{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,29]],"date-time":"2026-09-29T09:13:11Z","timestamp":1790673191861,"version":"4.1.0"},"reference-count":17,"publisher":"Wiley","issue":"10","license":[{"start":{"date-parts":[[2024,10,17]],"date-time":"2024-10-17T00:00:00Z","timestamp":1729123200000},"content-version":"vor","delay-in-days":16,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Respirology Case Reports"],"published-print":{"date-parts":[[2024,10]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Isolated Pauci\u2010immune pulmonary capillaritis (IPIPC) is a rare form of small vessel vasculitis that affects only the lungs, causing inflammation of pulmonary capillaries and potentially leading to severe outcomes like alveolar haemorrhage. A 23\u2010year\u2010old woman with a prior diagnosis of rheumatoid arthritis presented with hemoptysis and respiratory distress, ultimately diagnosed with IPIPC. Despite treatment with high\u2010dose steroids and intravenous immunoglobulin, her condition deteriorated, resulting in respiratory failure and death. IPIPC often lacks systemic symptoms and ANCA positivity, complicating diagnosis and treatment. Imaging, bronchoscopy, and histopathology are key for diagnosis, while management typically involves corticosteroids and possibly immunosuppressives. The case underscores the challenges in identifying and treating IPIPC, highlighting the importance of early intervention to improve prognosis, even though complications can still lead to significant respiratory issues and mortality.<\/jats:p>","DOI":"10.1002\/rcr2.70051","type":"journal-article","created":{"date-parts":[[2024,10,18]],"date-time":"2024-10-18T00:24:36Z","timestamp":1729211076000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":3,"title":["Fatal outcome in isolated Pauci\u2010immune pulmonary capillaritis: A case report"],"prefix":"10.1002","volume":"12","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-6418-7132","authenticated-orcid":false,"given":"Zeinab","family":"El Mawla","sequence":"first","affiliation":[{"name":"Department of Pulmonary &amp; Critical Care, Faculty of Medical Sciences Lebanese University  Hadat Lebanon"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ghinwa","family":"Hammoud","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, Faculty of Medical Sciences Lebanese University  Hadat Lebanon"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Racha","family":"Abed El Hamid","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, Faculty of Medical Sciences Lebanese University  Hadat Lebanon"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Abbas","family":"Zreik","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine, Faculty of Medical Sciences Lebanese University  Hadat Lebanon"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ali","family":"Tfayli","sequence":"additional","affiliation":[{"name":"Cardiology Division Zahraa Hospital, University Medical Center (ZHUMC)  Beirut Lebanon"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Bassam","family":"Mansour","sequence":"additional","affiliation":[{"name":"Department of Pulmonary &amp; 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