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This review elaborates the expanded phenomenology, including oculomotor apraxia and immunodeficiency, and estimates the presence of each movement disorder feature from previously reported literature. Initial manifestations of Ataxia\u2010telangiectasia include cerebellar symptoms (67%), dystonia (18%), choreoathetosis (10%), and tremor (4%), with parkinsonism and myoclonus not reported as initial features. The prevalence of movement disorders during the course of the disease includes cerebellar symptoms (96%), dystonia (89%), parkinsonism (41%), choreoathetosis (89%), myoclonus (92%), and tremor (74%). Phenomenology and age of onset is modulated by presence of residual <jats:italic>ATM<\/jats:italic> kinase activity, with genotypes heavily truncating the ATM protein associated with the most severe phenotypes. Ataxia\u2010telangiectasia commonly results in a spectrum of movement disorders beyond ataxia and telangiectasias. \u00a9 2018 International Parkinson and Movement Disorder Society<\/jats:p>","DOI":"10.1002\/mds.27319","type":"journal-article","created":{"date-parts":[[2018,2,13]],"date-time":"2018-02-13T05:43:27Z","timestamp":1518500607000},"page":"1238-1247","source":"Crossref","is-referenced-by-count":100,"title":["Ataxia\u2010telangiectasia: A review of movement disorders, clinical features, and genotype correlations"],"prefix":"10.1002","volume":"33","author":[{"given":"Ariel","family":"Levy","sequence":"first","affiliation":[{"name":"Edmond J Safra Program in Parkinson's Disease, Toronto Western Hospital Toronto Ontario Canada"},{"name":"Morton and Gloria Shulman Movement Disorders Clinic Toronto Ontario Canada"},{"name":"Department of Neuroscience, Faculty of Medicine Universit\u00e9 de Montr\u00e9al, Montreal Quebec 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