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After 8 years, a follow\u2010up study of 12 of the 17 original patients was done with a similar protocol. During this period, 2 patients died: one of sudden death while the other had acute left ventricular failure. In our first control study, we found EKG abnormalities in IS of our patients, consisting mostly of conduction defects or pseudonecrotic patterns. In our second control, all patients had conduction system disease and, in addition, 3 of them had premature ventricular beats. One patient developed dilated cardiomyopathy. In 6 patients, structural involvement of the right ventricle was found. We conclude that even in asymptomatic myotonic dystrophy patients a conduction system deficit is present and progresses, and cardiac death may occur in about 12% of these patients.<\/jats:p>","DOI":"10.1002\/clc.4960110407","type":"journal-article","created":{"date-parts":[[2009,2,5]],"date-time":"2009-02-05T05:11:14Z","timestamp":1233810674000},"page":"231-238","source":"Crossref","is-referenced-by-count":38,"title":["The natural history of cardiac involvement in myotonic dystrophy: An eight\u2010year follow\u2010up in 17 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