{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,12,28]],"date-time":"2025-12-28T19:26:17Z","timestamp":1766949977794,"version":"3.48.0"},"reference-count":5,"publisher":"Wiley","issue":"12","license":[{"start":{"date-parts":[[2025,12,9]],"date-time":"2025-12-09T00:00:00Z","timestamp":1765238400000},"content-version":"vor","delay-in-days":8,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Respirology Case Reports"],"published-print":{"date-parts":[[2025,12]]},"abstract":"<jats:title>ABSTRACT<\/jats:title>\n                  <jats:p>Partial anomalous pulmonary venous connection (PAPVC) is a rare congenital anomaly in which one or more pulmonary veins drain into the systemic venous circulation. PAPVC is often misdiagnosed as idiopathic pulmonary hypertension in the adult population. We report a case of a 48\u2010year\u2010old woman with long\u2010standing pulmonary hypertension who presented with recurrent pulmonary oedema and right\u2010sided heart failure. Transthoracic echocardiography showed severe pulmonary hypertension with preserved left ventricular function. Computed tomographic pulmonary angiography excluded pulmonary embolism but confirmed an anomalous drainage of the right upper pulmonary vein into the superior vena cava, consistent with isolated PAPVC without an atrial septal defect. Right heart catheterization confirmed severe precapillary pulmonary hypertension with a positive vasoreactivity response to adenosine. She was successfully managed medically with diltiazem and diuretics, showing sustained clinical improvement. This case highlights isolated PAPVC as a critical, under\u2010recognised cause of severe pulmonary hypertension in adults.<\/jats:p>","DOI":"10.1002\/rcr2.70438","type":"journal-article","created":{"date-parts":[[2025,12,9]],"date-time":"2025-12-09T10:48:07Z","timestamp":1765277287000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["A Case of Right\u2010Sided Heart Failure and Severe Pulmonary Hypertension Secondary to Partial Anomalous Pulmonary Venous Connection"],"prefix":"10.1002","volume":"13","author":[{"given":"Ahmed Tareq","family":"Alabsi","sequence":"first","affiliation":[{"name":"Department of Emergency Medicine Bahrain Defence Force Hospital\u2010Royal Medical Services  Riffa Bahrain"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6165-0598","authenticated-orcid":false,"given":"Khalifa Abdulrahman","family":"Yusuf","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine Bahrain Defence Force Hospital\u2010Royal Medical Services  Riffa Bahrain"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Alya Salman","family":"Aldoseri","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine Bahrain Defence Force Hospital\u2010Royal Medical Services  Riffa Bahrain"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Shadi Fayez","family":"Kanhosh","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine Bahrain Defence Force Hospital\u2010Royal Medical Services  Riffa Bahrain"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Abdulrahman Hasan","family":"Al\u2010Madani","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine Bahrain Defence Force Hospital\u2010Royal Medical Services  Riffa Bahrain"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ahmed Taha","family":"Shaarawy","sequence":"additional","affiliation":[{"name":"Department of Internal Medicine Bahrain Defence Force Hospital\u2010Royal Medical Services  Riffa Bahrain"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2025,12,9]]},"reference":[{"issue":"3","key":"e_1_2_8_2_1","first-page":"239","article-title":"Partial Anomalous Pulmonary Venous Return: A Ten\u2010Year Experience","volume":"12","author":"Weiman D. S.","year":"1985","journal-title":"Texas Heart Institute Journal"},{"key":"e_1_2_8_3_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.radcr.2025.01.027"},{"key":"e_1_2_8_4_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.rmcr.2019.100833"},{"issue":"6","key":"e_1_2_8_5_1","article-title":"Partial Anomalous Pulmonary Venous Return Presenting in Adults: A Case Series With Review of Literature","volume":"12","author":"Pendela V. S.","year":"2020","journal-title":"Cureus"},{"issue":"6","key":"e_1_2_8_6_1","article-title":"Medical Management of Isolated Partial Anomalous Pulmonary Venous Connection With Symptomatic Right Ventricular Failure and Pulmonary Hypertension","volume":"16","author":"Choi M. H.","year":"2024","journal-title":"Cureus"}],"container-title":["Respirology Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1002\/rcr2.70438","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,12,28]],"date-time":"2025-12-28T19:24:33Z","timestamp":1766949873000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1002\/rcr2.70438"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2025,12]]},"references-count":5,"journal-issue":{"issue":"12","published-print":{"date-parts":[[2025,12]]}},"alternative-id":["10.1002\/rcr2.70438"],"URL":"https:\/\/doi.org\/10.1002\/rcr2.70438","archive":["Portico"],"relation":{},"ISSN":["2051-3380","2051-3380"],"issn-type":[{"type":"print","value":"2051-3380"},{"type":"electronic","value":"2051-3380"}],"subject":[],"published":{"date-parts":[[2025,12]]},"assertion":[{"value":"2025-10-08","order":0,"name":"received","label":"Received","group":{"name":"publication_history","label":"Publication History"}},{"value":"2025-12-01","order":2,"name":"accepted","label":"Accepted","group":{"name":"publication_history","label":"Publication History"}},{"value":"2025-12-09","order":3,"name":"published","label":"Published","group":{"name":"publication_history","label":"Publication History"}}],"article-number":"e70438"}}