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The patient reported here was a 47\u2010year\u2010old man whose neurological symptoms apparently preceded his cutaneous lesions. His course consisted of a disseminated neurological disease and exacerbated following a herpes zoster infection. His condition rapidly deteriorated despite corticotropin, glucocorticoids, and low\u2010molecular\u2010weight dextran. Necropsy revealed a disseminated occlusive vasculopathy and diffuse encephalomyelomalacia of the brain and spinal cord. A review of autopsied patients with central nervous system involvement is provided.<\/jats:p>","DOI":"10.1002\/ana.410030504","type":"journal-article","created":{"date-parts":[[2005,1,1]],"date-time":"2005-01-01T13:06:44Z","timestamp":1104584804000},"page":"388-392","source":"Crossref","is-referenced-by-count":28,"title":["Papulosis atrophicans maligna (K\u00f6hlmeier\u2010Degos disease): A disseminated occlusive vasculopathy"],"prefix":"10.1002","volume":"3","author":[{"given":"H. 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