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Cytochrome b5 reductase deficiency was most severe in red cells (0.3\u20134%) and less marked in platelets (13\u201327%), lymphocytes (18\u201331%), and fibroblasts (50%). The present case appears to be a new variant of cytochrome b5 reductase deficiency (b5R<jats:sub>Kurashiki<\/jats:sub>). \u00a9 1992 Wiley\u2010Liss, Inc.<\/jats:p>","DOI":"10.1002\/ajh.2830400411","type":"journal-article","created":{"date-parts":[[2007,2,21]],"date-time":"2007-02-21T13:00:29Z","timestamp":1172062829000},"page":"299-305","source":"Crossref","is-referenced-by-count":13,"title":["New variant of cytochrome b5 reductase deficiency (b5R<sub>Kurashiki<\/sub>) in red cells, platelets, lymphocytes, and cultured fibroblasts with congenital methemoglobinemia, mental and neurological retardation, and skeletal 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