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Maternally transmitted very large trinucleotide repeats (&gt;100) are extremely rare in juvenile HD and may represent instability during female gametogenesis. \u00a9 2005 Movement Disorder Society<\/jats:p>","DOI":"10.1002\/mds.20557","type":"journal-article","created":{"date-parts":[[2005,7,8]],"date-time":"2005-07-08T16:32:39Z","timestamp":1120840359000},"page":"1380-1383","source":"Crossref","is-referenced-by-count":14,"title":["Case of maternally transmitted juvenile Huntington's disease with a very large trinucleotide 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