{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,4,10]],"date-time":"2026-04-10T23:08:29Z","timestamp":1775862509442,"version":"3.50.1"},"reference-count":6,"publisher":"Wiley","issue":"2","license":[{"start":{"date-parts":[[2015,5,22]],"date-time":"2015-05-22T00:00:00Z","timestamp":1432252800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Respirology Case Reports"],"published-print":{"date-parts":[[2015,6]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Pleuroparenchymal fibroelastosis (<jats:styled-content style=\"fixed-case\">PPFE<\/jats:styled-content>) is a newly described form of interstitial lung disease that originates in the upper lung zones and typically progresses to involve the entire lung. The disease may be idiopathic but is often associated with other pre\u2010 or coexisting conditions. Pneumothorax is a common complication and can occur at presentation or at other times during the course of the disease. Pathologically, interstitial fibrosis takes the form of a dense consolidation with some preservation of alveolar septal outlines and demonstrates a distinctly abrupt interface with residual normal lung. Unrecognized cases of <jats:styled-content style=\"fixed-case\">PPFE<\/jats:styled-content> may be incorrectly diagnosed as sarcoidosis, atypical idiopathic pulmonary fibrosis, or other unclassifiable interstitial pneumonias.<\/jats:p>","DOI":"10.1002\/rcr2.108","type":"journal-article","created":{"date-parts":[[2015,5,22]],"date-time":"2015-05-22T10:20:38Z","timestamp":1432290038000},"page":"82-84","source":"Crossref","is-referenced-by-count":16,"title":["Pleuroparenchymal fibroelastosis: a rare interstitial lung disease"],"prefix":"10.1002","volume":"3","author":[{"given":"John C.","family":"English","sequence":"first","affiliation":[{"name":"Department of Pathology and Laboratory Medicine Vancouver General Hospital  Vancouver British Columbia Canada"},{"name":"University of British Columbia  Vancouver British Columbia Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"John R.","family":"Mayo","sequence":"additional","affiliation":[{"name":"University of British Columbia  Vancouver British Columbia Canada"},{"name":"Department of Radiology Vancouver General Hospital  Vancouver British Columbia Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Robert","family":"Levy","sequence":"additional","affiliation":[{"name":"University of British Columbia  Vancouver British Columbia Canada"},{"name":"Division of Respirology Department of Medicine Vancouver General Hospital  Vancouver British Columbia Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"John","family":"Yee","sequence":"additional","affiliation":[{"name":"University of British Columbia  Vancouver British Columbia Canada"},{"name":"Division of Thoracic Surgery Department of Surgery Vancouver General Hospital  Vancouver British Columbia Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kevin O.","family":"Leslie","sequence":"additional","affiliation":[{"name":"Department of Pathology Mayo Clinic Arizona  Scottsdale Arizona"},{"name":"Mayo Clinic Medical School  Scottsdale Arizona"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2015,5,22]]},"reference":[{"key":"e_1_2_5_2_1","doi-asserted-by":"publisher","DOI":"10.1378\/chest.126.6.2007"},{"key":"e_1_2_5_3_1","doi-asserted-by":"publisher","DOI":"10.1038\/modpathol.2011.114"},{"key":"e_1_2_5_4_1","doi-asserted-by":"publisher","DOI":"10.1183\/09031936.00165111"},{"key":"e_1_2_5_5_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.resinv.2012.06.003"},{"key":"e_1_2_5_6_1","doi-asserted-by":"publisher","DOI":"10.1038\/modpathol.2012.171"},{"key":"e_1_2_5_7_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.healun.2004.08.026"}],"container-title":["Respirology Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Frcr2.108","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1002%2Frcr2.108","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/rcr2.108","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/full-xml\/10.1002\/rcr2.108","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/rcr2.108","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,5]],"date-time":"2023-10-05T01:14:01Z","timestamp":1696468441000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/rcr2.108"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2015,5,22]]},"references-count":6,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2015,6]]}},"alternative-id":["10.1002\/rcr2.108"],"URL":"https:\/\/doi.org\/10.1002\/rcr2.108","archive":["Portico"],"relation":{},"ISSN":["2051-3380","2051-3380"],"issn-type":[{"value":"2051-3380","type":"print"},{"value":"2051-3380","type":"electronic"}],"subject":[],"published":{"date-parts":[[2015,5,22]]}}}