{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,27]],"date-time":"2026-03-27T05:56:53Z","timestamp":1774591013122,"version":"3.50.1"},"reference-count":7,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[2026,3,11]],"date-time":"2026-03-11T00:00:00Z","timestamp":1773187200000},"content-version":"vor","delay-in-days":10,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"},{"start":{"date-parts":[[2026,3,1]],"date-time":"2026-03-01T00:00:00Z","timestamp":1772323200000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/doi.wiley.com\/10.1002\/tdm_license_1.1"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Respirology Case Reports"],"published-print":{"date-parts":[[2026,3]]},"abstract":"<jats:title>ABSTRACT<\/jats:title>\n                  <jats:p>Pleuroparenchymal fibroelastosis (PPFE) is a rare fibrosing interstitial lung disease that has been increasingly reported as a secondary condition following various underlying disorders including organ transplantation. However, reports on PPFE associated with inflammatory bowel disease (IBD), such as ulcerative colitis and Crohn's disease, remain extremely limited. We report the case of a 70\u2010year\u2010old man with Crohn's disease who developed slowly progressive upper\u2010lobe\u2010predominant lung lesions. Based on the clinical course, including the development of platythorax and pneumomediastinum, as well as the characteristic pulmonary function impairment and radiological findings, the patient was clinically diagnosed with PPFE. PPFE secondary to Crohn's disease is exceedingly rare, and this case is valuable in that longitudinal radiological progression could be followed in detail. This case highlights the importance of recognising PPFE as a pulmonary complication of Crohn's disease and underscores the value of careful longitudinal assessment using serial imaging and pulmonary function tests.<\/jats:p>","DOI":"10.1002\/rcr2.70555","type":"journal-article","created":{"date-parts":[[2026,3,12]],"date-time":"2026-03-12T00:13:43Z","timestamp":1773274423000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Long\u2010Term Follow\u2010Up of Pleuroparenchymal Fibroelastosis Associated With Crohn's Disease"],"prefix":"10.1002","volume":"14","author":[{"given":"Yuhei","family":"Suzuki","sequence":"first","affiliation":[{"name":"Department of Respiratory Medicine, Graduate School of Medicine The University of Tokyo  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7053-2841","authenticated-orcid":false,"given":"Hiroaki","family":"Ikushima","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine, Graduate School of Medicine The University of Tokyo  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yutaro","family":"Ueki","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine, Graduate School of Medicine The University of Tokyo  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Takashi","family":"Maeda","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine, Graduate School of Medicine The University of Tokyo  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Keiichiro","family":"Hida","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine, Graduate School of Medicine The University of Tokyo  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0009-0008-2649-4105","authenticated-orcid":false,"given":"Keishi","family":"Yoshida","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine, Graduate School of Medicine The University of Tokyo  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2746-9189","authenticated-orcid":false,"given":"Chihiro","family":"Takeuchi","sequence":"additional","affiliation":[{"name":"Department of Gastroenterology, Graduate School of Medicine The University of Tokyo  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hirokazu","family":"Urushiyama","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine, Graduate School of Medicine The University of Tokyo  Tokyo 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Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3658-4442","authenticated-orcid":false,"given":"Hidenori","family":"Kage","sequence":"additional","affiliation":[{"name":"Department of Respiratory Medicine, Graduate School of Medicine The University of Tokyo  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2026,3,11]]},"reference":[{"issue":"12","key":"e_1_2_9_2_1","article-title":"Pleuroparenchymal Fibroelastosis Associated With Crohn's Disease: A New Aetiology?","volume":"7","author":"Amado C.","year":"2020","journal-title":"European Journal of Case Reports in Internal Medicine"},{"issue":"4","key":"e_1_2_9_3_1","first-page":"196","article-title":"A Case of Pleuroparenchymal Fibroelastosis Associated With Crohn's Disease","volume":"12","author":"Nitta Y.","year":"2023","journal-title":"Journal of the Japanese Respiratory 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