibrosis","volume":"1","author":"Hurley","year":"2021","journal-title":"BMC Pulmonary Medicine"},{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0054|cit54","doi-asserted-by":"crossref","first-page":"39","DOI":"10.52964\/AMJA.0543","article-title":"Haemoptysis: diagnosis and treatment","volume":"11","author":"Hurt","year":"2012","journal-title":"Acute Medicine"},{"issue":"7","key":"10.1002\/14651858.CD013610.pub2-BIB0055|cit55","doi-asserted-by":"crossref","first-page":"e18465","DOI":"10.2196\/18465","article-title":"Development and preliminary evaluation of the effects of an mhealth web-based platform (HappyAir) on adherence to a maintenance program after pulmonary rehabilitation in patients with chronic obstructive pulmonary disease: randomized controlled trial","volume":"8","author":"Jim\u00e9nez-Reguera","year":"2020","journal-title":"JMIR mHealth and uHealth"},{"issue":"2","key":"10.1002\/14651858.CD013610.pub2-BIB0056|cit56","doi-asserted-by":"crossref","first-page":"213","DOI":"10.1016\/j.jcf.2017.11.014","article-title":"A guide to interpreting estimated median age of survival in cystic fibrosis patient registry reports","volume":"17","author":"Keogh","year":"2018","journal-title":"Journal of Cystic Fibrosis"},{"issue":"4","key":"10.1002\/14651858.CD013610.pub2-BIB0057|cit57","doi-asserted-by":"crossref","first-page":"1299","DOI":"10.1378\/chest.125.4.1299","article-title":"Effects of aerobic training in children with cystic fibrosis","volume":"125","author":"Klijn","year":"2004","journal-title":"Chest"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0058|cit58","unstructured":"Lefebvre C Glanville J Briscoe S Featherstone R Littlewood A Marshall C Chapter 4: Searching for and selecting studies. In: Higgins JPT, Thomas J, Chandler J, Cumpston M, Li T, Page MJ, Welch VA, editor(s). Cochrane Handbook for Systematic Reviews of Interventions version 6.3 (updated February 2022). Cochrane, 2022 Available from www.training.cochrane.org\/handbook"},{"issue":"10","key":"10.1002\/14651858.CD013610.pub2-BIB0059|cit59","doi-asserted-by":"crossref","first-page":"1865","DOI":"10.1016\/j.pec.2018.06.004","article-title":"Cystic fibrosis-related education: are we meeting patient and caregiver expectations?","volume":"101","author":"Lonabaugh","year":"2018","journal-title":"Patient Education and Counseling"},{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0060|cit60","doi-asserted-by":"publisher","first-page":"210013","DOI":"10.1183\/20734735.0013-2021","article-title":"The treatment burden of cystic fibrosis: a day-to-day experience with treatment as someone with cystic fibrosis","volume":"17","author":"Maetz","year":"2021","journal-title":"Breathe"},{"issue":"6","key":"10.1002\/14651858.CD013610.pub2-BIB0061|cit61","doi-asserted-by":"crossref","first-page":"613","DOI":"10.1097\/MCP.0000000000000110","article-title":"Physiotherapy and cystic fibrosis: what is the evidence base?","volume":"20","author":"McIlwaine","year":"2014","journal-title":"Current Opinion in Pulmonary Medicine"},{"issue":"11","key":"10.1002\/14651858.CD013610.pub2-BIB0062|cit62","doi-asserted-by":"publisher","DOI":"10.1002\/14651858.CD003147.pub5","article-title":"Positive expiratory pressure physiotherapy for airway clearance in people with cystic fibrosis","author":"McIlwaine","year":"2019","journal-title":"Cochrane Database of Systematic Reviews"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0063|cit63","doi-asserted-by":"crossref","first-page":"514","DOI":"10.1016\/j.math.2010.05.012","article-title":"Interventions for enhancing adherence with physiotherapy: A systematic review","volume":"15","year":"2010","journal-title":"Manual Therapy"},{"issue":"6","key":"10.1002\/14651858.CD013610.pub2-BIB0064|cit64","doi-asserted-by":"crossref","first-page":"858","DOI":"10.1016\/j.jcf.2020.08.015","article-title":"Outcomes and endpoints reported in studies of pulmonary exacerbations in people with cystic fibrosis: A systematic review","volume":"19","author":"McLeod","year":"2020","journal-title":"Journal of Cystic Fibrosis"},{"issue":"4","key":"10.1002\/14651858.CD013610.pub2-BIB0065|cit65","doi-asserted-by":"crossref","first-page":"387","DOI":"10.1080\/135485099106135","article-title":"The relationship between control beliefs and self-reported adherence in adults with cystic fibrosis","volume":"4","author":"Meyers","year":"1999","journal-title":"Psychology, Health and Medicine"},{"issue":"6","key":"10.1002\/14651858.CD013610.pub2-BIB0066|cit66","doi-asserted-by":"crossref","first-page":"915","DOI":"10.1177\/1359105306069093","article-title":"Adherence to chest physiotherapy in adults with cystic fibrosis","volume":"11","author":"Meyers","year":"2006","journal-title":"Journal of Health Psychology"},{"issue":"3","key":"10.1002\/14651858.CD013610.pub2-BIB0067|cit67","doi-asserted-by":"crossref","first-page":"117","DOI":"10.1016\/j.jcf.2006.03.002","article-title":"A multi-method assessment of treatment adherence for children with cystic fibrosis","volume":"5","author":"Modi","year":"2006","journal-title":"Journal of Cystic Fibrosis"},{"issue":"2","key":"10.1002\/14651858.CD013610.pub2-BIB0068|cit68","doi-asserted-by":"publisher","DOI":"10.1002\/14651858.CD002769.pub5","article-title":"Non-invasive ventilation for cystic fibrosis","author":"Moran","year":"2017","journal-title":"Cochrane Database of Systematic Reviews"},{"issue":"4","key":"10.1002\/14651858.CD013610.pub2-BIB0069|cit69","doi-asserted-by":"publisher","DOI":"10.1002\/14651858.CD006842.pub5","article-title":"Oscillating devices for airway clearance in people with cystic fibrosis","author":"Morrison","year":"2020","journal-title":"Cochrane Database of Systematic Reviews"},{"issue":"6","key":"10.1002\/14651858.CD013610.pub2-BIB0070|cit70","doi-asserted-by":"crossref","first-page":"915","DOI":"10.1177\/1359105306069093","article-title":"Adherence to chest physiotherapy in adults with cystic fibrosis","volume":"11","author":"Myers","year":"2006","journal-title":"Journal of Health Psychology"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0071|cit71","unstructured":"National Institute Clinical Excellence Cystic Fibrosis; Diagnosis and Management [NG78] Available at www.nice.org.uk\/guidance\/ng78\/chapter\/Recommendations 2017"},{"issue":"6","key":"10.1002\/14651858.CD013610.pub2-BIB0072|cit72","doi-asserted-by":"publisher","first-page":"671","DOI":"10.1097\/MCP.0000000000000732","article-title":"Monitoring early stage lung disease in cystic fibrosis","volume":"26","author":"Nissenbaum","year":"2020","journal-title":"Current Opinion in Pulmonary Medicine"},{"issue":"11","key":"10.1002\/14651858.CD013610.pub2-BIB0073|cit73","doi-asserted-by":"crossref","first-page":"1731","DOI":"10.4187\/respcare.02990","article-title":"Adherence of subjects with cystic fibrosis to their home programme: a systematic review","volume":"59","author":"O'Donohoe","year":"2014","journal-title":"Respiratory Care"},{"issue":"9678","key":"10.1002\/14651858.CD013610.pub2-BIB0074|cit74","doi-asserted-by":"crossref","first-page":"1891","DOI":"10.1016\/S0140-6736(09)60327-5","article-title":"Cystic Fibrosis","volume":"373","author":"O'Sullivan","year":"2009","journal-title":"Lancet"},{"issue":"2","key":"10.1002\/14651858.CD013610.pub2-BIB0075|cit75","doi-asserted-by":"crossref","first-page":"176","DOI":"10.4187\/respcare.06436","article-title":"Objective versus self-reported adherence to airway clearance therapy in cystic fibrosis","volume":"64","author":"Oates","year":"2019","journal-title":"Respiratory Care"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0076|cit76","doi-asserted-by":"crossref","first-page":"535","DOI":"10.12968\/ijtr.2015.22.11.535","article-title":"Patient adherence to physiotherapist prescribed self-management strategies: a critical review","volume":"22","author":"Peek","year":"2015","journal-title":"International Journal of Therapy and Rehabilitation"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0077|cit77","doi-asserted-by":"crossref","first-page":"127","DOI":"10.1016\/j.physio.2015.10.003","article-title":"Interventions to aid patient adherence to physiotherapist prescribed self-management strategies: a systematic review","volume":"102","author":"Peek","year":"2016","journal-title":"Physiotherapy"},{"issue":"4","key":"10.1002\/14651858.CD013610.pub2-BIB0078|cit78","doi-asserted-by":"crossref","first-page":"2347","DOI":"10.1378\/chest.128.4.2347","article-title":"Development and validation of The Cystic Fibrosis Questionnaire in the United States: a health-related quality-of-life measure for cystic fibrosis","volume":"128","author":"Quittner","year":"2005","journal-title":"Chest"},{"issue":"6","key":"10.1002\/14651858.CD013610.pub2-BIB0079|cit79","doi-asserted-by":"crossref","first-page":"1610","DOI":"10.1378\/chest.08-1190","article-title":"Determination of the minimal clinically important difference scores for the Cystic Fibrosis Questionnaire-Revised respiratory symptom scale in two populations of patients with cystic fibrosis and chronic Pseudomonas aeruginosa airway infection","volume":"135","author":"Quittner","year":"2009","journal-title":"Chest"},{"issue":"8","key":"10.1002\/14651858.CD013610.pub2-BIB0080|cit80","doi-asserted-by":"publisher","DOI":"10.1002\/14651858.CD002768.pub5","article-title":"Physical exercise training for cystic fibrosis","author":"Radtke","year":"2022","journal-title":"Cochrane Database of Systematic Reviews"},{"issue":"3","key":"10.1002\/14651858.CD013610.pub2-BIB0081|cit81","doi-asserted-by":"crossref","first-page":"341","DOI":"10.1586\/ers.12.19","article-title":"Exercise as part of a cystic fibrosis therapeutic routine","volume":"6","author":"Rand","year":"2012","journal-title":"Expert Review of Respiratory Medicine"},{"issue":"5","key":"10.1002\/14651858.CD013610.pub2-BIB0082|cit82","doi-asserted-by":"crossref","first-page":"595","DOI":"10.4187\/aarc0427","article-title":"Cystic Fibrosis: pathogenesis and future treatment strategies","volume":"54","author":"Ratjen","year":"2009","journal-title":"Respiratory Care"},{"issue":"10","key":"10.1002\/14651858.CD013610.pub2-BIB0083|cit83","doi-asserted-by":"publisher","first-page":"e039587","DOI":"10.1136\/bmjopen-2020-039587","article-title":"Protocol for Project Fizzyo, an analytic longitudinal observational cohort study of physiotherapy for children and young people with cystic fibrosis, with interrupted time-series design","volume":"10","author":"Raywood","year":"2020","journal-title":"BMJ Open"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0084|cit84","unstructured":"Raywood E Shannon H Filipow N Tanriver G Stanojevic S Kapoor K Quantity and quality of airway clearance in children and young peoplewith cystic fibrosis Journal of Cystic Fibrosis S1569 1993(22)00686-5 10.1016\/j.jcf.2022.09.008"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0085|cit85","doi-asserted-by":"publisher","first-page":"24","DOI":"10.1186\/s40900-019-0159-x","article-title":"Adapting the James Lind Priority Setting Process to better support patient participation: an example from cystic fibrosis","volume":"5","author":"Rowbotham","year":"2019","journal-title":"Research Involvment and Engagement"},{"issue":"10","key":"10.1002\/14651858.CD013610.pub2-BIB0086|cit86","doi-asserted-by":"crossref","first-page":"2646","DOI":"10.1002\/ppul.24912","article-title":"Adherence and barriers to general and respiratory exercises in cystic fibrosis","volume":"55","author":"Santuzzi","year":"2020","journal-title":"Pediatric Pulmonology"},{"issue":"2","key":"10.1002\/14651858.CD013610.pub2-BIB0087|cit87","doi-asserted-by":"crossref","first-page":"91","DOI":"10.1016\/j.jcf.2008.09.007","article-title":"High treatment burden in adults with cystic fibrosis: challenges to disease self-management","volume":"8","author":"Sawicki","year":"2009","journal-title":"Journal of Cystic Fibrosis"},{"issue":"5","key":"10.1002\/14651858.CD013610.pub2-BIB0088|cit88","doi-asserted-by":"crossref","first-page":"461","DOI":"10.1016\/j.jcf.2012.12.009","article-title":"Treatment complexity in cystic fibrosis: trends over time and associations with site-specific outcomes","volume":"12","author":"Sawicki","year":"2013","journal-title":"Journal Cystic Fibrosis"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0089|cit89","unstructured":"Sch\u00fcnemann HJ Higgins JP Vist GE Glasziou P Akl EA Skoetz N Guyatt GH Chapter 14: Completing \u2018Summary of findings\u2019 tables and grading the certainty of the evidence. In: Higgins JP, Thomas J, Chandler J, Cumpston M, Li T, Page MJ, Welch VA, editor(s). Cochrane Handbook for Systematic Reviews of Interventions version 6.3 (updated February 2022). Cochrane, 2022 Available from www.training.cochrane.org\/handbook"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0090|cit90","unstructured":"Sch\u00fcnemann HJ Vist GE Higgins JP Santesso N Deeks JJ Glasziou P Chapter 15: Interpreting results and drawing conclusions. In: Higgins JP, Thomas J, Chandler J, Cumpston M, Li T, Page MJ, Welch VA, editor(s). Cochrane Handbook for Systematic Reviews of Interventions version 6.3 (updated February 2022). Cochrane, 2022 Available from www.training.cochrane.org\/handbook"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0091|cit91","unstructured":"Rand 36 Item Short Form Health Survey www.rand.org\/health-care\/surveys_tools\/mos\/36-item-short-form\/scoring.html"},{"issue":"7","key":"10.1002\/14651858.CD013610.pub2-BIB0092|cit92","doi-asserted-by":"crossref","first-page":"778","DOI":"10.4187\/respcare.06500","article-title":"Persistent adherence to airway clearance therapy in adults with cystic fibrosis","volume":"64","author":"Sherman","year":"2019","journal-title":"Respiratory Care"},{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0093|cit93","doi-asserted-by":"crossref","first-page":"43","DOI":"10.1016\/j.jphys.2018.11.006","article-title":"Exercise is commonly used as a substitute for traditional airway clearance techniques by adults with cystic fibrosis in Australia: a survey","volume":"65","author":"Ward","year":"2019","journal-title":"Journal of Physiotherapy"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0094|cit94","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1080\/09593985.2020.1858465","article-title":"Development of a device to measure adherence and pressure characteristics of positive expiratory pressure therapies used by adults with cystic fibrosis","volume":"Dec 13","author":"Ward","year":"2020","journal-title":"Physiotherapy Theory and Practice"},{"key":"10.1002\/14651858.CD013610.pub2-BIB0095|cit95","unstructured":"World Health Organisation Adherence to long term therapies: evidence for action Available at www.who.int\/chp\/ knowledge\/publications\/adherence \u0307report\/en\/ 2003"},{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0096|cit96","doi-asserted-by":"crossref","first-page":"16","DOI":"10.1016\/j.prrv.2014.04.007","article-title":"Moving cystic fibrosis care from rescue to prevention by embedding adherence measurement in routine care","volume":"15","author":"Wildman","year":"2014","journal-title":"Paediatric Respiratory Reviews"},{"issue":"5","key":"10.1002\/14651858.CD013610.pub2-BIB0097|cit97","doi-asserted-by":"publisher","first-page":"461","DOI":"10.1136\/thoraxjnl-2021-217594","article-title":"Self-management intervention to reduce pulmonary exacerbations by supporting treatment adherence in adults with cystic fibrosis: a randomised controlled trial","volume":"77","author":"Wildman","year":"2022","journal-title":"Thorax"},{"issue":"1","key":"10.1002\/14651858.CD013610.pub2-BIB0098|cit98","doi-asserted-by":"publisher","DOI":"10.1002\/14651858.CD011231.pub2","article-title":"Airway clearance techniques for cystic fibrosis: an overview of Cochrane systematic reviews","author":"Wilson","year":"2019","journal-title":"Cochrane Database of Systematic Reviews"},{"issue":"2","key":"10.1002\/14651858.CD013610.pub2-BIB0099|cit99","doi-asserted-by":"publisher","DOI":"10.1002\/14651858.CD007862.pub5","article-title":"Active cycle of breathing technique for cystic fibrosis","author":"Wilson","year":"2023","journal-title":"Cochrane Database of Systematic Reviews"},{"issue":"5","key":"10.1002\/14651858.CD013610.pub2-BIB0100|cit100","doi-asserted-by":"publisher","DOI":"10.1002\/14651858.CD013610","article-title":"Interventions for improving adherence to airway clearance treatment and exercise in people with cystic fibrosis","author":"Jones","year":"2020","journal-title":"Cochrane Database of Systematic Reviews"}],"container-title":["Cochrane Database of Systematic Reviews"],"original-title":[],"language":"en","deposited":{"date-parts":[[2024,8,6]],"date-time":"2024-08-06T06:28:42Z","timestamp":1722925722000},"score":1,"resource":{"primary":{"URL":"http:\/\/doi.wiley.com\/10.1002\/14651858.CD013610.pub2"}},"subtitle":[],"editor":[{"name":"Cochrane Cystic Fibrosis and Genetic Disorders Group","sequence":"first","affiliation":[],"role":[{"role":"editor","vocabulary":"crossref"}]}],"short-title":[],"issued":{"date-parts":[[2023,7,18]]},"references-count":100,"journal-issue":{"issue":"7","published-online":{"date-parts":[[2023,7]]}},"URL":"https:\/\/doi.org\/10.1002\/14651858.cd013610.pub2","relation":{},"ISSN":["1465-1858"],"issn-type":[{"value":"1465-1858","type":"electronic"}],"subject":[],"published":{"date-parts":[[2023,7,18]]}}}