{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,6]],"date-time":"2026-10-06T22:39:06Z","timestamp":1791326346146,"version":"4.3.1"},"reference-count":31,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2022,1,29]],"date-time":"2022-01-29T00:00:00Z","timestamp":1643414400000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["American J of Med Genetics Pt A"],"published-print":{"date-parts":[[2022,5]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Prader\u2010Willi Syndrome (PWS) is a rare genetic disorder associated with emotional\/behavioral disturbances. These difficulties are well documented in the literature, but the positive attributes of these individuals are not described. Taking a strengths\u2010based approach, the aim of this study was to describe the emotional\/behavioral strengths and difficulties in children and young people with PWS from their parent caregivers' perspectives. Parent caregivers of 52 individuals with PWS aged 4\u201324\u2009years (median\u00a0=\u00a012.1\u2009years; including 22 males) completed the parent form of the Developmental Behavior Checklist (DBC\u2010P), including its original two open\u2010ended questions regarding positive traits. Prevalences of emotional\/behavioral disturbances were comparable to those reported in previous literature: common behaviors of concern across studies being skin\u2010picking (75%), impulsivity (69%), poor sense of danger (67%), lying (67%), and tantrums (54%). Total DBC\u2010P scores showed that just over half (<jats:italic>n<\/jats:italic>\u00a0=\u00a028, 54%) had scores indicative of clinically significant behavior problems. However, thematic analysis of caregivers' written comments regarding their children's strengths resolved into three themes: warmth (94%), persistence (41%), and skills (41%). Warmth encompassed friendliness, happiness, and empathy. A strength\u2010based approach to behavioral difficulties in PWS provides a more balanced view of the children and a more holistic foundation for interventions.<\/jats:p>","DOI":"10.1002\/ajmg.a.62671","type":"journal-article","created":{"date-parts":[[2022,1,29]],"date-time":"2022-01-29T10:33:19Z","timestamp":1643452399000},"page":"1488-1496","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":3,"title":["Strengths and challenging behaviors in children and adolescents with<scp>Prader\u2010Willi<\/scp>syndrome: Two sides to the coin"],"prefix":"10.1002","volume":"188","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-7358-9037","authenticated-orcid":false,"given":"Jenny","family":"Downs","sequence":"first","affiliation":[{"name":"Child Disability Telethon Kids Institute Nedlands Western Australia Australia"},{"name":"School of Physiotherapy and Exercise Science Curtin University Bentley Western Australia Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A. 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