{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,7]],"date-time":"2026-05-07T16:07:47Z","timestamp":1778170067252,"version":"3.51.4"},"reference-count":19,"publisher":"Wiley","issue":"1","license":[{"start":{"date-parts":[[2016,8,27]],"date-time":"2016-08-27T00:00:00Z","timestamp":1472256000000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatric Blood &amp; Cancer"],"published-print":{"date-parts":[[2017,1]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Patients with Wiskott\u2013Aldrich syndrome (WAS) are predisposed to malignancy and autoimmunity in addition to infections. We report a male child with WAS, who had presented with recurrent pneumonia, eczema, thrombocytopenia, autoimmune hemolytic anemia, and vasculitic skin lesions. Genetic analysis revealed a classical genotype <jats:italic>WAS<\/jats:italic> 155C&gt;T; R41X. At 2 years of follow\u2010up, he developed persistent headache and progressive hepatomegaly. Brain imaging showed a mass in the right frontal region, which on histopathology was shown to be high\u2010grade non\u2010Hodgkin lymphoma. Magnetic resonance cholangiopancreatography showed features of sclerosing cholangitis. This report extends the clinical spectrum and highlights unusual manifestations of sclerosing cholangitis and intracranial lymphoma in a patient with WAS.<\/jats:p>","DOI":"10.1002\/pbc.26196","type":"journal-article","created":{"date-parts":[[2016,8,27]],"date-time":"2016-08-27T12:42:44Z","timestamp":1472301764000},"page":"106-109","source":"Crossref","is-referenced-by-count":14,"title":["Sclerosing cholangitis and intracranial lymphoma in a child with classical Wiskott\u2013Aldrich syndrome"],"prefix":"10.1002","volume":"64","author":[{"given":"Pandiarajan","family":"Vignesh","sequence":"first","affiliation":[{"name":"Pediatric Allergy Immunology Unit Department of Pediatrics Advanced Pediatrics Centre Postgraduate Institute of Medical Education and Research  Chandigarh India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Deepti","family":"Suri","sequence":"additional","affiliation":[{"name":"Pediatric Allergy Immunology Unit Department of Pediatrics Advanced 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