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We compared survival and survival to discharge rates between patients who underwent tracheostomies during their NICU stays (T group, <jats:italic>n<\/jats:italic>\u2009=\u20098) and those who did not (non\u2010T group, <jats:italic>n<\/jats:italic>\u2009=\u200911). A total of 19 patients enrolled. Median survival in all patients was 673 (266\u20131535) days. Significant differences in the 1\u2010, 2\u2010, and 3\u2010year survival rates were found between the T and the non\u2010T groups (100% vs. 46%, <jats:italic>p<\/jats:italic>\u2009=\u20090.018; 88% vs. 18%, <jats:italic>p<\/jats:italic>\u2009=\u20090.006; 63% vs. 9%, <jats:italic>p<\/jats:italic>\u2009=\u20090.041, respectively). The survival to discharge rate was higher in the T versus non\u2010T group (75% vs. 45%, <jats:italic>p<\/jats:italic>\u2009=\u20090.352). This study highlights a significantly higher long\u2010term survival of patients with trisomy 13 syndrome who underwent tracheostomies during their NICU stays.<\/jats:p>","DOI":"10.1002\/ajmg.a.63393","type":"journal-article","created":{"date-parts":[[2023,9,2]],"date-time":"2023-09-02T05:06:16Z","timestamp":1693631176000},"page":"2736-2742","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":4,"title":["Impact of tracheostomies on the long\u2010term survival of patients with trisomy 13 syndrome"],"prefix":"10.1002","volume":"191","author":[{"given":"Shoko","family":"Tamaki","sequence":"first","affiliation":[{"name":"Department of Neonatology Hyogo Prefectural Kobe Children's Hospital Perinatal Center  Kobe Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2871-4000","authenticated-orcid":false,"given":"Sota","family":"Iwatani","sequence":"additional","affiliation":[{"name":"Department of Neonatology Hyogo Prefectural Kobe Children's Hospital Perinatal Center  Kobe Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shinji","family":"Hagimoto","sequence":"additional","affiliation":[{"name":"Department of Neonatology Hyogo Prefectural Kobe Children's Hospital Perinatal Center  Kobe Japan"},{"name":"Department of Pediatrics Tottori Prefectural Central Hospital  Tottori Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ayako","family":"Izumi","sequence":"additional","affiliation":[{"name":"Department of Neonatology Hyogo Prefectural Kobe Children's Hospital Perinatal Center  Kobe Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Toshihiko","family":"Ikuta","sequence":"additional","affiliation":[{"name":"Department of Neonatology Hyogo Prefectural Kobe Children's Hospital Perinatal Center  Kobe Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Emiko","family":"Takeoka","sequence":"additional","affiliation":[{"name":"Department of Neonatology Hyogo Prefectural Kobe Children's Hospital Perinatal Center  Kobe Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sachiko","family":"Matsui","sequence":"additional","affiliation":[{"name":"Department of Neonatology Hyogo Prefectural Kobe Children's Hospital Perinatal Center  Kobe Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hitomi","family":"Mimura","sequence":"additional","affiliation":[{"name":"Department of Neonatology Hyogo Prefectural Kobe Children's Hospital Perinatal Center  Kobe Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shogo","family":"Minamikawa","sequence":"additional","affiliation":[{"name":"Department of General Pediatrics Hyogo Prefectural Kobe Children's Hospital  Kobe Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Yasuo","family":"Nakagishi","sequence":"additional","affiliation":[{"name":"Department of General Pediatrics Hyogo Prefectural Kobe Children's Hospital  Kobe Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Seiji","family":"Yoshimoto","sequence":"additional","affiliation":[{"name":"Department of Neonatology Hyogo Prefectural Kobe Children's Hospital Perinatal Center  Kobe Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hideto","family":"Nakao","sequence":"additional","affiliation":[{"name":"Department of Neonatology Hyogo Prefectural Kobe Children's Hospital Perinatal Center  Kobe Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2023,9]]},"reference":[{"key":"e_1_2_11_2_1","doi-asserted-by":"publisher","DOI":"10.1002\/lary.30416"},{"key":"e_1_2_11_3_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpeds.2016.11.054"},{"key":"e_1_2_11_4_1","doi-asserted-by":"publisher","DOI":"10.1002\/9780470893159.ch54"},{"key":"e_1_2_11_5_1","doi-asserted-by":"publisher","DOI":"10.1161\/JAHA.119.012349"},{"key":"e_1_2_11_6_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpeds.2022.04.010"},{"key":"e_1_2_11_7_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.a.62175"},{"key":"e_1_2_11_8_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.a.61365"},{"key":"e_1_2_11_9_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.amjcard.2003.12.012"},{"key":"e_1_2_11_10_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.a.37104"},{"key":"e_1_2_11_11_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.c.31526"},{"key":"e_1_2_11_12_1","unstructured":"Japan Society for Neonatal Health and Development. 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