{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,17]],"date-time":"2026-08-17T14:53:21Z","timestamp":1786978401497,"version":"build-2736575974"},"reference-count":11,"publisher":"Wiley","issue":"4","license":[{"start":{"date-parts":[[2005,10,21]],"date-time":"2005-10-21T00:00:00Z","timestamp":1129852800000},"content-version":"vor","delay-in-days":4403,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatric Pulmonology"],"published-print":{"date-parts":[[1993,10]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:p>Williams\u2013Campbell syndrome was first described in 1960 as a rare form of bronchiectasis. Its pathogenesis is characterized by the absence or markedly diminished cartilage around the bronchi. Although the familial nature was postulated early on, only one possible familial Occurrence has been reported in the literature. We present two family members in whom respiratory symptoms developed within the first year of life and were found to have histopathologic changes consistent with Williams\u2013Campbell syndrome. This would lend further support of a developmental origin for this type of bronchiectasis. Pediatr Pulmonol. 1993; 16:263\u2013267. \u00a9 1993 Wiley\u2010Liss, Inc.<\/jats:p>","DOI":"10.1002\/ppul.1950160410","type":"journal-article","created":{"date-parts":[[2007,3,6]],"date-time":"2007-03-06T13:36:39Z","timestamp":1173188199000},"page":"263-267","source":"Crossref","is-referenced-by-count":42,"title":["Familial congenital bronchiectasis: Williams\u2010Campbell syndrome"],"prefix":"10.1002","volume":"16","author":[{"given":"V. Faye","family":"Jones","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nemr S.","family":"Eid","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sofia M.","family":"Franco","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"J. Thomas","family":"Badgett","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"John J.","family":"Buchino","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2005,10,21]]},"reference":[{"key":"e_1_2_1_2_2","unstructured":"LaennccRTH De l'auscultation me'diate un trait\u00e9 du diagnostic des maladies des poumons et du coeur fond\u00e9 principalement sur ce nouveau moyen d'exploration. 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Am RevRespirDis 1976;11415\u201322."},{"key":"e_1_2_1_9_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3476(83)80515-0"},{"key":"e_1_2_1_10_2","first-page":"821","article-title":"Airway dynamics in bronchiectasis, a combined cinefluorographic\u2010manometric study","volume":"93","author":"Fraser RG","year":"1965","journal-title":"Am J Roentgenol Radium Ther Nucl Med."},{"key":"e_1_2_1_11_2","doi-asserted-by":"publisher","DOI":"10.1097\/00004728-198707000-00028"},{"key":"e_1_2_1_12_2","doi-asserted-by":"publisher","DOI":"10.1136\/thx.29.3.304"}],"container-title":["Pediatric Pulmonology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Fppul.1950160410","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/ppul.1950160410","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,28]],"date-time":"2023-09-28T01:11:00Z","timestamp":1695863460000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/ppul.1950160410"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1993,10]]},"references-count":11,"journal-issue":{"issue":"4","published-print":{"date-parts":[[1993,10]]}},"alternative-id":["10.1002\/ppul.1950160410"],"URL":"https:\/\/doi.org\/10.1002\/ppul.1950160410","archive":["Portico"],"relation":{},"ISSN":["8755-6863","1099-0496"],"issn-type":[{"value":"8755-6863","type":"print"},{"value":"1099-0496","type":"electronic"}],"subject":[],"published":{"date-parts":[[1993,10]]}}}