{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,12]],"date-time":"2025-07-12T22:44:51Z","timestamp":1752360291096,"version":"3.40.5"},"reference-count":20,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2024,7,15]],"date-time":"2024-07-15T00:00:00Z","timestamp":1721001600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["IJU Case Reports"],"published-print":{"date-parts":[[2024,9]]},"abstract":"<jats:sec><jats:title>Introduction<\/jats:title><jats:p>Paraneoplastic syndromes are frequent in patients with renal cell carcinoma. Dermatomyositis is an idiopathic inflammatory myopathy that may be associated with neoplasms. This case aims to describe the rare association of dermatomyositis with renal cell carcinoma and to increase clinical suspicion of this neoplasm when systemic rheumatologic symptoms are present.<\/jats:p><\/jats:sec><jats:sec><jats:title>Case presentation<\/jats:title><jats:p>A 35\u2010year\u2010old female developed severe rheumatologic symptoms (progressive muscle weakness, heliotrope rash, and Gottron's papules). Clinical and laboratory findings indicated dermatomyositis. During the investigation, computed tomography revealed a left kidney solid mass. She underwent a left radical nephrectomy, and histology confirmed renal cell carcinoma. After 3\u2009months, dermatomyositis manifestations disappeared and the patient withdrawn steroid therapy.<\/jats:p><\/jats:sec><jats:sec><jats:title>Conclusion<\/jats:title><jats:p>Most paraneoplastic syndromes associated with renal cell carcinoma are only cured with nephrectomy. We highlight the potential role of surgery in dermatomyositis caused by renal cell carcinoma. The recurrence of symptoms related to the syndrome should alert for disease progression.<\/jats:p><\/jats:sec>","DOI":"10.1002\/iju5.12754","type":"journal-article","created":{"date-parts":[[2024,7,15]],"date-time":"2024-07-15T11:44:50Z","timestamp":1721043890000},"page":"359-363","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":1,"title":["Dermatomyositis in a young patient: A rare paraneoplastic syndrome of renal cell carcinoma"],"prefix":"10.1002","volume":"7","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-5918-8621","authenticated-orcid":false,"given":"Margarida","family":"Andr\u00e9","sequence":"first","affiliation":[{"name":"Urology Department Hospital Garcia de Orta EPE  Almada Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Alexandre","family":"Macedo","sequence":"additional","affiliation":[{"name":"Urology Department Hospital Garcia de Orta EPE  Almada Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Vanessa","family":"Metrogos","sequence":"additional","affiliation":[{"name":"Urology Department Instituto Portugu\u00eas de Oncologia de Lisboa  Lisbon Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Lu\u00edsa","family":"Moreira","sequence":"additional","affiliation":[{"name":"Urology Department Hospital Garcia de Orta EPE  Almada Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jos\u00e9","family":"Pereira","sequence":"additional","affiliation":[{"name":"Radiology Department Hospital Garcia de Orta EPE  Almada Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nuno","family":"Figueira","sequence":"additional","affiliation":[{"name":"Urology Department Hospital Garcia de Orta EPE  Almada Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jo\u00e3o Paulo","family":"Rosa","sequence":"additional","affiliation":[{"name":"Urology Department Hospital Garcia de Orta EPE  Almada Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Miguel","family":"Carvalho","sequence":"additional","affiliation":[{"name":"Urology Department Hospital Garcia de Orta EPE  Almada Portugal"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2024,7,15]]},"reference":[{"key":"e_1_2_12_2_1","first-page":"163","article-title":"Paraneoplastic syndromes in urologic malignancy: the many faces of renal cell carcinoma","volume":"4","author":"Palapattu GS","year":"2002","journal-title":"Rev. Urol."},{"key":"e_1_2_12_3_1","doi-asserted-by":"publisher","DOI":"10.1001\/archdermatol.2009.328"},{"key":"e_1_2_12_4_1","doi-asserted-by":"publisher","DOI":"10.1136\/annrheumdis-2013-205127"},{"key":"e_1_2_12_5_1","doi-asserted-by":"publisher","DOI":"10.3899\/jrheum.140566"},{"key":"e_1_2_12_6_1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM197502132920706"},{"key":"e_1_2_12_7_1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM197502202920807"},{"key":"e_1_2_12_8_1","doi-asserted-by":"publisher","DOI":"10.1159\/000224860"},{"key":"e_1_2_12_9_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00345-016-1793-7"},{"key":"e_1_2_12_10_1","doi-asserted-by":"publisher","DOI":"10.4103\/aian.aian_748_22"},{"key":"e_1_2_12_11_1","first-page":"421","article-title":"Paraneoplastic cardiac involvement in renal cell carcinoma with dermatomyositis sine dermatitis","volume":"17","author":"Kyaw H","year":"2017","journal-title":"Ochsner J."},{"key":"e_1_2_12_12_1","doi-asserted-by":"publisher","DOI":"10.1136\/bcr-2015-212387"},{"key":"e_1_2_12_13_1","doi-asserted-by":"publisher","DOI":"10.5489\/cuaj.2362"},{"key":"e_1_2_12_14_1","doi-asserted-by":"publisher","DOI":"10.4103\/0974-7796.120302"},{"key":"e_1_2_12_15_1","doi-asserted-by":"publisher","DOI":"10.1097\/01.RVI.0000114833.75873.25"},{"key":"e_1_2_12_16_1","doi-asserted-by":"publisher","DOI":"10.1007\/s11926-002-0087-9"},{"key":"e_1_2_12_17_1","first-page":"1855","article-title":"The overall and temporal association of cancer with polymyositis and dermatomyositis","volume":"21","author":"Zantos D","year":"1994","journal-title":"J. Rheumatol."},{"key":"e_1_2_12_18_1","doi-asserted-by":"publisher","DOI":"10.5114\/reum.2015.51510"},{"key":"e_1_2_12_19_1","doi-asserted-by":"publisher","DOI":"10.1097\/01.bor.0000245721.02512.77"},{"key":"e_1_2_12_20_1","doi-asserted-by":"publisher","DOI":"10.1186\/s13075-017-1469-8"},{"key":"e_1_2_12_21_1","doi-asserted-by":"publisher","DOI":"10.1097\/MD.0000000000009639"}],"container-title":["IJU Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/iju5.12754","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,9,2]],"date-time":"2024-09-02T00:27:22Z","timestamp":1725236842000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/iju5.12754"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,7,15]]},"references-count":20,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2024,9]]}},"alternative-id":["10.1002\/iju5.12754"],"URL":"https:\/\/doi.org\/10.1002\/iju5.12754","archive":["Portico"],"relation":{},"ISSN":["2577-171X","2577-171X"],"issn-type":[{"type":"print","value":"2577-171X"},{"type":"electronic","value":"2577-171X"}],"subject":[],"published":{"date-parts":[[2024,7,15]]},"assertion":[{"value":"2024-01-02","order":0,"name":"received","label":"Received","group":{"name":"publication_history","label":"Publication History"}},{"value":"2024-06-04","order":2,"name":"accepted","label":"Accepted","group":{"name":"publication_history","label":"Publication History"}},{"value":"2024-07-15","order":3,"name":"published","label":"Published","group":{"name":"publication_history","label":"Publication History"}}]}}