{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,5]],"date-time":"2026-05-05T05:29:55Z","timestamp":1777958995224,"version":"3.51.4"},"reference-count":16,"publisher":"Wiley","issue":"1","license":[{"start":{"date-parts":[[2019,4,24]],"date-time":"2019-04-24T00:00:00Z","timestamp":1556064000000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Muscle and Nerve"],"published-print":{"date-parts":[[2019,7]]},"abstract":"<jats:title>ABSTRACT<\/jats:title><jats:p><jats:italic>Introduction<\/jats:italic>: The main objective of this study was to describe muscle involvement on whole\u2010body magnetic resonance imaging scans in adults at different stages of glycogen\u2010storage disease type III (GSDIII). <jats:italic>Methods<\/jats:italic>: Fifteen patients, 16\u201359 years of age, were examined on a 3\u2010T system. The examinations consisted of coronal and axial T1\u2010weighted images or fat images with a Dixon technique, and were scored for 47 muscles using Mercuri's classification. Muscle changes consisted of internal bright signals of fatty replacement. <jats:italic>Results<\/jats:italic>: Distribution across muscles showed predominant signal alteration in the lower limbs and postural muscles. This finding is consistent with the overall clinical presentation of GSDIII and the results of heatmap scores. Review of the MRI scans provided new information regarding recurrent muscle changes, particularly in the soleus, gastrocnemius medial head, and thoracic extensor muscles. <jats:italic>Discussion<\/jats:italic>: Whole\u2010body muscle imaging provides clinically relevant information regarding muscle involvement in GSDIII. A severity score may contribute to improved patient management. <jats:italic>Muscle Nerve<\/jats:italic>, 2019<\/jats:p>","DOI":"10.1002\/mus.26483","type":"journal-article","created":{"date-parts":[[2019,4,11]],"date-time":"2019-04-11T23:59:02Z","timestamp":1555027142000},"page":"72-79","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":11,"title":["Whole\u2010Body Muscle Magnetic Resonance Imaging in Glycogen\u2010Storage Disease Type III"],"prefix":"10.1002","volume":"60","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-9736-8482","authenticated-orcid":false,"given":"David","family":"Tobaly","sequence":"first","affiliation":[{"name":"APHP, Service de Radiologie GHU PIFO p\u00f4le neuro\u2010locomoteur H\u00f4pital Raymond Poincar\u00e9  Garches France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pascal","family":"Lafor\u00eat","sequence":"additional","affiliation":[{"name":"AP\u2010HP, Service de Neurologie H\u00f4pital Raymond\u2010Poincar\u00e9  Garches France"},{"name":"Centre de r\u00e9f\u00e9rence des maladies neuromusculaires Nord\/Est\/Ile de France  France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ariane","family":"Perry","sequence":"additional","affiliation":[{"name":"Universit\u00e9 Paris\u2010Diderot\u2010Sorbonne Paris Cit\u00e9  UMR 1149, Paris France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Dalila","family":"Habes","sequence":"additional","affiliation":[{"name":"AP\u2010HP, Service de p\u00e9diatrie H\u00f4pital Bic\u00eatre  Kremlin\u2010Bic\u00eatre France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Philippe","family":"Labrune","sequence":"additional","affiliation":[{"name":"APHP, H\u00f4pital Antoine B\u00e9cl\u00e8re, Centre de R\u00e9f\u00e9rence Maladies H\u00e9r\u00e9ditaires du M\u00e9tabolisme H\u00e9patique H\u00f4pitaux Universitaires Paris Sud  Clamart France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Valerie","family":"Decostre","sequence":"additional","affiliation":[{"name":"AIM\u2013Institute of Myology  Paris France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marion","family":"Masingue","sequence":"additional","affiliation":[{"name":"Centre de r\u00e9f\u00e9rence des maladies neuromusculaires Nord\/Est\/Ile de France H\u00f4pital Piti\u00e9\u2010Salp\u00eatri\u00e8re  APHP, Paris France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Francois","family":"Petit","sequence":"additional","affiliation":[{"name":"APHP, Laboratoire de G\u00e9n\u00e9tique Mol\u00e9culaire H\u00f4pitaux Universitaires Paris\u2010Sud, H\u00f4pital Antoine B\u00e9cl\u00e8re  Clamart France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Andrea","family":"Barp","sequence":"additional","affiliation":[{"name":"Department of Neurosciences University of Padova  Padova Italy"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Luca","family":"Bello","sequence":"additional","affiliation":[{"name":"Department of Neurosciences University of Padova  Padova Italy"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pierre","family":"Carlier","sequence":"additional","affiliation":[{"name":"AIM &amp; 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