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In contrast to the adult population, children present early\u2010on with behavioral, psychiatric, and cognitive symptoms, in addition to a diverse spectrum of movement disorders. This poses a distinct challenge in diagnosis and management. We here describe the spectrum of movement disorders, accompanied with detailed video recordings, in seven cases of juvenile\u2010onset HD. Our findings highlight early cognitive and behavioral symptoms, preceding motor symptoms. The diverse movement disorder phenotypes included dystonia, Parkinsonism, myoclonus, and chorea, findings which underscore the heterogeneity of presenting symptoms.<\/jats:p>","DOI":"10.1002\/acn3.52193","type":"journal-article","created":{"date-parts":[[2024,9,6]],"date-time":"2024-09-06T10:45:24Z","timestamp":1725619524000},"page":"2805-2810","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":10,"title":["Juvenile\u2010onset Huntington's disease \u2013 Spectrum and evolution of presenting movement disorders"],"prefix":"10.1002","volume":"11","author":[{"ORCID":"https:\/\/orcid.org\/0009-0004-6892-5189","authenticated-orcid":false,"given":"Kathryn","family":"Yang","sequence":"first","affiliation":[{"name":"Movement Disorders Program, Department of Neurology, Boston Children's Hospital Harvard Medical School  Boston Massachusetts 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