{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2023,10,23]],"date-time":"2023-10-23T05:04:51Z","timestamp":1698037491304},"reference-count":6,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[2006,7,11]],"date-time":"2006-07-11T00:00:00Z","timestamp":1152576000000},"content-version":"vor","delay-in-days":5489,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["American J Hematol"],"published-print":{"date-parts":[[1991,7]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Retroperitoneal fibrosis represents an idiopathic systemic fibrosing syndrome which leads to the development of progressive hydronephrosis and azotemia (Stewart and Friberg: Southern Medical Journal 77:1185\u20131187, 1984; Morad et al.: <jats:italic>American Journal of Medicine<\/jats:italic> 82:363\u2013366, 1987). Evidence in the literature supports a hypothesis that retroperitoneal fibrosis represents a systemic autoimmune process (Lichon et al.: <jats:italic>Journal of Rheumatology<\/jats:italic> 11:373,374, 1984; Lipman et al.: JAMA 196:204\u2013206, 1966; Littlejohn and Keystone: <jats:italic>Journal Rheumatology<\/jats:italic> 8:665\u2013669, 1981; Katz et al.: <jats:italic>American Journal of Clinical Pathology<\/jats:italic> 67:436\u2013439, 1977). We report a case of a patient with retroperitoneal fibrosis, immune thrombocytopenia, presence of antinuclear antibody, and direct Coombs positivity which provides further evidence that retroperitoneal fibrosis is an autoimmune process. Progressive obstructive uropathy related to his fibrosis led to bilateral hydronephrosis and significant renal function impairment. Also, he developed marked immune thrombocytopenia. Treatment with prednisone produced a dramatic response in both platelet count and renal function.<\/jats:p>","DOI":"10.1002\/ajh.2830370315","type":"journal-article","created":{"date-parts":[[2007,2,21]],"date-time":"2007-02-21T12:50:36Z","timestamp":1172062236000},"page":"204-205","source":"Crossref","is-referenced-by-count":6,"title":["Retroperitoneal fibrosis accompanying immune thrombocytopenia"],"prefix":"10.1002","volume":"37","author":[{"given":"Paul M.","family":"Wallach","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Michael T.","family":"Flannery","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Harold M.","family":"Adelman","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Julio","family":"Powsang","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hussein","family":"Saba","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Philip","family":"Altus","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Luis R.","family":"Espinoza","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2006,7,11]]},"reference":[{"key":"e_1_2_1_2_2","doi-asserted-by":"publisher","DOI":"10.1097\/00007611-198409000-00036"},{"key":"e_1_2_1_3_2","doi-asserted-by":"publisher","DOI":"10.1016\/0002-9343(87)90089-1"},{"key":"e_1_2_1_4_2","first-page":"373","article-title":"Retroperitoneal fibrosis associated with systemic lupus erythematosus: A case report and brief review","volume":"11","author":"Lichon FS","year":"1984","journal-title":"J Rheumatol"},{"key":"e_1_2_1_5_2","doi-asserted-by":"publisher","DOI":"10.1001\/jama.196.11.1022"},{"key":"e_1_2_1_6_2","first-page":"665","article-title":"The association of retroperitoneal fibrosis with systemic vasculitis and HLA\u2010B 27: A case report and review of the literature","volume":"8","author":"Littlejohn GO","year":"1981","journal-title":"J Rheumatol"},{"key":"e_1_2_1_7_2","doi-asserted-by":"publisher","DOI":"10.1093\/ajcp\/67.5.436"}],"container-title":["American Journal of Hematology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Fajh.2830370315","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/ajh.2830370315","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,22]],"date-time":"2023-10-22T22:16:13Z","timestamp":1698012973000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/ajh.2830370315"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1991,7]]},"references-count":6,"journal-issue":{"issue":"3","published-print":{"date-parts":[[1991,7]]}},"alternative-id":["10.1002\/ajh.2830370315"],"URL":"https:\/\/doi.org\/10.1002\/ajh.2830370315","archive":["Portico"],"relation":{},"ISSN":["0361-8609","1096-8652"],"issn-type":[{"value":"0361-8609","type":"print"},{"value":"1096-8652","type":"electronic"}],"subject":[],"published":{"date-parts":[[1991,7]]}}}