{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,4]],"date-time":"2026-10-04T04:57:48Z","timestamp":1791089868837,"version":"4.1.0"},"reference-count":16,"publisher":"Wiley","issue":"4","license":[{"start":{"date-parts":[[2003,11,24]],"date-time":"2003-11-24T00:00:00Z","timestamp":1069632000000},"content-version":"vor","delay-in-days":327,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Ment. Retard. Dev. Disabil. Res. Rev."],"published-print":{"date-parts":[[2003,1]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Auditory brainstem responses (ABRs) and otoacoustic emissions (OAEs) are objective measures of auditory function, but are not hearing tests. Normal OAEs reflect normal cochlear outer hair cell function, and an ABR indicates a synchronous neural response. It is quite possible for a patient to have normal OAEs but absent or grossly abnormal ABR and a behavioral audiogram that is inconsistent with either test. These patients, who may constitute as much as 10% of the diagnosed deaf population, have auditory neuropathy\/dys\u2010synchrony (AN\/AD). To diagnose AN\/AD accurately, ABRs are obtained in response to condensation and rarefaction clicks to distinguish cochlear microphonics (CM) from neural responses. Appropriate management is confounded by variation among patients and changes in auditory function in some patients over time. Recommendations for management include visual language exposure through methods such as American Sign Language (ASL), Cued Speech, or baby signs, and closely following patients. MRDD Research Reviews 2003;9:225\u2013231. \u00a9 2003 Wiley\u2010Liss, Inc.<\/jats:p>","DOI":"10.1002\/mrdd.10084","type":"journal-article","created":{"date-parts":[[2003,12,2]],"date-time":"2003-12-02T14:22:53Z","timestamp":1070374973000},"page":"225-231","source":"Crossref","is-referenced-by-count":110,"title":["Auditory neuropathy\/dys\u2010synchrony: Diagnosis and management"],"prefix":"10.1002","volume":"9","author":[{"given":"Charles I.","family":"Berlin","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Linda","family":"Hood","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Thierry","family":"Morlet","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kelly","family":"Rose","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shanda","family":"Brashears","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2003,11,24]]},"reference":[{"key":"e_1_2_1_2_1","doi-asserted-by":"publisher","DOI":"10.1001\/archotol.127.6.629"},{"key":"e_1_2_1_3_1","doi-asserted-by":"publisher","DOI":"10.1016\/0378-5955(93)90199-B"},{"key":"e_1_2_1_4_1","doi-asserted-by":"publisher","DOI":"10.1097\/00003446-199802000-00002"},{"key":"e_1_2_1_5_1","first-page":"15","article-title":"On renaming auditory neuropathy as auditory dys\u2010synchrony: Implications for a clearer understanding of the underlying mechanisms and management options","volume":"13","author":"Berlin C","year":"2001","journal-title":"Audiology Today"},{"key":"e_1_2_1_6_1","first-page":"137","article-title":"Managing and renaming auditory neuropathy as a continuum of auditory dys\u2010synchrony","volume":"24","author":"Berlin CI","year":"2001","journal-title":"ARO Abstracts"},{"key":"e_1_2_1_7_1","volume-title":"Hair Cell Micromechanics and Otoacoustic Emissions","author":"Berlin CI","year":"2002"},{"key":"e_1_2_1_8_1","first-page":"xi","volume-title":"The Cued Speech Resource Book for Parents of Deaf Children","author":"Cornett RO","year":"1992"},{"key":"e_1_2_1_9_1","volume-title":"Cued Language Structure: An Analysis of Cued American English Based on Linguistic Principles","author":"Fleetwood E","year":"1998"},{"key":"e_1_2_1_10_1","volume-title":"Auditory Neuropathy","author":"Hood L","year":"2001"},{"key":"e_1_2_1_11_1","unstructured":"Joint Committee on Infant Hearing.2000.JCIH Year 2000 Position Statement."},{"key":"e_1_2_1_12_1","doi-asserted-by":"publisher","DOI":"10.1121\/1.1908659"},{"key":"e_1_2_1_13_1","first-page":"460","article-title":"PET studies of auditory pathways in patients with auditory neuropathy","volume":"46","author":"Lockwood AH","year":"1999","journal-title":"Ann Neurol"},{"key":"e_1_2_1_14_1","doi-asserted-by":"publisher","DOI":"10.1038\/sj.jp.7210635"},{"key":"e_1_2_1_15_1","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/119.3.741"},{"key":"e_1_2_1_16_1","doi-asserted-by":"publisher","DOI":"10.1097\/00003446-200102000-00008"},{"key":"e_1_2_1_17_1","first-page":"67","volume-title":"Auditory Neuropathy: A New Perspective on Hearing Disorders","author":"Starr A","year":"2001"}],"container-title":["Mental Retardation and Developmental Disabilities Research Reviews"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Fmrdd.10084","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/mrdd.10084","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,11,17]],"date-time":"2023-11-17T04:55:52Z","timestamp":1700196952000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/mrdd.10084"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2003,1]]},"references-count":16,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2003,1]]}},"alternative-id":["10.1002\/mrdd.10084"],"URL":"https:\/\/doi.org\/10.1002\/mrdd.10084","archive":["Portico"],"relation":{},"ISSN":["1080-4013","1098-2779"],"issn-type":[{"value":"1080-4013","type":"print"},{"value":"1098-2779","type":"electronic"}],"subject":[],"published":{"date-parts":[[2003,1]]}}}