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Many physicians incorrectly diagnose PCD or eliminate PCD from their differential diagnosis due to inexperience with diagnostic testing methods. Thus far, all therapies used for PCD are unproven through large clinical trials. This review article outlines consensus recommendations from PCD physicians in North America who have been engaged in a PCD centered research consortium for the last 10 years. These recommendations have been adopted by the governing board of the PCD Foundation to provide guidance for PCD clinical centers for diagnostic testing, monitoring, and appropriate short and long\u2010term therapeutics in PCD patients.\n                      <jats:bold>Pediatr Pulmonol. 2016;51:115\u2013132<\/jats:bold>\n                      . \u00a9 2015 The Authors.\n                      <jats:italic>Pediatric Pulmonology<\/jats:italic>\n                      Published by Wiley Periodicals, Inc.\n                    <\/jats:p>\n                  <\/jats:sec>","DOI":"10.1002\/ppul.23304","type":"journal-article","created":{"date-parts":[[2015,9,29]],"date-time":"2015-09-29T11:34:32Z","timestamp":1443526472000},"page":"115-132","source":"Crossref","is-referenced-by-count":415,"title":["Diagnosis, monitoring, and treatment of primary ciliary dyskinesia: PCD foundation consensus recommendations based on state of the art 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