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Research methodologies, self\u2010concept dimensions, prominent self\u2010concept findings and clinical recommendations are identified. Preferred Reporting Items for Systematic Review and Meta\u2010analyses guidelines were applied. PubMed, Scopus, Medline, Psycinfo, CINAHL (ebsco), and CENTRAL Cochrane electronic databases were searched from 2012 to 2022. Methodological quality was assessed using the critical appraisal skills program. Data\u2010based convergent synthesis was applied to analyze and report on qualitative and quantitative studies in parallel. Thirty\u2010seven publications met the inclusion criteria, most of which employed a cross\u2010sectional, single\u2010center design within an adolescent and adult population. Self\u2010efficacy, self\u2010esteem, and self\u2010identity studies were dimensions of self\u2010concept identified, with studies relating to self\u2010efficacy surrounding physical health management most prevalent. All three dimensions were positively associated with improved treatment adherence and psychosocial health. Efficacy tested intervention programs to enhance self\u2010concept are limited; however, an extensive range of clinical recommendations are offered, highlighting the importance of clinician self\u2010concept awareness, quality clinician\u2013patient conversations and online CF peer\u2010support. Self\u2010concept is an important mechanism to optimize patient outcomes. Further CF self\u2010concept research is required, particularly multicenter, longitudinal, and interventional studies. Early childhood, post lung transplant and the older adult CF population in particular, lack research attention. Given the potential impact of rapidly evolving CF transmembrane conductance regulator modulator drugs on many aspects of self, future self\u2010concept research beyond the dimension of self\u2010efficacy may be beneficial.<\/jats:p>","DOI":"10.1002\/ppul.26916","type":"journal-article","created":{"date-parts":[[2024,2,20]],"date-time":"2024-02-20T10:55:49Z","timestamp":1708426549000},"page":"1175-1195","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":9,"title":["Me, myself, and I: A systematic review of cystic fibrosis and self\u2010concept"],"prefix":"10.1002","volume":"59","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-7636-2708","authenticated-orcid":false,"given":"Maggie","family":"Harrigan","sequence":"first","affiliation":[{"name":"UWA Medical School The University of Western Australia Perth Western Australia Australia"},{"name":"Institute for Respiratory Health (IRH) Perth Western Australia Australia"},{"name":"Cystic Fibrosis Western Australia (CFWA) Perth Western Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-5243-9117","authenticated-orcid":false,"given":"Melanie","family":"Jessup","sequence":"additional","affiliation":[{"name":"School of Nursing, Midwifery and Social Work The University of Queensl Brisbane Queensland Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7091-5060","authenticated-orcid":false,"given":"Kellie","family":"Bennett","sequence":"additional","affiliation":[{"name":"UWA Medical School The University of Western Australia Perth Western Australia Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7480-4835","authenticated-orcid":false,"given":"Siobhain","family":"Mulrennan","sequence":"additional","affiliation":[{"name":"UWA Medical School The University of Western Australia Perth Western Australia Australia"},{"name":"Institute for Respiratory Health (IRH) Perth Western Australia Australia"},{"name":"Department of Respiratory Health Sir Chares Gairdner Hospital (SCGH) Cystic Fibrosis Clinic Perth Western Australia Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2024,2,20]]},"reference":[{"key":"e_1_2_11_2_1","unstructured":"Cystic Fibrosis Foundation. 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