{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,15]],"date-time":"2026-09-15T12:34:05Z","timestamp":1789475645098,"version":"build-2803163510"},"reference-count":15,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2004,10,8]],"date-time":"2004-10-08T00:00:00Z","timestamp":1097193600000},"content-version":"vor","delay-in-days":3448,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Annals of Neurology"],"published-print":{"date-parts":[[1995,5]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Linear scleroderma en coup de sabre (LScs) is a rare disorder not infrequently associated with neurologic symptoms, notably epilepsy. However, histopathologic documentation of intracerebral lesions in LScs is very limited and the etiology of the central nervous system symptoms has therefore never been convincingly established. We describe a 27\u2010year\u2010old woman with LScs and a long\u2010standing history of epilepsy. Radiographic studies demonstrated a focal, intraparenchymal lesion in the left frontal lobe directly subjacent to the area of scleroderma on the forehead and scalp. The resected cerebral lesion revealed localized band\u2010like sclerosis of the leptomeninges and associated vessels, as well as intraparenchymal calcifications and anomalous, ectatic vessels. These findings suggest that LScs may represent a neurocutaneous syndrome of vascular dysplasia similar to the Sturge\u2010Weber syndrome, rather than a localized form of collagen vascular disease, as suggested by some.<\/jats:p>","DOI":"10.1002\/ana.410370519","type":"journal-article","created":{"date-parts":[[2005,1,1]],"date-time":"2005-01-01T16:17:05Z","timestamp":1104596225000},"page":"679-681","source":"Crossref","is-referenced-by-count":71,"title":["Intracerebral involvement in scleroderma en coup de sabre: Report of a case with neuropathologic findings"],"prefix":"10.1002","volume":"37","author":[{"given":"Marilda H.","family":"Chung","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"John","family":"Sum","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Martha J.","family":"Morrell","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dikran S.","family":"Horoupian","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2004,10,8]]},"reference":[{"key":"e_1_2_1_2_2","doi-asserted-by":"publisher","DOI":"10.1111\/1523-1747.ep12550429"},{"key":"e_1_2_1_3_2","first-page":"65","article-title":"Localized cutaneous scleroderma","volume":"11","author":"Krafchik BR","year":"1992","journal-title":"Semin Dermatol"},{"key":"e_1_2_1_4_2","doi-asserted-by":"publisher","DOI":"10.7326\/0003-4819-104-6-849"},{"key":"e_1_2_1_5_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3476(62)80064-X"},{"key":"e_1_2_1_6_2","doi-asserted-by":"publisher","DOI":"10.1007\/BF00315664"},{"key":"e_1_2_1_7_2","doi-asserted-by":"publisher","DOI":"10.1001\/archneurpsyc.1945.02300080003001"},{"key":"e_1_2_1_8_2","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.37.9.997"},{"key":"e_1_2_1_9_2","doi-asserted-by":"crossref","first-page":"688","DOI":"10.1001\/archderm.1968.01610120078012","article-title":"Bilateral linear scleroderma en coup de sabre","volume":"97","author":"Dilley JJ","year":"1968","journal-title":"Arch Dermatol"},{"key":"e_1_2_1_10_2","doi-asserted-by":"publisher","DOI":"10.1097\/00005053-193507000-00004"},{"key":"e_1_2_1_11_2","doi-asserted-by":"publisher","DOI":"10.1136\/ard.50.4.260"},{"key":"e_1_2_1_12_2","first-page":"145","article-title":"MR of brain involvement in progressive facial hemiatrophy (Romberg disease): reconsideration of a syndrome","volume":"15","author":"Terstegge K.","year":"1994","journal-title":"AJNR"},{"key":"e_1_2_1_13_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3476(37)80192-4"},{"key":"e_1_2_1_14_2","doi-asserted-by":"publisher","DOI":"10.1097\/00006534-199005000-00001"},{"key":"e_1_2_1_15_2","doi-asserted-by":"publisher","DOI":"10.1001\/archderm.1948.01520200004001"},{"key":"e_1_2_1_16_2","first-page":"512","volume-title":"The phakomatoses","author":"Koch G.","year":"1972"}],"container-title":["Annals of Neurology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Fana.410370519","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/ana.410370519","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,28]],"date-time":"2023-09-28T09:11:38Z","timestamp":1695892298000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/ana.410370519"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1995,5]]},"references-count":15,"journal-issue":{"issue":"5","published-print":{"date-parts":[[1995,5]]}},"alternative-id":["10.1002\/ana.410370519"],"URL":"https:\/\/doi.org\/10.1002\/ana.410370519","archive":["Portico"],"relation":{},"ISSN":["0364-5134","1531-8249"],"issn-type":[{"value":"0364-5134","type":"print"},{"value":"1531-8249","type":"electronic"}],"subject":[],"published":{"date-parts":[[1995,5]]}}}