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There has been an increasing number of <jats:styled-content style=\"fixed-case\">BA<\/jats:styled-content>\u2010related publications, which may challenge researchers to determine their actual scientific value. This study aimed to evaluate the global research activity and developments relating to <jats:styled-content style=\"fixed-case\">BA<\/jats:styled-content> using a combination of scientometric methodologies and visualization tools. A comprehensive search strategy for the Web of Science\u2122 database was designed to obtain bibliographic data on scientific <jats:styled-content style=\"fixed-case\">BA<\/jats:styled-content> publications for the timespan 1900\u20132018. Research output of countries, institutions, individual authors and collaborative networks was analyzed. Semi\u2010qualitative research measures including citation rate and <jats:italic>h<\/jats:italic>\u2010index were assessed. Choropleth mapping and network diagrams were used to visualize results. In total, 4,459 publications on <jats:styled-content style=\"fixed-case\">BA<\/jats:styled-content> were identified (88.5% in English), originating from 63 countries. The largest number was published by the <jats:styled-content style=\"fixed-case\">USA<\/jats:styled-content> (<jats:italic>n\u00a0<\/jats:italic>=<jats:italic>\u00a0<\/jats:italic>991; 22.2%), Japan (<jats:italic>n\u00a0<\/jats:italic>=<jats:italic>\u00a0<\/jats:italic>667; 15.0%) and the <jats:styled-content style=\"fixed-case\">UK<\/jats:styled-content> (<jats:italic>n\u00a0<\/jats:italic>=<jats:italic>\u00a0<\/jats:italic>294; 6.6%). The <jats:styled-content style=\"fixed-case\">USA<\/jats:styled-content> combined the highest number of cooperation articles (<jats:italic>n\u00a0<\/jats:italic>=<jats:italic>\u00a0<\/jats:italic>140). The most productive collaborative network was established between the <jats:styled-content style=\"fixed-case\">USA<\/jats:styled-content> and Canada (<jats:italic>n\u00a0<\/jats:italic>=<jats:italic>\u00a0<\/jats:italic>17). Scientific papers from the <jats:styled-content style=\"fixed-case\">UK<\/jats:styled-content> received the highest average citation rate (16.7), whereas the <jats:styled-content style=\"fixed-case\">USA<\/jats:styled-content> had the highest country\u2010specific <jats:italic>h<\/jats:italic>\u2010index (59). Eighty\u2010eight (2.0%) items were published under the auspices of multicenter consortiums and registries. The most productive institutions and authors were based in the <jats:styled-content style=\"fixed-case\">USA<\/jats:styled-content>, the <jats:styled-content style=\"fixed-case\">UK<\/jats:styled-content>, Japan, France, Canada and Taiwan. <jats:styled-content style=\"fixed-case\">BA<\/jats:styled-content>\u2010related research has constantly been progressing, becoming more multidisciplinary but with main research endeavors concentrated in a few high\u2010income countries. Studies into pathogenesis of <jats:styled-content style=\"fixed-case\">BA<\/jats:styled-content> remain uncommon, but are sorely needed to foster true scientific progress with this rare disease. Hence, international collaborative and translational research should be strengthened to allow further evolution in this field.<\/jats:p>","DOI":"10.1002\/jhbp.628","type":"journal-article","created":{"date-parts":[[2019,4,13]],"date-time":"2019-04-13T04:37:17Z","timestamp":1555130237000},"page":"201-210","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":11,"title":["Biliary atresia: a scientometric analysis of the global research architecture and scientific developments"],"prefix":"10.1002","volume":"26","author":[{"given":"Florian","family":"Friedmacher","sequence":"first","affiliation":[{"name":"Department of Pediatric Surgery King's College Hospital Denmark Hill London SE5 9RS UK"},{"name":"Department of Pediatric Surgery The Royal London Hospital London UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kathryn","family":"Ford","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery King's College Hospital Denmark Hill London SE5 9RS UK"},{"name":"Department of Specialist Neonatal and Pediatric Surgery Great Ormond Street Hospital London UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mark","family":"Davenport","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery King's College Hospital Denmark Hill London SE5 9RS 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