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This observation, together with other literature reports, suggests that the occurrence of ICS with polysplenia and extrahepatic biliary atresia represent the result of a single dysmorphogenetic process. It is concluded that polysplenia and extrahepatic biliary atresia are rare and unusual manifestations of ICS.<\/jats:p>","DOI":"10.1002\/ajmg.1320330320","type":"journal-article","created":{"date-parts":[[2005,6,12]],"date-time":"2005-06-12T03:05:12Z","timestamp":1118545512000},"page":"390-393","source":"Crossref","is-referenced-by-count":48,"title":["Immotile cilia syndrome including polysplenia, situs inversus, and extrahepatic biliary 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