{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,1]],"date-time":"2025-11-01T12:53:38Z","timestamp":1762001618636,"version":"3.33.0"},"reference-count":14,"publisher":"Ovid Technologies (Wolters Kluwer Health)","issue":"10","license":[{"start":{"date-parts":[[2015,9,1]],"date-time":"2015-09-01T00:00:00Z","timestamp":1441065600000},"content-version":"tdm","delay-in-days":3622,"URL":"http:\/\/doi.wiley.com\/10.1002\/tdm_license_1.1"}],"content-domain":{"domain":["lww.com","ovid.com"],"crossmark-restriction":true},"short-container-title":[],"published-print":{"date-parts":[[2005,10]]},"abstract":"<jats:sec>\n            <jats:title\/>\n            <jats:p>\n                                 <jats:bold>Congenital absence of the portal vein (CAPV) is a rare malformation of the splanchnic venous system. Although CAPV is usually detected in the pediatric age group, our patient was a 35-year-old woman. She had been diagnosed with CAPV in 1996 when she was 27 years old. In 1998, she was placed on hemodialysis due to chronic renal failure. After several episodes of encephalopathy in 2002, liver transplantation (LT) was recommended to her and her family. Since there was no suitable living donor candidate, she was put on the waiting list for a deceased donor liver transplant in Japan. In 2004, her ammonia level increased to around 300 \u03bcg\/dl, and she went into a coma lasting for three days. After recovering from this event, she underwent a living domino transplantation using a whole liver donated by a familial amyloid polyneuropathy (FAP) patient. Her portal vein, which had drained directly into the inferior vena cava (IVC), was transected together with a cuff of the IVC wall and anastomosed to the graft liver portal vein in an end-to-end fashion. In conclusion, liver transplantation proved to be a safe and effective way to save this patient and improve her quality of life.<\/jats:bold>\n                              <\/jats:p>\n          <\/jats:sec>","DOI":"10.1002\/lt.20561","type":"journal-article","created":{"date-parts":[[2005,9,23]],"date-time":"2005-09-23T18:17:34Z","timestamp":1127499454000},"page":"1285-1288","update-policy":"https:\/\/doi.org\/10.1097\/lww.0000000000001000","source":"Crossref","is-referenced-by-count":14,"title":["Living Domino Liver Transplantation in an Adult With Congenital Absence of Portal Vein"],"prefix":"10.1097","volume":"11","author":[{"given":"Takayuki","family":"Takeichi","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hideaki","family":"Okajima","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hiroko","family":"Suda","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Shintarou","family":"Hayashida","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hironori","family":"Iwasaki","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Manuel Zeledon","family":"Ramirez","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mikako","family":"Ueno","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Katsuhiro","family":"Asonuma","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yukihiro","family":"Inomata","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"276","reference":[{"key":"R1-23-20250124","first-page":"295","article-title":"Account of two instances of uncommon formation in the viscera of the human body.","volume":"83","author":"Abernethy","year":"1793","journal-title":"Philos Trans R Soc Lond B Biol Sci"},{"key":"R2-23-20250124","first-page":"711","article-title":"The anatomy and physiology of the liver.","volume":"123","author":"Kiernan","year":"1833","journal-title":"Philos Trans R Soc Lond B Biol Sci"},{"key":"R3-23-20250124","first-page":"475","article-title":"Successful hepatic transplantation in congenital absence of recipent portal vein.","volume":"107","author":"Woodle","year":"1990","journal-title":"Surgery"},{"key":"R4-23-20250124","doi-asserted-by":"crossref","first-page":"1026","DOI":"10.1053\/jpsu.2001.24731","article-title":"Congenital absence of the portal vein and role of liver transplantation in children.","volume":"36","author":"Shinkai","year":"2001","journal-title":"J Pediatr Surg"},{"key":"R5-23-20250124","doi-asserted-by":"crossref","first-page":"1203","DOI":"10.1002\/lt.20170","article-title":"Orthotopic liver transplantation for porto systemic encephalopathy in an adult with congenital absence of the portal vein.","volume":"10","author":"Wojcicki","year":"2004","journal-title":"Liver Transpl"},{"key":"R6-23-20250124","doi-asserted-by":"crossref","first-page":"258","DOI":"10.1097\/00007890-200001270-00011","article-title":"Right lobe graft in living donor liver transplantation.","volume":"69","author":"Inomata","year":"2000","journal-title":"Transplantation"},{"key":"R7-23-20250124","doi-asserted-by":"crossref","first-page":"681","DOI":"10.1097\/00004728-200209000-00003","article-title":"Congenital absence of the portal vein: clinical and radiologic findings.","volume":"26","author":"Niwa","year":"2002","journal-title":"J Comput Assist Tomogr"},{"key":"R8-23-20250124","doi-asserted-by":"crossref","first-page":"608","DOI":"10.1007\/s004310050892","article-title":"Elevated galactose in newborn screening due to congenital absence of the portal vein.","volume":"157","author":"Kim","year":"1998","journal-title":"Eur J Pediatr"},{"key":"R9-23-20250124","doi-asserted-by":"crossref","first-page":"425","DOI":"10.1016\/S0387-7604(99)00049-2","article-title":"Subclinical portal-systemic encephalopathy in a child with congenital absence of portal vein.","volume":"21","author":"Wakamoto","year":"1999","journal-title":"Brain Dev"},{"key":"R10-23-20250124","first-page":"55","article-title":"2nd. 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