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This study aims to review the literature on CHB to better define presentation, diagnosis, available treatments and management options. The analysis of outcomes suggests that a significant portion of mortality is unrelated to the malignant nature of the tumour. Key factors influencing overall outcomes were identified: mortality linked to the \u2018mass effect\u2019 during both the prenatal (22%) and perinatal (32%) stages, as well as \u2018oncological\u2019 mortality encompassing tumour and\/or treatment\u2010related factors (46%). Overall, after birth, CHB does not seem to confer a worse oncological prognosis per se, and should be managed similarly to older children, if patients are stable enough to undergo proper staging and treatment. A deeper knowledge and better outcomes would come from a large, homogeneous, collection of data possibly allowing a global protocol, focusing on a comprehensive management of CHB.<\/jats:p>","DOI":"10.1002\/pbc.31132","type":"journal-article","created":{"date-parts":[[2024,7,2]],"date-time":"2024-07-02T07:30:08Z","timestamp":1719905408000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":4,"title":["Congenital hepatoblastoma: Expanding knowledge, improving outcomes"],"prefix":"10.1002","volume":"71","author":[{"given":"Francesca","family":"Gigola","sequence":"first","affiliation":[{"name":"School of Pediatric Surgery University of Florence  Florence Italy"},{"name":"Department of Pediatric and Neonatal Surgery Meyer Children's Hospital IRCCS  Florence 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