{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,8]],"date-time":"2026-10-08T12:10:53Z","timestamp":1791461453996,"version":"4.3.4"},"reference-count":9,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2010,10,21]],"date-time":"2010-10-21T00:00:00Z","timestamp":1287619200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Muscle and Nerve"],"published-print":{"date-parts":[[2010,11]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Creutzfeldt\u2013Jakob disease (CJD) is a degenerative neurological disorder caused by a prion protein. The diagnosis may be challenging in unusual early presentations. A bulbar symptom as the initial complaint is a rare presentation for CJD, with only a few reports so far. These patients can be misdiagnosed with motor neuron disease or the Miller Fisher variant of Guillain\u2013Barr\u00e9 syndrome. We describe a 69\u2010year\u2010old woman with CJD who presented with bulbar symptoms at the onset. Muscle Nerve 42: 833\u2013835, 2010<\/jats:p>","DOI":"10.1002\/mus.21849","type":"journal-article","created":{"date-parts":[[2010,11,4]],"date-time":"2010-11-04T09:11:24Z","timestamp":1288861884000},"page":"833-835","source":"Crossref","is-referenced-by-count":8,"title":["Creutzfeldt\u2013Jakob disease presenting as bulbar palsy"],"prefix":"10.1002","volume":"42","author":[{"given":"Manoj","family":"Mittal","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nancy","family":"Hammond","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kathrin","family":"Husmann","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Abhijit","family":"Lele","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mamatha","family":"Pasnoor","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2010,10,21]]},"reference":[{"key":"e_1_2_4_2_2","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/96.1.1"},{"key":"e_1_2_4_3_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.55.6.811"},{"key":"e_1_2_4_4_2","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.57.12.1751"},{"key":"e_1_2_4_5_2","doi-asserted-by":"publisher","DOI":"10.1212\/01.wnl.0000308955.25760.c2"},{"key":"e_1_2_4_6_2","doi-asserted-by":"publisher","DOI":"10.1093\/bmb\/66.1.213"},{"key":"e_1_2_4_7_2","doi-asserted-by":"publisher","DOI":"10.1159\/000008213"},{"key":"e_1_2_4_8_2","doi-asserted-by":"publisher","DOI":"10.1002\/ana.410350504"},{"key":"e_1_2_4_9_2","first-page":"159","article-title":"Encephalopathy of rapid development with supranuclear ophthalmoplegia and peripheral neuropathy","volume":"142","author":"Brunet P","year":"1986","journal-title":"Rev Neurol (Paris)"},{"key":"e_1_2_4_10_2","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.0409651102"}],"container-title":["Muscle &amp; Nerve"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Fmus.21849","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/mus.21849","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,17]],"date-time":"2023-10-17T07:02:30Z","timestamp":1697526150000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/mus.21849"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2010,10,21]]},"references-count":9,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2010,11]]}},"alternative-id":["10.1002\/mus.21849"],"URL":"https:\/\/doi.org\/10.1002\/mus.21849","archive":["Portico"],"relation":{},"ISSN":["0148-639X","1097-4598"],"issn-type":[{"value":"0148-639X","type":"print"},{"value":"1097-4598","type":"electronic"}],"subject":[],"published":{"date-parts":[[2010,10,21]]}}}