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We report a family in which four successive offspring exhibited a previously undescribed combination of congenital lethal renal disorders: bilateral renal dysplasia, megalocystis secondary to urethral obstruction and, sirenomelia with associated renal agenesis. \u00a9 1993 Wiley\u2010Liss, Inc.<\/jats:p>","DOI":"10.1002\/tera.1420470111","type":"journal-article","created":{"date-parts":[[2005,6,11]],"date-time":"2005-06-11T15:54:12Z","timestamp":1118505252000},"page":"65-71","source":"Crossref","is-referenced-by-count":19,"title":["Renal dysplasia, megalocystis, and sirenomelia in four siblings"],"prefix":"10.1002","volume":"47","author":[{"given":"Abby M.","family":"Selig","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Beryl","family":"Benacerraf","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Michael F.","family":"Greene","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mary\u2010Frances","family":"Garber","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David R.","family":"Genest","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2005,6,2]]},"reference":[{"key":"e_1_2_1_2_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3476(84)80481-3"},{"key":"e_1_2_1_3_1","first-page":"11","article-title":"Famililial renal agenesis and hereditary renal adysplasia","volume":"115","author":"Buchta R. 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