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We report an additional 9 cases from one pediatric center, suggesting that this syndrome is not as rare as was previously thought.<\/jats:p><jats:p>Normal amniotic fluid volumes in affected pregnancies prior to the 22nd week of gestation have been documented, compromising early prenatal diagnosis. Late second trimester sonographic demonstration of oligohydramnios, with structurally normal kidneys, should suggest this diagnosis and the need for detailed post\u2010mortem pathological examination. \u00a9 1992 Wiley\u2010Liss, Inc.<\/jats:p>","DOI":"10.1002\/ajmg.1320430512","type":"journal-article","created":{"date-parts":[[2005,6,12]],"date-time":"2005-06-12T04:49:25Z","timestamp":1118551765000},"page":"811-814","source":"Crossref","is-referenced-by-count":52,"title":["Renal tubular dysgenesis: A not not uncommon autosomal recessive syndrome: A review"],"prefix":"10.1002","volume":"43","author":[{"given":"Judith E.","family":"Allanson","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Alasdair G. 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