{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,27]],"date-time":"2025-11-27T14:25:11Z","timestamp":1764253511614,"version":"3.46.0"},"reference-count":15,"publisher":"Wiley","issue":"10","license":[{"start":{"date-parts":[[2023,10,10]],"date-time":"2023-10-10T00:00:00Z","timestamp":1696896000000},"content-version":"vor","delay-in-days":9,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Clinical Case Reports"],"published-print":{"date-parts":[[2023,10]]},"abstract":"<jats:title>Key Clinical Message<\/jats:title>\n                  <jats:p>Hemophagocytic lymphohistiocytosis (HLH) is a rare hematologic disease that occurs due to immune system dysfunction. Clinical manifestations of this disease are fever, increased ferritin level, cytopenia, and hemophagocytosis in the biopsy report of the bone marrow. We report a 36\u2010year\u2010old woman referred to our hospital with persistent fever, arthralgia in interphalangeal joints, and cutaneous rash on the trunk, was subsequently diagnosed as an adult\u2010onset Still's disease (AOSD), and after bone marrow aspiration, HLH was diagnosed with her.<\/jats:p>","DOI":"10.1002\/ccr3.7955","type":"journal-article","created":{"date-parts":[[2023,10,11]],"date-time":"2023-10-11T00:59:01Z","timestamp":1696985941000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":3,"title":["Hemophagocytic lymphohistiocytosis accompanying Still's disease: A case report"],"prefix":"10.1002","volume":"11","author":[{"given":"Arman","family":"Ahmadzadeh","sequence":"first","affiliation":[{"name":"Rheumatology Ward of Loghman Hakim Hospital Shahid Beheshti University of Medical Sciences  Tehran Iran"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0009-0005-4274-4432","authenticated-orcid":false,"given":"Neda","family":"Babadi","sequence":"additional","affiliation":[{"name":"Department of Adult Rheumatology, Loghman Hakim Hospital, School of Medicine Shahid Beheshti University of Medical Sciences  Tehran Iran"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6744-762X","authenticated-orcid":false,"given":"Faraneh","family":"Farsad","sequence":"additional","affiliation":[{"name":"Research Centre of Loghman Hakim Hospital Shahid Beheshti University of Medical Sciences  Tehran Iran"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Saba","family":"Babadi","sequence":"additional","affiliation":[{"name":"Department of Adult Internal Medicine Naft Grand Hospital  Ahvaz Iran"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7278-492X","authenticated-orcid":false,"given":"Shirin","family":"Assar","sequence":"additional","affiliation":[{"name":"Clinical Research Development Center, Imam Reza Hospital Kermanshah University of Medical Sciences  Kermanshah Iran"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2023,10,10]]},"reference":[{"issue":"10","key":"e_1_2_11_2_1","first-page":"1414","article-title":"Haemophagocytic syndrome in rheumatic patients. A systematic review","volume":"16","author":"Atteritano M","year":"2012","journal-title":"Eur Rev Med Pharmacol Sci"},{"key":"e_1_2_11_3_1","doi-asserted-by":"publisher","DOI":"10.3109\/s10165-004-0293-6"},{"key":"e_1_2_11_4_1","doi-asserted-by":"publisher","DOI":"10.1002\/pbc.25308"},{"key":"e_1_2_11_5_1","doi-asserted-by":"publisher","DOI":"10.1002\/pbc.21039"},{"issue":"4","key":"e_1_2_11_6_1","first-page":"377","article-title":"Hemophagocytic syndrome secondary to adult\u2010onset still's disease but very similar to lymphoma","volume":"5","author":"Zhang X\u2010H","year":"2012","journal-title":"Int J Clin Exp Pathol"},{"key":"e_1_2_11_7_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2011-03-278127"},{"key":"e_1_2_11_8_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2017-06-788349"},{"key":"e_1_2_11_9_1","doi-asserted-by":"publisher","DOI":"10.12659\/AJCR.901846"},{"key":"e_1_2_11_10_1","doi-asserted-by":"publisher","DOI":"10.1097\/MD.0b013e3181caf100"},{"key":"e_1_2_11_11_1","doi-asserted-by":"publisher","DOI":"10.1097\/MD.0000000000000451"},{"issue":"9","key":"e_1_2_11_12_1","article-title":"Hemophagocytic Lymphohistiocytosis secondary to adult\u2010onset Still's disease","volume":"13","author":"Barman B","year":"2021","journal-title":"Cureus"},{"issue":"10","key":"e_1_2_11_13_1","article-title":"An unusual presentation of adult\u2010onset Still's disease as Hemophagocytic Lymphohistiocytosis in a male patient","volume":"12","author":"Kuruvilla N","year":"2020","journal-title":"Cureus"},{"key":"e_1_2_11_14_1","doi-asserted-by":"publisher","DOI":"10.1007\/s10067-016-3178-0"},{"key":"e_1_2_11_15_1","doi-asserted-by":"publisher","DOI":"10.1186\/s13045-021-01100-7"},{"key":"e_1_2_11_16_1","doi-asserted-by":"publisher","DOI":"10.1007\/s15010-022-01786-y"}],"container-title":["Clinical Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/ccr3.7955","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,11,27]],"date-time":"2025-11-27T14:22:16Z","timestamp":1764253336000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/ccr3.7955"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,10]]},"references-count":15,"journal-issue":{"issue":"10","published-print":{"date-parts":[[2023,10]]}},"alternative-id":["10.1002\/ccr3.7955"],"URL":"https:\/\/doi.org\/10.1002\/ccr3.7955","archive":["Portico"],"relation":{},"ISSN":["2050-0904","2050-0904"],"issn-type":[{"type":"print","value":"2050-0904"},{"type":"electronic","value":"2050-0904"}],"subject":[],"published":{"date-parts":[[2023,10]]},"assertion":[{"value":"2023-05-29","order":0,"name":"received","label":"Received","group":{"name":"publication_history","label":"Publication History"}},{"value":"2023-09-12","order":2,"name":"accepted","label":"Accepted","group":{"name":"publication_history","label":"Publication History"}},{"value":"2023-10-10","order":3,"name":"published","label":"Published","group":{"name":"publication_history","label":"Publication History"}}],"article-number":"e7955"}}