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Interrater reliability was high for upper limbs, with an ICC of 0.92 for three\u2010point pinch and 0.98 for elbow flexion and grip. For lower limbs interrater reliability was good with ICC &gt;0.85 for all measures except foot dorsiflexion. Test\u2013retest results were excellent with ICC &gt;0.91 in all instances. Hand\u2010held myometry is easily performed in SMA patients of various ages and muscle strengths, is a reliable measure of limb muscle strength, and can be used in longitudinal studies and clinical trials. \u00a9 2002 Wiley Periodicals, Inc. 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