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The serum P\u2010III\u2010NP levels correlated with the amount of type III procollagen secreted by the patients' cultured fibroblasts. Serum P\u2010III\u2010NP determination is a simple test that identifies a major subgroup of patients with this lifethreatening, dominantly inherited connective tissue disorder and may be especially helpful in making the diagnosis in children.<\/jats:p>","DOI":"10.1002\/ajmg.1320340113","type":"journal-article","created":{"date-parts":[[2005,6,11]],"date-time":"2005-06-11T13:27:54Z","timestamp":1118496474000},"page":"68-71","source":"Crossref","is-referenced-by-count":19,"title":["Ehlers\u2010Danlos syndrome type IV: A subset of patients distinguished by low serum levels of the amino\u2010terminal propeptide of type III procollagen"],"prefix":"10.1002","volume":"34","author":[{"given":"Beat","family":"Steinmann","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Andrea","family":"Superti\u2010Furga","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Helen 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