{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,23]],"date-time":"2026-08-23T14:53:26Z","timestamp":1787496806493,"version":"build-2736575974"},"reference-count":20,"publisher":"Wiley","issue":"6","license":[{"start":{"date-parts":[[2013,5,16]],"date-time":"2013-05-16T00:00:00Z","timestamp":1368662400000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Movement Disorders"],"published-print":{"date-parts":[[2013,6]]},"abstract":"<jats:title>ABSTRACT<\/jats:title>\n                  <jats:sec>\n                    <jats:title>Background<\/jats:title>\n                    <jats:p>Hereditary sensory and autonomic neuropathy type III features marked ataxic gait that progressively worsens over time. We assessed whether proprioceptive disturbances can explain the ataxia.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Methods<\/jats:title>\n                    <jats:p>Proprioception at the knee joint was assessed using passive joint angle matching in 18 patients and 14 age\u2010matched controls; 5 patients with cerebellar ataxia were also studied. Ataxia was quantified using the Brief Ataxia Rating Score, which ranged from 7 to 26 of 30.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Results<\/jats:title>\n                    <jats:p>Neuropathy patients performed poorly in judging joint position: mean absolute error was 8.7\u00b0\u2009\u00b1\u20091.0\u00b0, and the range was very wide (2.8\u00b0\u201318.1\u00b0); conversely, absolute error was only 2.7\u00b0\u2009\u00b1\u20090.3\u00b0 (1.6\u00b0\u20135.5\u00b0) in the controls and 3.0\u00b0\u2009\u00b1\u20090.2\u00b0 (2.1\u00b0\u20133.4\u00b0) in the cerebellar patients. This error was positively correlated to the degree of ataxia in the neuropathy patients but not the cerebellar patients.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusions<\/jats:title>\n                    <jats:p>\n                      These results suggest that poor proprioceptive acuity at the knee joint is a major contributor to the ataxic gait associated with hereditary sensory and autonomic neuropathy type III. \u00a9 2013\n                      <jats:italic>Movement<\/jats:italic>\n                      Disorder Society\n                    <\/jats:p>\n                  <\/jats:sec>","DOI":"10.1002\/mds.25482","type":"journal-article","created":{"date-parts":[[2013,5,16]],"date-time":"2013-05-16T14:49:48Z","timestamp":1368715788000},"page":"823-827","source":"Crossref","is-referenced-by-count":30,"title":["Relationship between proprioception at the knee joint and gait ataxia in HSAN III"],"prefix":"10.1002","volume":"28","author":[{"given":"Vaughan G.","family":"Macefield","sequence":"first","affiliation":[{"name":"School of Medicine University of Western Sydney Sydney Australia"},{"name":"Neuroscience Research Australia Sydney Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Lucy J.","family":"Norcliffe\u2010Kaufmann","sequence":"additional","affiliation":[{"name":"Dysautonomia Center NYU Langone Medical Center New York New York USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Felicia B.","family":"Axelrod","sequence":"additional","affiliation":[{"name":"Dysautonomia Center NYU Langone Medical Center New York New York USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Horacio","family":"Kaufmann","sequence":"additional","affiliation":[{"name":"Dysautonomia Center NYU Langone Medical Center New York New York USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2013,5,16]]},"reference":[{"key":"e_1_2_7_2_1","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1971.00480320034003"},{"key":"e_1_2_7_3_1","doi-asserted-by":"publisher","DOI":"10.1016\/0022-510X(70)90083-3"},{"key":"e_1_2_7_4_1","doi-asserted-by":"publisher","DOI":"10.1007\/BF02291353"},{"key":"e_1_2_7_5_1","doi-asserted-by":"publisher","DOI":"10.1002\/mds.22681"},{"key":"e_1_2_7_6_1","doi-asserted-by":"publisher","DOI":"10.1038\/nrn1953"},{"key":"e_1_2_7_7_1","doi-asserted-by":"publisher","DOI":"10.1152\/jn.1993.70.5.1853"},{"key":"e_1_2_7_8_1","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/117.6.1433"},{"key":"e_1_2_7_9_1","doi-asserted-by":"publisher","DOI":"10.1002\/mds.870070202"},{"key":"e_1_2_7_10_1","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/awr168"},{"key":"e_1_2_7_11_1","doi-asserted-by":"crossref","first-page":"1060","DOI":"10.1542\/peds.38.6.1060","article-title":"Nerves 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