{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,30]],"date-time":"2025-07-30T10:09:15Z","timestamp":1753870155725,"version":"3.41.2"},"reference-count":34,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2023,4,12]],"date-time":"2023-04-12T00:00:00Z","timestamp":1681257600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Respirology Case Reports"],"published-print":{"date-parts":[[2023,5]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>We report a 35\u2010year\u2010old woman who presented with dyspnoea and chest pain for 1 week. High\u2010resolution computed tomography (HRCT) thorax revealed bilateral pneumothoraces with diffuse lung cysts. Bilateral intercostal chest tubes were inserted, and there was a persistent air leak (PAL) bilaterally. We performed an autologous blood patch pleurodesis (ABPP) for the left PAL. For the right PAL, she underwent a successful right video\u2010assisted thoracic (VATS) surgery, wedge biopsy, and surgical pleurodesis. Histopathology examination confirmed the diagnosis of lymphangioleiomyomatosis (LAM). The left pneumothorax recurred. An indwelling pleural catheter (Rocket\u00ae IPC\u2122; Rocket Medical plc; WASHINGTON) was inserted and the patient was discharged after 1 day with an atrium pneumostat (Pneumostat\u2122; Atrium Medical Corporation, Hudson, NH, USA) chest drain valve. The patient was initiated on Sirolimus 2\u2009mg daily. The left PAL resolved at 6\u2009weeks. This case highlights the benefit of IPC with an ambulatory pneumothorax device in a patient with LAM with PAL.<\/jats:p>","DOI":"10.1002\/rcr2.1143","type":"journal-article","created":{"date-parts":[[2023,4,13]],"date-time":"2023-04-13T04:55:33Z","timestamp":1681361733000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":3,"title":["The benefit of indwelling pleural catheter with ambulatory pneumothorax device and autologous blood patch pleurodesis in lymphangioleiomyomatosis with persistent air leak"],"prefix":"10.1002","volume":"11","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-0750-3087","authenticated-orcid":false,"given":"Boon Hau","family":"Ng","sequence":"first","affiliation":[{"name":"Pulmonology Unit, Department of Internal Medicine, Faculty of Medicine Universiti Kebangsaan Malaysia Medical Centre Kuala Lumpur Malaysia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hsueh Jing","family":"Low","sequence":"additional","affiliation":[{"name":"Department of Anesthesiology &amp; Intensive Care Unit, Faculty of Medicine Universiti Kebangsaan Malaysia Medical Centre Kuala Lumpur Malaysia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nik Nuratiqah","family":"Nik Abeed","sequence":"additional","affiliation":[{"name":"Pulmonology Unit, Department of Internal Medicine, Faculty of Medicine Universiti Kebangsaan Malaysia Medical Centre Kuala Lumpur Malaysia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mas Fazlin Mohamad","family":"Jailaini","sequence":"additional","affiliation":[{"name":"Pulmonology Unit, Department of Internal Medicine, Faculty of Medicine Universiti Kebangsaan Malaysia Medical Centre Kuala Lumpur Malaysia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7526-361X","authenticated-orcid":false,"given":"Mohamed Faisal","family":"Abdul Hamid","sequence":"additional","affiliation":[{"name":"Pulmonology Unit, Department of Internal Medicine, Faculty of Medicine Universiti Kebangsaan Malaysia Medical Centre Kuala Lumpur Malaysia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3788-4789","authenticated-orcid":false,"given":"Andrea","family":"Ban Yu\u2010Lin","sequence":"additional","affiliation":[{"name":"Pulmonology Unit, Department of Internal Medicine, Faculty of Medicine Universiti Kebangsaan Malaysia Medical Centre Kuala Lumpur Malaysia"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2023,4,12]]},"reference":[{"key":"e_1_2_7_2_1","doi-asserted-by":"publisher","DOI":"10.1136\/thorax.55.12.1052"},{"issue":"5","key":"e_1_2_7_3_1","first-page":"E99","article-title":"Bilateral spontaneous tension pneumothorax is secondary to lymphangioleiomyomatosis","volume":"70","author":"Cheng YL","year":"2011","journal-title":"J Trauma"},{"key":"e_1_2_7_4_1","doi-asserted-by":"publisher","DOI":"10.1148\/rg.253055006"},{"key":"e_1_2_7_5_1","doi-asserted-by":"publisher","DOI":"10.1378\/chest.115.4.1041"},{"key":"e_1_2_7_6_1","doi-asserted-by":"publisher","DOI":"10.1164\/rccm.201607-1384ST"},{"key":"e_1_2_7_7_1","doi-asserted-by":"publisher","DOI":"10.1136\/thx.2010.137026"},{"key":"e_1_2_7_8_1","doi-asserted-by":"publisher","DOI":"10.1378\/chest.08-2389"},{"key":"e_1_2_7_9_1","doi-asserted-by":"publisher","DOI":"10.4103\/1817-1737.56011"},{"key":"e_1_2_7_10_1","unstructured":"KapoorS Al\u2010SaffarF BajwaAA ShujaatA.Autologous Blood Patch Pleurodesis for Persistent Air\u2010Leak from Secondary Spontaneous Pneumothorax: A Systematic Review. 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