{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,31]],"date-time":"2026-08-31T23:26:25Z","timestamp":1788218785675,"version":"build-2803163510"},"reference-count":24,"publisher":"Wiley","issue":"9","license":[{"start":{"date-parts":[[2020,8,15]],"date-time":"2020-08-15T00:00:00Z","timestamp":1597449600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["J Hepato Biliary Pancreat"],"published-print":{"date-parts":[[2020,9]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:sec><jats:title>Background\/Purpose<\/jats:title><jats:p>Epidemiological data on immunoglobulin G4\u2010related sclerosing cholangitis (IgG4\u2010SC) are scarce.<\/jats:p><\/jats:sec><jats:sec><jats:title>Method<\/jats:title><jats:p>We randomly selected healthcare facilities from a list of all facilities in Japan. The selection rate was determined according to a stratification based on the facility characteristics and scale. We sent questionnaires to the selected facilities enquiring about the number and sex of patients with IgG4\u2010SC in 2018. Among responding facilities, we further inquired about the clinical characteristics of the patients with IgG4\u2010SC.<\/jats:p><\/jats:sec><jats:sec><jats:title>Results<\/jats:title><jats:p>We selected 1180 departments from health centers across Japan. Of them, 532 (45.1%) responded to the questionnaires. The number of reported patients with IgG4\u2010SC was 1045, and the estimated point prevalence was 2.18 (95% confidence interval, 2.13\u20102.23) per 100\u00a0000 population. In addition, we enrolled 1096 patients with IgG4\u2010SC, combining data from previously and newly registered patients. Male patients comprised 79.5% of the population and patients aged 60\u201380\u00a0years had the highest risk for developing the disease. The follow\u2010up period was 5.1\u00a0\u00b1\u00a04.0\u00a0years and the 5\u2010 and 10\u2010year overall survival rates were 95.3% and 89.0%, respectively.<\/jats:p><\/jats:sec><jats:sec><jats:title>Conclusions<\/jats:title><jats:p>The point prevalence of IgG4\u2010SC was 2.18 per 100\u00a0000 population. The epidemiological features were similar to those observed in previous studies.<\/jats:p><\/jats:sec>","DOI":"10.1002\/jhbp.793","type":"journal-article","created":{"date-parts":[[2020,6,30]],"date-time":"2020-06-30T18:18:22Z","timestamp":1593541102000},"page":"598-603","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":35,"title":["Epidemiological features of immunoglobulin G4\u2010related sclerosing cholangitis in Japan"],"prefix":"10.1002","volume":"27","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-6358-5283","authenticated-orcid":false,"given":"Atsushi","family":"Tanaka","sequence":"first","affiliation":[{"name":"Department of Medicine Teikyo University School of Medicine Tokyo Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mitsuru","family":"Mori","sequence":"additional","affiliation":[{"name":"Hokkaido Chitose College of Rehabilitation Chitose Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6767-0410","authenticated-orcid":false,"given":"Kensuke","family":"Kubota","sequence":"additional","affiliation":[{"name":"Department of Endoscopy Yokohama City University Hospital Yokohama Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Itaru","family":"Naitoh","sequence":"additional","affiliation":[{"name":"Department of Gastroenterology Nagoya City University Graduate School of Medical Sciences Nagoya Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Takahiro","family":"Nakazawa","sequence":"additional","affiliation":[{"name":"Department of Gastroenterology Nagoya City University Graduate School of Medical Sciences Nagoya Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hajime","family":"Takikawa","sequence":"additional","affiliation":[{"name":"Faculty of Medical Technology Teikyo University Tokyo Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2145-6416","authenticated-orcid":false,"given":"Michiaki","family":"Unno","sequence":"additional","affiliation":[{"name":"Division of Hepato\u2010Biliary Pancreatic Surgery Tohoku University Graduate School, of Medicine Sendai Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Terumi","family":"Kamisawa","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine Tokyo Metropolitan Komagome Hospital Tokyo Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shigeyuki","family":"Kawa","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine Matsumoto Dental University Matsumoto Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kazuichi","family":"Okazaki","sequence":"additional","affiliation":[{"name":"The Third Department of Internal Medicine Kansai Medical University Hirakata Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2020,8,15]]},"reference":[{"key":"e_1_2_7_2_1","doi-asserted-by":"publisher","DOI":"10.1002\/jhbp.596"},{"key":"e_1_2_7_3_1","doi-asserted-by":"publisher","DOI":"10.1038\/modpathol.2012.72"},{"key":"e_1_2_7_4_1","doi-asserted-by":"publisher","DOI":"10.1002\/art.39132"},{"key":"e_1_2_7_5_1","doi-asserted-by":"publisher","DOI":"10.1002\/art.34593"},{"key":"e_1_2_7_6_1","doi-asserted-by":"publisher","DOI":"10.3109\/s10165-011-0508-6"},{"key":"e_1_2_7_7_1","doi-asserted-by":"publisher","DOI":"10.3109\/s10165-011-0571-z"},{"key":"e_1_2_7_8_1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM200103083441005"},{"key":"e_1_2_7_9_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00535-003-1175-y"},{"key":"e_1_2_7_10_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00535-012-0744-3"},{"key":"e_1_2_7_11_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00535-006-1868-0"},{"key":"e_1_2_7_12_1","doi-asserted-by":"publisher","DOI":"10.1097\/MPA.0000000000000325"},{"key":"e_1_2_7_13_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1872-034X.2007.00235.x"},{"key":"e_1_2_7_14_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1572-0241.2007.01040_8.x"},{"key":"e_1_2_7_15_1","doi-asserted-by":"publisher","DOI":"10.1053\/j.gastro.2007.12.009"},{"key":"e_1_2_7_16_1","doi-asserted-by":"publisher","DOI":"10.1038\/ajg.2014.223"},{"key":"e_1_2_7_17_1","doi-asserted-by":"publisher","DOI":"10.1002\/jhbp.50"},{"key":"e_1_2_7_18_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.cgh.2016.12.038"},{"key":"e_1_2_7_19_1","unstructured":"NakamuraYandDiseases. 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