{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,9,10]],"date-time":"2025-09-10T21:48:23Z","timestamp":1757540903465},"reference-count":20,"publisher":"Wiley","issue":"4","license":[{"start":{"date-parts":[[2004,10,13]],"date-time":"2004-10-13T00:00:00Z","timestamp":1097625600000},"content-version":"vor","delay-in-days":3848,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Muscle and Nerve"],"published-print":{"date-parts":[[1994,4]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>A 43\u2010year\u2010old male was referred by a veterinarian who evaluated his dog for a seizure and suspected a toxic lead exposure for both. He refurbished houses, removing old paint, and complained of decreased cognition, fatigue, and muscle cramps. He had a depressed affect, postural tremor, right arm weakness with partial denervation on EMG, and borderline\u2010low sensory nerve action potential (SNAP) amplitudes. A mild anemia and elevated serum and urine lead levels supported a diagnosis of lead neuropathy. Chelation therapy increased urine lead excretion without symptomatic improvement. His brother worked part\u2010time with him and developed similar findings, but also had difficulty chewing, dysphagia, perioral twitching, gynecomastia, and multifocal denervation of extremity and facial muscles. His lead levels were not elevated, but an androgen receptor mutation identified on the X chromosome for both brothers confirmed the diagnosis of X\u2010linked bulbospinomuscular atrophy (Kennedy's disease). \u00a9 1994 John Wiley &amp; Sons, Inc.<\/jats:p>","DOI":"10.1002\/mus.880170409","type":"journal-article","created":{"date-parts":[[2005,1,1]],"date-time":"2005-01-01T02:17:24Z","timestamp":1104545844000},"page":"419-423","source":"Crossref","is-referenced-by-count":7,"title":["X\u2010linked bulbospinomuscular atrophy (Kennedy's disease) masquerading as lead neuropathy"],"prefix":"10.1002","volume":"17","author":[{"given":"James W.","family":"Albers","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mark B.","family":"Bromberg","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2004,10,13]]},"reference":[{"key":"e_1_2_1_2_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.43.4.791"},{"key":"e_1_2_1_3_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.41.7.1077"},{"key":"e_1_2_1_4_2","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.33.6.877"},{"key":"e_1_2_1_5_2","first-page":"201","article-title":"Motor neuron disease and toxic metals","volume":"36","author":"Conradi S","year":"1982","journal-title":"Adv Neurol"},{"key":"e_1_2_1_6_2","doi-asserted-by":"publisher","DOI":"10.1001\/jama.247.14.2007"},{"key":"e_1_2_1_7_2","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.45.11.1012"},{"key":"e_1_2_1_8_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.42.12.2300"},{"key":"e_1_2_1_9_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.18.7.671"},{"key":"e_1_2_1_10_2","doi-asserted-by":"publisher","DOI":"10.1002\/ana.410060105"},{"key":"e_1_2_1_11_2","doi-asserted-by":"publisher","DOI":"10.1038\/352077a0"},{"key":"e_1_2_1_12_2","first-page":"312","article-title":"Lead neuropathy: case report","volume":"56","author":"Oh SJ","year":"1975","journal-title":"Arch Phys Med Rehabil"},{"key":"e_1_2_1_13_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.41.6.823"},{"key":"e_1_2_1_14_2","first-page":"143","volume-title":"Metal Binding in Medicine","author":"Rieders F","year":"1960"},{"key":"e_1_2_1_15_2","first-page":"337","article-title":"Lead neuropathy in childhood","volume":"107","author":"Seto DSY","year":"1964","journal-title":"Am J Dis Child"},{"key":"e_1_2_1_16_2","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.27.6.536"},{"key":"e_1_2_1_17_2","first-page":"193","article-title":"Lead exposure and nerve conduction velocity: the differential time course of sensory and motor nerve effects","volume":"4","author":"Singer R","year":"1983","journal-title":"Neurotoxicology"},{"key":"e_1_2_1_18_2","doi-asserted-by":"publisher","DOI":"10.1007\/BF00398813"},{"key":"e_1_2_1_19_2","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1990.00530100087018"},{"key":"e_1_2_1_20_2","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.50.3.279"},{"key":"e_1_2_1_21_2","first-page":"1549","volume-title":"Peripheral Neuropathy","author":"Windebank AJ","year":"1993"}],"container-title":["Muscle &amp; Nerve"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Fmus.880170409","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/mus.880170409","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,24]],"date-time":"2023-10-24T06:07:04Z","timestamp":1698127624000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/mus.880170409"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1994,4]]},"references-count":20,"journal-issue":{"issue":"4","published-print":{"date-parts":[[1994,4]]}},"alternative-id":["10.1002\/mus.880170409"],"URL":"https:\/\/doi.org\/10.1002\/mus.880170409","archive":["Portico"],"relation":{},"ISSN":["0148-639X","1097-4598"],"issn-type":[{"value":"0148-639X","type":"print"},{"value":"1097-4598","type":"electronic"}],"subject":[],"published":{"date-parts":[[1994,4]]}}}