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CIDP frequently precedes the malignancy diagnosis, and there is a favorable CIDP response to treatment more than 70% of the time. Melanoma is the second most common association and may be accompanied by antiganglioside antibodies; CIDP shows a good response to immunotherapy. Other cancers are rare, with variable timings and presentations but good responses to immunomodulation and\/or cancer therapy. Unusual neurological features such as ataxia, distal\/upper limb predominance, or cranial\/respiratory\/autonomic involvement may suggest associated malignancy as may abdominal pain, diarrhea\/constipation, poor appetite\/weight loss, dermatological lesions, and lymphadenopathy. In the appropriate clinical and electrophysiological setting, CIDP associated with cancer should be considered. Immunomodulatory therapy, cancer treatment alone, or a combination may be effective. <jats:italic>Muscle Nerve<\/jats:italic> <jats:bold>57<\/jats:bold>: 875\u2013883, 2018<\/jats:p>","DOI":"10.1002\/mus.26028","type":"journal-article","created":{"date-parts":[[2017,12,1]],"date-time":"2017-12-01T20:03:35Z","timestamp":1512158615000},"page":"875-883","source":"Crossref","is-referenced-by-count":30,"title":["Chronic inflammatory demyelinating polyneuropathy and malignancy: A systematic review"],"prefix":"10.1002","volume":"57","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-7170-8343","authenticated-orcid":false,"given":"Yusuf A.","family":"Rajabally","sequence":"first","affiliation":[{"name":"School of Life and Health Sciences, Aston Brain Centre, Aston University, Aston Triangle Birmingham B4 7ET United Kingdom"},{"name":"Regional Neuromuscular Service, University Hospitals Birmingham Birmingham United 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