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Hydrops fetalis may be present in newborns with the Hennekam syndrome. Lymphoscintigraphy can be useful in explaining pleural\u2010pulmonary involvement of this generalized lymph vessel malformation syndrome. \u00a9 2003 Wiley\u2010Liss, Inc.<\/jats:p>","DOI":"10.1002\/ajmg.a.20180","type":"journal-article","created":{"date-parts":[[2003,6,4]],"date-time":"2003-06-04T10:07:08Z","timestamp":1054721228000},"page":"92-96","source":"Crossref","is-referenced-by-count":41,"title":["Hennekam syndrome presenting as nonimmune hydrops fetalis, congenital chylothorax, and congenital pulmonary lymphangiectasia"],"prefix":"10.1002","volume":"120A","author":[{"given":"Carlo","family":"Bellini","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Massimo","family":"Mazzella","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Cesare","family":"Arioni","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Corradino","family":"Campisi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gioconda","family":"Taddei","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Paolo","family":"Tom\u00e0","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Francesco","family":"Boccardo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Raoul C.","family":"Hennekam","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Giovanni","family":"Serra","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2003,4,8]]},"reference":[{"key":"e_1_2_4_2_1","doi-asserted-by":"publisher","DOI":"10.1002\/(SICI)1096-8628(19970808)71:2<211::AID-AJMG17>3.0.CO;2-H"},{"key":"e_1_2_4_3_1","first-page":"61","article-title":"A case of Hennekam syndrome diagnosed at birth and review of the literature","volume":"28","author":"Bellini C","year":"2002","journal-title":"Ital J Pediatr"},{"key":"e_1_2_4_4_1","doi-asserted-by":"publisher","DOI":"10.1097\/00003072-200205000-00023"},{"key":"e_1_2_4_5_1","doi-asserted-by":"publisher","DOI":"10.2214\/ajr.173.6.10584805"},{"key":"e_1_2_4_6_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320570115"},{"key":"e_1_2_4_7_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0929-693X(99)80054-2"},{"key":"e_1_2_4_8_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.10509"},{"key":"e_1_2_4_9_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320400223"},{"key":"e_1_2_4_10_1","doi-asserted-by":"publisher","DOI":"10.1002\/(SICI)1096-8628(19961230)66:4<438::AID-AJMG10>3.0.CO;2-V"},{"key":"e_1_2_4_11_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320340429"},{"key":"e_1_2_4_12_1","doi-asserted-by":"publisher","DOI":"10.1097\/00019605-200009010-00004"},{"key":"e_1_2_4_13_1","doi-asserted-by":"publisher","DOI":"10.1002\/1096-8628(20000814)93:4<264::AID-AJMG2>3.0.CO;2-5"},{"key":"e_1_2_4_14_1","first-page":"560","volume-title":"Smith's recognizable patterns of human malformations","author":"Jones KL","year":"1988"},{"key":"e_1_2_4_15_1","first-page":"429","volume-title":"Textbook of fetal and perinatal pathology","author":"Keeling JW","year":"1991"},{"key":"e_1_2_4_16_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320470112"},{"key":"e_1_2_4_17_1","doi-asserted-by":"publisher","DOI":"10.1007\/s004310050862"},{"key":"e_1_2_4_18_1","first-page":"533","article-title":"Congenital pulmonary lymphangiectasis","volume":"100","author":"Noonan JA","year":"1971","journal-title":"Radiology"},{"key":"e_1_2_4_19_1","unstructured":"OMIM Online Mendelian Inheritance in Man (TM).2000. 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