{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,24]],"date-time":"2026-08-24T23:28:13Z","timestamp":1787614093280,"version":"build-2736575974"},"reference-count":11,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2014,10,12]],"date-time":"2014-10-12T00:00:00Z","timestamp":1413072000000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatric Blood &amp; Cancer"],"published-print":{"date-parts":[[2015,5]]},"abstract":"<jats:sec><jats:label\/><jats:p>Kaposiform lymphangiomatosis (KLA) is a rare proliferation of abnormal lymphatic vessels often complicated by pleural\/pericardial effusions and a consumptive coagulopathy that may lead to life threatening hemorrhage. Establishing the diagnosis is challenging due to the clinical heterogeneity and variable findings in laboratory values, radiographic features, and pathologic characteristics. We report three patients who had slowly progressive symptoms and presented with pleural or pericardial effusions, evidence of a consumptive coagulopathy and anemia. Despite being a rare and challenging diagnosis, KLA should be considered in patients presenting with non\u2010specific indolent symptoms, pleural or pericardial effusions and laboratory evidence of a consumptive coagulopathy. Pediatr Blood Cancer 2015;62:901\u2013904. \u00a9 2014 Wiley Periodicals, Inc.<\/jats:p><\/jats:sec>","DOI":"10.1002\/pbc.25278","type":"journal-article","created":{"date-parts":[[2014,10,12]],"date-time":"2014-10-12T20:43:14Z","timestamp":1413146594000},"page":"901-904","source":"Crossref","is-referenced-by-count":53,"title":["Kaposiform lymphangiomatosis: Unifying features of a heterogeneous disorder"],"prefix":"10.1002","volume":"62","author":[{"given":"Violet M.","family":"Fernandes","sequence":"first","affiliation":[{"name":"Center for Cancer and Blood Disorders Children's National Health System Washington District of Columbia"},{"name":"Department of Pediatrics The George Washington University School of Medicine and Health Sciences Washington District of Columbia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"John H.","family":"Fargo","sequence":"additional","affiliation":[{"name":"Center for Cancer and Blood Disorders Children's National Health System Washington District of Columbia"},{"name":"Department of Pediatrics The George Washington University School of Medicine and Health Sciences Washington District of Columbia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Surbhi","family":"Saini","sequence":"additional","affiliation":[{"name":"Center for Cancer and Blood Disorders Children's National Health System Washington District of Columbia"},{"name":"Department of Pediatrics The George Washington University School of Medicine and Health Sciences Washington District of Columbia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michael F.","family":"Guerrera","sequence":"additional","affiliation":[{"name":"Center for Cancer and Blood Disorders Children's National Health System Washington District of Columbia"},{"name":"Department of Pediatrics The George Washington University School of Medicine and Health Sciences Washington District of Columbia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Leigh","family":"Marcus","sequence":"additional","affiliation":[{"name":"Center for Cancer and Blood Disorders Children's National Health System Washington District of Columbia"},{"name":"Department of Pediatrics The George Washington University School of Medicine and Health Sciences Washington District of Columbia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Lori","family":"Luchtman\u2010Jones","sequence":"additional","affiliation":[{"name":"Center for Cancer and Blood Disorders Children's National Health System Washington District of Columbia"},{"name":"Department of Pediatrics The George Washington University School of Medicine and Health Sciences Washington District of Columbia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Denise","family":"Adams","sequence":"additional","affiliation":[{"name":"Cincinnati Children's Hospital Medical Center Cincinnati Ohio"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Emily Riehm","family":"Meier","sequence":"additional","affiliation":[{"name":"Center for Cancer and Blood Disorders Children's National Health System Washington District of Columbia"},{"name":"Department of Pediatrics The George Washington University School of Medicine and Health Sciences Washington District of Columbia"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2014,10,12]]},"reference":[{"key":"e_1_2_5_2_1","doi-asserted-by":"publisher","DOI":"10.1164\/ajrccm.161.3.9904056"},{"key":"e_1_2_5_3_1","doi-asserted-by":"publisher","DOI":"10.1097\/RLU.0b013e3181e4dc3c"},{"key":"e_1_2_5_4_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.crad.2005.03.006"},{"key":"e_1_2_5_5_1","doi-asserted-by":"publisher","DOI":"10.1097\/00000478-199304000-00002"},{"key":"e_1_2_5_6_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00256-012-1565-4"},{"key":"e_1_2_5_7_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpeds.2013.10.013"},{"key":"e_1_2_5_8_1","doi-asserted-by":"publisher","DOI":"10.1002\/pbc.23124"},{"key":"e_1_2_5_9_1","doi-asserted-by":"crossref","first-page":"184","DOI":"10.1089\/lrb.2011.0020","article-title":"Lymphangiomatosis: A clinical overview","volume":"9","author":"Blei F","year":"2011","journal-title":"Lymphat Res Biol"},{"key":"e_1_2_5_10_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.cps.2010.08.002"},{"key":"e_1_2_5_11_1","unstructured":"International Society for the Study of Vascular Anomalies Classification System. 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