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In view of the growing list of recognized disorders and recent advances in genetics, we review the autosomal recessive forms of dystonia parkinsonism, summarizing clinical presentations, results of investigations, and response to treatment of gene\u2010proven cases. We concentrate on <jats:italic>PANK2<\/jats:italic>\u2010, <jats:italic>PLA2G6<\/jats:italic>\u2010, <jats:italic>ATP13A2<\/jats:italic>\u2010, <jats:italic>FBX07<\/jats:italic>, <jats:italic>TAF1<\/jats:italic>\u2010, and <jats:italic>PRKRA<\/jats:italic>\u2010associated neurodegeneration. <jats:italic>Parkin<\/jats:italic>, <jats:italic>PINK1<\/jats:italic>, and <jats:italic>DJ\u20101<\/jats:italic> are also briefly reviewed. \u00a9 2009 Movement Disorder Society<\/jats:p>","DOI":"10.1002\/mds.22314","type":"journal-article","created":{"date-parts":[[2009,1,30]],"date-time":"2009-01-30T16:38:51Z","timestamp":1233333531000},"page":"490-499","source":"Crossref","is-referenced-by-count":69,"title":["Complicated recessive dystonia parkinsonism syndromes"],"prefix":"10.1002","volume":"24","author":[{"given":"Susanne A.","family":"Schneider","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kailash 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