{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,29]],"date-time":"2025-10-29T18:59:50Z","timestamp":1761764390094},"reference-count":26,"publisher":"Wiley","issue":"7","license":[{"start":{"date-parts":[[2004,10,13]],"date-time":"2004-10-13T00:00:00Z","timestamp":1097625600000},"content-version":"vor","delay-in-days":5218,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Muscle and Nerve"],"published-print":{"date-parts":[[1990,7]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Electrophysiologic studies in 11 patients with Dejerine\u2010Sottas disease (hereditary motor and sensory neuropathy type III, HMSN II) showed median and ulnar motor nerve conduction velocities less than 6 m\/sec in all but 1 patient. Marked temporal dispersion without conduction block was present in all patients. Uniform slowing in adjacent motor nerves was consistent with other studies of inherited neuropathies, although marked temporal dispersion may make HMSN III more difficult to distinguish from acquired neuropathies than other hereditary conditions. The electrophysiologic features of HMSN III patients were significantly different from a series of patients with other hereditary neuropathies chosen because of very slow nerve conduction velocity.<\/jats:p>","DOI":"10.1002\/mus.880130705","type":"journal-article","created":{"date-parts":[[2005,1,1]],"date-time":"2005-01-01T09:40:50Z","timestamp":1104572450000},"page":"586-592","source":"Crossref","is-referenced-by-count":35,"title":["The electrophysiologic profile of Dejerine\u2013Sottas disease (HMSN III)"],"prefix":"10.1002","volume":"13","author":[{"given":"Timothy J.","family":"Benstead","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nancy L.","family":"Kuntz","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Robert G.","family":"Miller","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jasper R.","family":"Daube","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2004,10,13]]},"reference":[{"key":"e_1_2_1_2_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.12.10.712"},{"key":"e_1_2_1_3_2","doi-asserted-by":"publisher","DOI":"10.1097\/00005792-195609000-00002"},{"key":"e_1_2_1_4_2","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1960.00450040031003"},{"key":"e_1_2_1_5_2","first-page":"265","volume-title":"Electrodiagnosis in Clinical Neurology","author":"Daube","year":"1986"},{"key":"e_1_2_1_6_2","first-page":"311","article-title":"The peroneal muscular atrophy syndrome. (Clinical, genetic, electrophysiological and nerve biopsy studies)","volume":"26","author":"Davis CJF","year":"1978","journal-title":"J Genet Hum"},{"key":"e_1_2_1_7_2","first-page":"881","article-title":"Contribution \u00e0 l'\u00e9tude de la n\u00e9vrite interstitielle hypertrophique et progressive de l'enfance","volume":"16","author":"Dejerine J","year":"1896","journal-title":"Revue de M\u00e9decine"},{"key":"e_1_2_1_8_2","first-page":"63","article-title":"Sur la n\u00e9vrite interstitielle, hypertrophique et progressive de l'enfance","volume":"45","author":"Dejerine J","year":"1893","journal-title":"Comptes Rendu de la Soci\u00e9t\u00e9 de Biologie"},{"key":"e_1_2_1_9_2","first-page":"1605","volume-title":"Peripheral Neuropathy","author":"Dyc PJ","year":"1984"},{"key":"e_1_2_1_10_2","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1968.00470360025002"},{"key":"e_1_2_1_11_2","first-page":"432","article-title":"Severe hypomyelination and marked abnormality of conduction in Dejerine\u2010Sottas hypertrophic neuropathy: Myelin thickness and compound action potential of sural nerve in vitro","volume":"46","author":"Dyck PJ","year":"1971","journal-title":"Mayo Clin Proc"},{"key":"e_1_2_1_12_2","first-page":"239","article-title":"Prednisone\u2010responsive herediatary motor and sensory neuropathy","volume":"57","author":"Dyck PJ","year":"1982","journal-title":"Mayo Clin Proc"},{"key":"e_1_2_1_13_2","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/105.2.395"},{"key":"e_1_2_1_14_2","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/103.2.259"},{"key":"e_1_2_1_15_2","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.43.8.669"},{"key":"e_1_2_1_16_2","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1977.00500180031007"},{"key":"e_1_2_1_17_2","doi-asserted-by":"publisher","DOI":"10.1002\/ana.410050604"},{"key":"e_1_2_1_18_2","doi-asserted-by":"publisher","DOI":"10.1016\/0013-4694(75)90144-3"},{"key":"e_1_2_1_19_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.32.6.592"},{"key":"e_1_2_1_20_2","doi-asserted-by":"publisher","DOI":"10.1007\/BF00687025"},{"key":"e_1_2_1_21_2","doi-asserted-by":"publisher","DOI":"10.1002\/mus.880080305"},{"key":"e_1_2_1_22_2","first-page":"79","article-title":"Hypertrophic neuropathy: A report of Dejerine\u2010Sottas desease in two sibs","volume":"117","author":"O'Brien MD","year":"1968","journal-title":"Guy's Hospital Reports"},{"key":"e_1_2_1_23_2","doi-asserted-by":"publisher","DOI":"10.1002\/mus.880100809"},{"key":"e_1_2_1_24_2","doi-asserted-by":"publisher","DOI":"10.1002\/mus.880070812"},{"key":"e_1_2_1_25_2","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/110.1.121"},{"key":"e_1_2_1_26_2","first-page":"223","article-title":"Hypertrophic neuropathy","volume":"36","author":"Thomas PK","year":"1967","journal-title":"Q J Med"},{"key":"e_1_2_1_27_2","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.30.2.111"}],"container-title":["Muscle &amp; Nerve"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Fmus.880130705","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/mus.880130705","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,23]],"date-time":"2023-10-23T02:07:19Z","timestamp":1698026839000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/mus.880130705"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1990,7]]},"references-count":26,"journal-issue":{"issue":"7","published-print":{"date-parts":[[1990,7]]}},"alternative-id":["10.1002\/mus.880130705"],"URL":"https:\/\/doi.org\/10.1002\/mus.880130705","archive":["Portico"],"relation":{},"ISSN":["0148-639X","1097-4598"],"issn-type":[{"value":"0148-639X","type":"print"},{"value":"1097-4598","type":"electronic"}],"subject":[],"published":{"date-parts":[[1990,7]]}}}