{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,11]],"date-time":"2026-07-11T12:54:22Z","timestamp":1783774462647,"version":"3.55.0"},"reference-count":17,"publisher":"Wiley","issue":"1","license":[{"start":{"date-parts":[[2005,8,17]],"date-time":"2005-08-17T00:00:00Z","timestamp":1124236800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Movement Disorders"],"published-print":{"date-parts":[[2006,1]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Hallervorden\u2013Spatz disease (HSD) is a rare disorder characterized by progressive motor dysfunction and dementia. Dystonia is the most prominent and disabling symptom, responding only to a modest extent to pharmacological therapy. At the moment, only a few cases have been reported to improve dystonia and even fewer to resolve status dystonicus for a longer period in children. The authors present the case of a 10\u2010year\u2010old boy who had progressive generalized dystonia, resulting in spontaneous femur fracture and life\u2010threatening swallowing and respiratory disability. As a rescue solution, staged bilateral pallidothalamotomy was performed. Postoperatively, Burke\u2013Fahn\u2013Marsden Dystonia Rating Scale and Dystonia Disability Rating Scale improved (from 116 and 30 points to 41 and 18 points, respectively) and painful dystonia was resolved, which was still continuous 4 years later (47 and 20 points). Stereotactic staged bilateral pallidothalamotomy should be considered as a potential treatment in the management of life\u2010threatening generalized dystonia related to HSD. \u00a9 2005 Movement Disorder Society<\/jats:p>","DOI":"10.1002\/mds.20655","type":"journal-article","created":{"date-parts":[[2005,8,17]],"date-time":"2005-08-17T13:47:14Z","timestamp":1124286434000},"page":"82-85","source":"Crossref","is-referenced-by-count":55,"title":["Staged bilateral stereotactic pallidothalamotomy for life\u2010threatening dystonia in a child with Hallervorden\u2013Spatz disease"],"prefix":"10.1002","volume":"21","author":[{"given":"Istvan","family":"Balas","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Norbert","family":"Kovacs","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Katalin","family":"Hollody","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2005,8,17]]},"reference":[{"key":"e_1_2_5_2_2","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1991.00530240091029"},{"key":"e_1_2_5_3_2","doi-asserted-by":"publisher","DOI":"10.1007\/BF00588145"},{"key":"e_1_2_5_4_2","doi-asserted-by":"publisher","DOI":"10.3171\/jns.1999.90.3.0551"},{"key":"e_1_2_5_5_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0387-7604(12)80246-4"},{"key":"e_1_2_5_6_2","doi-asserted-by":"publisher","DOI":"10.3171\/jns.2004.101.2.0189"},{"key":"e_1_2_5_7_2","first-page":"309","article-title":"Off\u2010period dystonia in Parkinson's disease but not generalized dystonia is improved by high\u2010frequency stimulation of the subthalamic nucleus","volume":"94","author":"Detante O","year":"2004","journal-title":"Adv Neurol"},{"key":"e_1_2_5_8_2","doi-asserted-by":"publisher","DOI":"10.1002\/ana.410240519"},{"key":"e_1_2_5_9_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.35.1.73"},{"key":"e_1_2_5_10_2","doi-asserted-by":"publisher","DOI":"10.1002\/1531-8257(199911)14:6<1057::AID-MDS1034>3.0.CO;2-1"},{"key":"e_1_2_5_11_2","doi-asserted-by":"publisher","DOI":"10.1097\/00006123-200104000-00025"},{"key":"e_1_2_5_12_2","first-page":"52","article-title":"Treatment of dystonic syndromes by chronic electrical stimulation of the internal globus pallidus","volume":"47","author":"Cif L","year":"2003","journal-title":"J Neurosurg Sci"},{"key":"e_1_2_5_13_2","doi-asserted-by":"publisher","DOI":"10.1002\/mds.10380"},{"key":"e_1_2_5_14_2","doi-asserted-by":"publisher","DOI":"10.1002\/mds.1250"},{"key":"e_1_2_5_15_2","doi-asserted-by":"publisher","DOI":"10.3171\/jns.2004.100.4.0706"},{"key":"e_1_2_5_16_2","doi-asserted-by":"publisher","DOI":"10.1007\/s004150170116"},{"key":"e_1_2_5_17_2","first-page":"231","article-title":"Treatment of intractable generalized dystonia by bilateral posteroventral pallidotomy: one\u2010year results","volume":"64","author":"Lin JJ","year":"2001","journal-title":"Zhonghua Yi Xue Za Zhi (Taipei)"},{"key":"e_1_2_5_18_2","doi-asserted-by":"publisher","DOI":"10.1002\/ana.10474"}],"container-title":["Movement Disorders"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Fmds.20655","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/movementdisorders.onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/mds.20655","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,10,20]],"date-time":"2025-10-20T14:19:13Z","timestamp":1760969953000},"score":1,"resource":{"primary":{"URL":"https:\/\/movementdisorders.onlinelibrary.wiley.com\/doi\/10.1002\/mds.20655"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2005,8,17]]},"references-count":17,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2006,1]]}},"alternative-id":["10.1002\/mds.20655"],"URL":"https:\/\/doi.org\/10.1002\/mds.20655","archive":["Portico"],"relation":{},"ISSN":["0885-3185","1531-8257"],"issn-type":[{"value":"0885-3185","type":"print"},{"value":"1531-8257","type":"electronic"}],"subject":[],"published":{"date-parts":[[2005,8,17]]}}}