{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,12]],"date-time":"2026-09-12T08:21:30Z","timestamp":1789201290061,"version":"build-2803163510"},"reference-count":13,"publisher":"Wiley","issue":"8","license":[{"start":{"date-parts":[[2004,10,13]],"date-time":"2004-10-13T00:00:00Z","timestamp":1097625600000},"content-version":"vor","delay-in-days":5552,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Muscle and Nerve"],"published-print":{"date-parts":[[1989,8]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>We compared acid \u03b1\u2010glucosidase of acid maltase\u2010deficient Japanese quails, an animal model of human late\u2010onset glycogenosis type II, with that of normal controls. Antibody produced in a rabbit against acid \u03b1\u2010glucosidase purified from chicken pectoral muscle cross\u2010reacted with that of Japanese quails. The presence of a 110K and 98K form of acid \u03b1\u2010glucosidase was confirmed in normal controls by immunoblotting. However the 98K form was absent in the affected quails. Subcellular distribution studies demonstrated that the 98K form, but not the 110K form, was localized in the lysosomes. This suggests that the 110K form is a precursor of the mature 98K form of acid \u03b1\u2010glucosidase. In the affected quails, the 11OK precursor is synthesized, but maturation to the 98K form does not occur or may be extremely deficient.<\/jats:p>","DOI":"10.1002\/mus.880120808","type":"journal-article","created":{"date-parts":[[2005,1,1]],"date-time":"2005-01-01T09:27:03Z","timestamp":1104571623000},"page":"670-678","source":"Crossref","is-referenced-by-count":9,"title":["Mature 98,000\u2010dalton acid \u03b1\u2010glucosidase is deficient in Japanese quails with acid maltase deficiency"],"prefix":"10.1002","volume":"12","author":[{"given":"Yoshihiro","family":"Suhara","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shoichi","family":"Ishiura","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Toshifumi","family":"Tsukahara","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hideo","family":"Sugita","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2004,10,13]]},"reference":[{"key":"e_1_2_1_2_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.23.1.95"},{"key":"e_1_2_1_3_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0021-9258(19)85585-0"},{"key":"e_1_2_1_4_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0021-9258(19)85586-2"},{"key":"e_1_2_1_5_2","doi-asserted-by":"publisher","DOI":"10.1042\/bj0860011"},{"key":"e_1_2_1_6_2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1462-5822.2007.00901.x"},{"key":"e_1_2_1_7_2","first-page":"37","volume-title":"Muscular Dystrophy","author":"Murakami H","year":"1980"},{"key":"e_1_2_1_8_2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1432-1033.1985.tb09266.x"},{"key":"e_1_2_1_9_2","doi-asserted-by":"publisher","DOI":"10.1177\/24.4.1063791"},{"key":"e_1_2_1_10_2","first-page":"132","article-title":"Biochemical, immunological and cell genetic studies in glycogenosis type II","volume":"30","author":"Reuser AJJ","year":"1982","journal-title":"Am J Hum Genet"},{"key":"e_1_2_1_11_2","doi-asserted-by":"publisher","DOI":"10.1016\/0014-5793(82)80953-8"},{"key":"e_1_2_1_12_2","doi-asserted-by":"publisher","DOI":"10.1172\/JCI113008"},{"key":"e_1_2_1_13_2","doi-asserted-by":"publisher","DOI":"10.1016\/0014-5793(82)81306-9"},{"key":"e_1_2_1_14_2","doi-asserted-by":"publisher","DOI":"10.1002\/mus.880090610"}],"container-title":["Muscle &amp; Nerve"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Fmus.880120808","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/mus.880120808","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,22]],"date-time":"2023-10-22T03:46:50Z","timestamp":1697946410000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/mus.880120808"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1989,8]]},"references-count":13,"journal-issue":{"issue":"8","published-print":{"date-parts":[[1989,8]]}},"alternative-id":["10.1002\/mus.880120808"],"URL":"https:\/\/doi.org\/10.1002\/mus.880120808","archive":["Portico"],"relation":{},"ISSN":["0148-639X","1097-4598"],"issn-type":[{"value":"0148-639X","type":"print"},{"value":"1097-4598","type":"electronic"}],"subject":[],"published":{"date-parts":[[1989,8]]}}}