{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,4,2]],"date-time":"2026-04-02T00:54:07Z","timestamp":1775091247376,"version":"3.50.1"},"reference-count":18,"publisher":"Wiley","issue":"4","license":[{"start":{"date-parts":[[2004,10,13]],"date-time":"2004-10-13T00:00:00Z","timestamp":1097625600000},"content-version":"vor","delay-in-days":4578,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Muscle and Nerve"],"published-print":{"date-parts":[[1992,4]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Phrenic nerve and diaphragmatic dysfunction has been assumed to be the cause of respiratory failure in hereditary motor and sensory neuropathy, type 1 (HMSN I). In order to determine the relationship between phrenic nerve and pulmonary function in this disease, 25 patients underwent a 4\u2010step evaluation process consisting of: (1) bilateral phrenic nerve conduction study; (2) median, peroneal, and tibial motor conduction studies; (3) measurement of forced vital capacity (FVC) and maximal inspiratory and expiratory pressures (MIP, MEP); and (4) pulmonary\u2010focused history and physical. Phrenic nerve motor latency was abnormally prolonged in 22 of the 23 (96%) subjects when a response was obtained. All had slowed velocity or absent peripheral motor conduction responses. Vital capacity was abnormally reduced in 6 of the 25 (24%) subjects. Eight (32%) had an abnormally reduced MIP, while 19 (76%) had an abnormally reduced MEP. Only 2 (8%) subjects had clinical evidence of pulmonary dysfunction. None of the depenent variables (FVC, MIP, MEP, peripheral nerve conduction, or clinical examination) correlated with phrenic nerve latencies. Although phrenic nerve latencies are markedly prolonged in HMSN I, these values are not useful in predicting respiratory dysfunction.<\/jats:p>","DOI":"10.1002\/mus.880150407","type":"journal-article","created":{"date-parts":[[2005,1,1]],"date-time":"2005-01-01T10:00:43Z","timestamp":1104573643000},"page":"459-462","source":"Crossref","is-referenced-by-count":40,"title":["Evaluation of phrenic nerve and pulmonary function in hereditary motor and sensory neuropathy, type I"],"prefix":"10.1002","volume":"15","author":[{"given":"Gregory T.","family":"Carter","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"David D.","family":"Kilmer","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"H. William","family":"Bonekat","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"James S.","family":"Lieberman","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"suffix":"Jr.","given":"William M.","family":"Fowler","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2004,10,13]]},"reference":[{"key":"e_1_2_1_2_2","first-page":"696","article-title":"Maximal respiratory pressures: normal values and relationship to age and sex","volume":"99","author":"Black LF","year":"1969","journal-title":"Am Rev Respir Dis"},{"key":"e_1_2_1_3_2","doi-asserted-by":"publisher","DOI":"10.1378\/chest.91.4.567"},{"key":"e_1_2_1_4_2","first-page":"187","volume-title":"Pulmonary Function Testing Guidelines and Controversies","author":"Clausen JL","year":"1982"},{"key":"e_1_2_1_5_2","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.30.5.420"},{"key":"e_1_2_1_6_2","first-page":"1600","volume-title":"Peripheral Neuropathy","author":"Dyck PJ","year":"1984"},{"key":"e_1_2_1_7_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.39.10.1302"},{"key":"e_1_2_1_8_2","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1968.00470360025002"},{"key":"e_1_2_1_9_2","doi-asserted-by":"publisher","DOI":"10.1378\/chest.93.1.221"},{"key":"e_1_2_1_10_2","doi-asserted-by":"publisher","DOI":"10.1001\/archinte.148.8.1739"},{"key":"e_1_2_1_11_2","doi-asserted-by":"publisher","DOI":"10.1378\/chest.96.5.1197"},{"key":"e_1_2_1_12_2","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.53.4.348"},{"key":"e_1_2_1_13_2","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/103.2.259"},{"key":"e_1_2_1_14_2","doi-asserted-by":"publisher","DOI":"10.1152\/jappl.1985.58.5.1469"},{"key":"e_1_2_1_15_2","doi-asserted-by":"publisher","DOI":"10.1136\/thx.43.6.478"},{"key":"e_1_2_1_16_2","first-page":"41","volume-title":"Nerve Conduction Handbook","author":"Ma DM","year":"1983"},{"key":"e_1_2_1_17_2","first-page":"103","volume-title":"Clinical Pulmonary Function Testing: A Manual of Uniform Laboratory Procedure","author":"Morris AH","year":"1984"},{"key":"e_1_2_1_18_2","doi-asserted-by":"publisher","DOI":"10.1001\/archinte.149.6.1389"},{"key":"e_1_2_1_19_2","first-page":"760","article-title":"Pulmonary rehabilitation, including artificial ventilation in hereditary motor sensory neuropathy, type I","volume":"71","author":"Varlotta GP","year":"1990","journal-title":"Arch Phys Med Rehabil"}],"container-title":["Muscle &amp; Nerve"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Fmus.880150407","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/mus.880150407","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,23]],"date-time":"2023-10-23T18:50:31Z","timestamp":1698087031000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/mus.880150407"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1992,4]]},"references-count":18,"journal-issue":{"issue":"4","published-print":{"date-parts":[[1992,4]]}},"alternative-id":["10.1002\/mus.880150407"],"URL":"https:\/\/doi.org\/10.1002\/mus.880150407","archive":["Portico"],"relation":{},"ISSN":["0148-639X","1097-4598"],"issn-type":[{"value":"0148-639X","type":"print"},{"value":"1097-4598","type":"electronic"}],"subject":[],"published":{"date-parts":[[1992,4]]}}}