{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,6]],"date-time":"2026-10-06T19:01:00Z","timestamp":1791313260198,"version":"4.3.1"},"reference-count":15,"publisher":"Wiley","issue":"2","license":[{"start":{"date-parts":[[2023,2,27]],"date-time":"2023-02-27T00:00:00Z","timestamp":1677456000000},"content-version":"vor","delay-in-days":26,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Clinical Case Reports"],"published-print":{"date-parts":[[2023,2]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Kyphoscoliotic Ehlers\u2013Danlos syndrome (kEDS) is a rare genetic disorder combining congenital hypotonia, congenital\/early onset and progressive kyphoscoliosis, and generalized joint hypermobility. Vascular fragility is another characteristic of the disease rarely described. We report a severe case of kEDS\u2010PLOD1 with several vascular complications leading to difficulties in disease management.<\/jats:p>","DOI":"10.1002\/ccr3.6760","type":"journal-article","created":{"date-parts":[[2023,2,27]],"date-time":"2023-02-27T12:36:42Z","timestamp":1677501402000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":8,"title":["A severe case of <scp><i>PLOD1<\/i><\/scp>\u2010related kyphoscoliotic <scp>Ehlers\u2013Danlos<\/scp> syndrome associated with several arterial and venous complications: A case report"],"prefix":"10.1002","volume":"11","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-2289-2738","authenticated-orcid":false,"given":"Malika","family":"Foy","sequence":"first","affiliation":[{"name":"AP\u2010HP, GHU Paris Saclay, H\u00f4pital Raymond Poincar\u00e9, Centre de r\u00e9f\u00e9rence des syndromes d'Ehlers\u2010Danlos non vasculaires  Garches 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