{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,20]],"date-time":"2026-10-20T23:59:04Z","timestamp":1792540744282,"version":"4.5.0"},"reference-count":13,"publisher":"Wiley","issue":"8","license":[{"start":{"date-parts":[[2010,8,17]],"date-time":"2010-08-17T00:00:00Z","timestamp":1282003200000},"content-version":"vor","delay-in-days":7321,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Arthritis &amp; Rheumatism"],"published-print":{"date-parts":[[1990,8]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Criteria for the classification of Churg\u2010Strauss syndrome (CSS) were developed by comparing 20 patients who had this diagnosis with 787 control patients with other forms of vasculitis. For the <jats:italic>traditional format classification<\/jats:italic>, 6 criteria were selected: asthma, eosinophilia &gt;10% on differential white blood cell count, mononeuropathy (including multiplex) or polyneuropathy, non\u2010fixed pulmonary infiltrates on roentgenography, paranasal sinus abnormality, and biopsy containing a blood vessel with extravascular eosinophils. The presence of 4 or more of these 6 criteria yielded a sensitivity of 85% and a specificity of 99.7%. A <jats:italic>classification tree<\/jats:italic> was also constructed with 3 selected criteria: asthma, eosinophilia &gt;10% on differential white blood cell count, and history of documented allergy other than asthma or drug sensitivity. If a subject has eosinophilia and a documented history of either asthma or allergy, then that subject is classified as having CSS. For the tree classification, the sensitivity was 95% and the specificity was 99.2%. Advantages of the traditional format compared with the classification tree format, when applied to patients with systemic vasculitis, and their comparison with earlier work on CSS are discussed.<\/jats:p>","DOI":"10.1002\/art.1780330806","type":"journal-article","created":{"date-parts":[[2010,8,18]],"date-time":"2010-08-18T07:02:03Z","timestamp":1282114923000},"page":"1094-1100","source":"Crossref","is-referenced-by-count":1801,"title":["The American College of Rheumatology 1990 criteria for the classification of churg\u2010strauss syndrome (allergic granulomatosis and angiitis)"],"prefix":"10.1002","volume":"33","author":[{"given":"Alfonse T.","family":"Masi","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gene G.","family":"Hunder","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"J. T.","family":"Lie","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Beat A.","family":"Michel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Daniel A.","family":"Bloch","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"William P.","family":"Arend","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Leonard H.","family":"Calabrese","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Steven M.","family":"Edworthy","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anthony S.","family":"Fauci","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Randi Y.","family":"Leavitt","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"suffix":"Jr","given":"Robert W.","family":"Lightfoot","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dennis J.","family":"McShane","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"John A.","family":"Mills","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mary Betty","family":"Stevens","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Stanley L.","family":"Wallace","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nathan J.","family":"Zvaifler","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2010,8,17]]},"reference":[{"key":"e_1_2_1_2_2","first-page":"277","article-title":"Allergic granulomatosis, allergic angiitis, and periarteritis nodosa","volume":"27","author":"Churg J","year":"1951","journal-title":"Am J Pathol"},{"key":"e_1_2_1_3_2","first-page":"619","article-title":"Allergic granulomatosis and granulomatous\u2010vascular syndromes","volume":"21","author":"Churg J","year":"1963","journal-title":"Ann Allergy"},{"key":"e_1_2_1_4_2","first-page":"477","article-title":"Allergic granulomatosis and angiitis (Churg\u2010Strauss syndrome): report and analysis of 30 cases","volume":"52","author":"Chumbley LC","year":"1977","journal-title":"Mayo Clin Proc"},{"key":"e_1_2_1_5_2","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM198103053041017"},{"key":"e_1_2_1_6_2","doi-asserted-by":"publisher","DOI":"10.1097\/00005792-198403000-00001"},{"key":"e_1_2_1_7_2","doi-asserted-by":"publisher","DOI":"10.1097\/00005792-198305000-00002"},{"key":"e_1_2_1_8_2","first-page":"429","article-title":"The classification of vasculitis and a reappraisal of allergic granulomatosis and angiitis (Churg\u2010Strauss syndrome)","volume":"53","author":"Lie JT","year":"1986","journal-title":"Mt Sinai J Med (NY)"},{"key":"e_1_2_1_9_2","doi-asserted-by":"crossref","first-page":"1074","DOI":"10.1002\/art.1780330804","article-title":"Illustrated histopathologic classification criteria for selected vasculitis syndromes","volume":"33","author":"Lie JT and Members and Consultants of the American College of Rheumatology Subcommittee on Classification of Vasculitis","year":"1990","journal-title":"Arthritis Rheum"},{"key":"e_1_2_1_10_2","doi-asserted-by":"publisher","DOI":"10.1002\/art.1780330803"},{"key":"e_1_2_1_11_2","doi-asserted-by":"publisher","DOI":"10.1002\/art.1780330802"},{"key":"e_1_2_1_12_2","first-page":"520","article-title":"Nosology of pulmonary vasculitides","volume":"52","author":"Lie JT","year":"1977","journal-title":"Mayo Clin Proc"},{"key":"e_1_2_1_13_2","first-page":"1","article-title":"Pulmonary angiitis and granulomatosis","volume":"108","author":"Liebow AA","year":"1973","journal-title":"Am Rev Respir Dis"},{"key":"e_1_2_1_14_2","doi-asserted-by":"publisher","DOI":"10.3949\/ccjm.56.2.199"}],"container-title":["Arthritis &amp; 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