{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,30]],"date-time":"2025-07-30T10:10:10Z","timestamp":1753870210272,"version":"3.41.2"},"reference-count":12,"publisher":"Oxford University Press (OUP)","issue":"3","license":[{"start":{"date-parts":[[2024,10,12]],"date-time":"2024-10-12T00:00:00Z","timestamp":1728691200000},"content-version":"vor","delay-in-days":663,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"funder":[{"name":"This article received no specific grant from any funding agency in the public, commercial, or not-for-profit sectors."}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2023,6,1]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>We present a series of five cases who presented to our institution with treatment-refractory mucosal ulceration, all of whom were subsequently diagnosed with paraneoplastic pemphigus (PNP). This case series highlights the diagnostic and treatment considerations for PNP \u2013 in particular, the steroid-dependent, recalcitrant, polymorphic manifestations; the combination of histopathological and clinical findings that may overlap with clinically similar diseases, for example, pemphigus vulgaris and lichen planus; the importance of immunopathological findings for its diagnosis, and the need for surveillance and management of life-threatening bronchiolitis obliterans.<\/jats:p>","DOI":"10.1002\/ski2.200","type":"journal-article","created":{"date-parts":[[2022,12,20]],"date-time":"2022-12-20T07:46:54Z","timestamp":1671522414000},"source":"Crossref","is-referenced-by-count":3,"title":["Paraneoplastic Pemphigus: Diagnostic Mimics, Confounders and Management Challenges in a Series of Five Long-Term Survivors from a Single Centre"],"prefix":"10.1093","volume":"3","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-9359-3834","authenticated-orcid":false,"given":"Jonathan S.","family":"Emerson","sequence":"first","affiliation":[{"name":"Department of Clinical Immunology and Immunopathology, Westmead Hospital , Sydney, New South Wales ,","place":["Australia"]},{"name":"Sydney Medical School, University of Sydney , Camperdown, New South Wales ,","place":["Australia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mark","family":"Schifter","sequence":"additional","affiliation":[{"name":"Department of Oral Medicine, Oral Pathology and Special Needs Dentistry, Westmead Centre for Oral Health, Westmead Hospital , Sydney, New South Wales ,","place":["Australia"]},{"name":"Sydney Dental School, Faculty of Medicine and Health, The University of Sydney , Sydney, New South Wales ,","place":["Australia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pei","family":"Dai","sequence":"additional","affiliation":[{"name":"Department of Clinical Immunology and Immunopathology, Westmead Hospital , Sydney, New South Wales 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Oral Health, Westmead Hospital , Sydney, New South Wales ,","place":["Australia"]},{"name":"Sydney Dental School, Faculty of Medicine and Health, The University of Sydney , Sydney, New South Wales ,","place":["Australia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kenelm","family":"Kwong","sequence":"additional","affiliation":[{"name":"Department of Oral Medicine, Oral Pathology and Special Needs Dentistry, Westmead Centre for Oral Health, Westmead Hospital , Sydney, New South Wales ,","place":["Australia"]},{"name":"Sydney Dental School, Faculty of Medicine and Health, The University of Sydney , Sydney, New South Wales ,","place":["Australia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hadleigh","family":"Clark","sequence":"additional","affiliation":[{"name":"Department of Oral Medicine, Oral Pathology and Special Needs Dentistry, Westmead Centre for Oral Health, Westmead Hospital , Sydney, New South Wales ,","place":["Australia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Suzanne","family":"Cullican","sequence":"additional","affiliation":[{"name":"Department of Clinical Immunology and Immunopathology, Westmead Hospital , Sydney, New South Wales ,","place":["Australia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"David","family":"Campbell","sequence":"additional","affiliation":[{"name":"Department of Clinical Immunology and Immunopathology, Westmead Hospital , Sydney, New South Wales ,","place":["Australia"]}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ming-Wei","family":"Lin","sequence":"additional","affiliation":[{"name":"Department of Clinical Immunology and Immunopathology, Westmead Hospital , Sydney, New South Wales ,","place":["Australia"]},{"name":"Sydney Medical School, University of Sydney , Camperdown, New South Wales ,","place":["Australia"]}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2022,12,19]]},"reference":[{"issue":"18","key":"2025010818112963400_ski2200-bib-0001","doi-asserted-by":"publisher","first-page":"1406","DOI":"10.1056\/nejm199905063401805","article-title":"The mechanism of respiratory failure in paraneoplastic pemphigus","volume":"340","author":"Nousari","year":"1999","journal-title":"N Engl J Med"},{"issue":"3","key":"2025010818112963400_ski2200-bib-0002","doi-asserted-by":"publisher","first-page":"300","DOI":"10.1111\/1346-8138.12753","article-title":"Paraneoplastic pemphigus: two cases of intra-abdominal malignancy presenting solely as treatment refractory oral ulceration","volume":"42","author":"Kelly","year":"2015","journal-title":"J 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