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Unlike the case with most (nonmyoclonic) HD patients, centro\u2010parietal components of somatosensory evoked potentials (SEPs) were well defined and a clear V2 response was found. Treatment with valproic acid greatly reduced myoclonus suggesting that the \u03c3\u2010aminobutyric acid (GABA) system might be involved in the pathophysiology of myoclonus in HD.<\/jats:p>","DOI":"10.1002\/mds.870080216","type":"journal-article","created":{"date-parts":[[2004,12,31]],"date-time":"2004-12-31T10:06:57Z","timestamp":1104487617000},"page":"201-205","source":"Crossref","is-referenced-by-count":37,"title":["Adult onset myoclonic Huntington's 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