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The identified rating scales and functional ability tests were reviewed and ranked by the panel as \u201crecommended,\u201d \u201csuggested,\u201d or \u201clisted\u201d for the assessment of patients with discrete cerebellar disorders, using previously established criteria.<\/jats:p><\/jats:sec><jats:sec><jats:title>Results<\/jats:title><jats:p>We reviewed 14 instruments (9 rating scales and 5 functional tests). \u201cRecommended\u201d rating scales for the assessment of symptoms severity were: for Friedreich's ataxia, the Friedreich's Ataxia Rating Scale, the International Cooperative Ataxia Rating Scale (ICARS), and the Scale for the Assessment and Rating of Ataxia (SARA); for spinocerebellar ataxias, ICARS and SARA; for ataxia telangiectasia: ICARS and SARA; for brain tumors, SARA; for congenital disorder of glycosylation\u2010phosphomannomutase\u20102 deficiency, ICARS; for cerebellar symptoms in multiple sclerosis, ICARS; for cerebellar symptoms in multiple system atrophy: Unified Multiple System Atrophy Rating Scale and ICARS; and for fragile X\u2013associated tremor ataxia syndrome, ICARS. \u201cRecommended\u201d functional tests were: for Friedreich's ataxia, Ataxia Functional Composite Score and Composite Cerebellar Functional Severity Score; and for spinocerebellar ataxias, Ataxia Functional Composite Score, Composite Cerebellar Functional Severity Score, and SCA Functional Index.<\/jats:p><\/jats:sec><jats:sec><jats:title>Conclusions<\/jats:title><jats:p>We identified some \u201crecommended\u201d scales and functional tests for the assessment of patients with major hereditary ataxias and other cerebellar disorders. The main limitations of these instruments include the limited assessment of patients in the more severe end of the spectrum and children. Further research in these populations is warranted. \u00a9 2020 International Parkinson and Movement Disorder Society<\/jats:p><\/jats:sec>","DOI":"10.1002\/mds.28313","type":"journal-article","created":{"date-parts":[[2020,10,6]],"date-time":"2020-10-06T13:51:56Z","timestamp":1601992316000},"page":"283-297","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":97,"title":["Assessment of Ataxia Rating Scales and Cerebellar Functional Tests: Critique and Recommendations"],"prefix":"10.1002","volume":"36","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-9069-6512","authenticated-orcid":false,"given":"Santiago","family":"Perez\u2010Lloret","sequence":"first","affiliation":[{"name":"National Research Council (CAECIHS\u2010UAI, CONICET)  Buenos Aires Argentina"},{"name":"Faculty of Medicine Pontifical Catholic University of Argentina  Buenos Aires Argentina"},{"name":"Department of Physiology, Faculty of Medicine University of Buenos Aires  Buenos Aires Argentina"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Bart","family":"van de Warrenburg","sequence":"additional","affiliation":[{"name":"Donders Institute for Brain, Cognition and Behavior, Department of Neurology Center of Expertise for Parkinson and Movement Disorders, Radboud University Medical Center  Nijmegen the Netherlands"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3383-8566","authenticated-orcid":false,"given":"Malco","family":"Rossi","sequence":"additional","affiliation":[{"name":"Movement Disorders Section, Raul Carrea Institute for Neurological Research  Buenos Aires Argentina"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3829-0675","authenticated-orcid":false,"given":"Carmen","family":"Rodr\u00edguez\u2010Bl\u00e1zquez","sequence":"additional","affiliation":[{"name":"National Centre of Epidemiology Institute of Health Carlos III and CIBERNED  Madrid Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Theresa","family":"Zesiewicz","sequence":"additional","affiliation":[{"name":"Department of Neurology University of South Florida  Tampa Florida USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jonas A.M.","family":"Saute","sequence":"additional","affiliation":[{"name":"Medical Genetics Division Hospital de Cl\u00ednicas de Porto Alegre (HCPA)  Porto Alegre Brazil"},{"name":"Neurology Division Hospital de Cl\u00ednicas de Porto Alegre (HCPA)  Porto Alegre Brazil"},{"name":"Postgraduate Program in Medicine: Medical Sciences Universidade Federal do Rio Grande do Sul  Porto Alegre Brazil"},{"name":"Department of Internal Medicine Universidade Federal do Rio Grande do Sul  Porto Alegre Brazil"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alexandra","family":"Durr","sequence":"additional","affiliation":[{"name":"Sorbonne Universit\u00e9, Institut du Cerveau\u2010Paris Brain Institute (ICM), AP\u2010HP, INSERM, CNRS, University Hospital Piti\u00e9\u2010Salp\u00eatri\u00e8re  Paris France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Masatoyo","family":"Nishizawa","sequence":"additional","affiliation":[{"name":"Brain Research Institute, Niigata University  Niigata Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-0837-5280","authenticated-orcid":false,"given":"Pablo","family":"Martinez\u2010Martin","sequence":"additional","affiliation":[{"name":"Center for Networked Biomedical Research in Neurodegenerative Diseases (CIBERNED) Carlos III Institute of Health  Madrid Spain"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Glenn T.","family":"Stebbins","sequence":"additional","affiliation":[{"name":"Department of Neurological Sciences Rush University Medical Center  Chicago Illinois USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9872-6680","authenticated-orcid":false,"given":"Anette","family":"Schrag","sequence":"additional","affiliation":[{"name":"Department of Clinical Neurosciences UCL Institute of Neurology, Royal Free Campus  London United Kingdom"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Matej","family":"Skorvanek","sequence":"additional","affiliation":[{"name":"Department of Neurology, Faculty of Medicine P. 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