{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,14]],"date-time":"2025-10-14T06:44:47Z","timestamp":1760424287191},"reference-count":60,"publisher":"Elsevier BV","issue":"2","license":[{"start":{"date-parts":[[2000,3,1]],"date-time":"2000-03-01T00:00:00Z","timestamp":951868800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Archives of Biochemistry and Biophysics"],"published-print":{"date-parts":[[2000,3]]},"DOI":"10.1006\/abbi.1999.1641","type":"journal-article","created":{"date-parts":[[2002,10,6]],"date-time":"2002-10-06T18:21:12Z","timestamp":1033928472000},"page":"240-250","source":"Crossref","is-referenced-by-count":9,"title":["Spontaneous Porphyria of the Long\u2013Evans Cinnamon Rat: An Animal Model of Wilson's Disease"],"prefix":"10.1006","volume":"375","author":[{"given":"Kenji","family":"Nakayama","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Akira","family":"Takasawa","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Itaru","family":"Terai","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Toyo","family":"Okui","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tohru","family":"Ohyama","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mamoru","family":"Tamura","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"78","reference":[{"key":"10.1006\/abbi.1999.1641_RF1","doi-asserted-by":"crossref","first-page":"1615","DOI":"10.1016\/S0016-5085(19)30524-4","volume":"78","author":"Sternlieb","year":"1980","journal-title":"Gastroenterol"},{"key":"10.1006\/abbi.1999.1641_RF2","doi-asserted-by":"crossref","first-page":"165","DOI":"10.1016\/B978-0-12-364931-7.50011-2","volume":"31","author":"Alt","year":"1990","journal-title":"Int. Rev. Exp. Pathol."},{"key":"10.1006\/abbi.1999.1641_RF3","doi-asserted-by":"crossref","first-page":"142","DOI":"10.1007\/BF01963553","volume":"150","author":"Danks","year":"1991","journal-title":"Eur. J. Pediatr."},{"key":"10.1006\/abbi.1999.1641_RF4","first-page":"323","volume":"43","author":"Cuthbert","year":"1995","journal-title":"J. Invest. Med."},{"key":"10.1006\/abbi.1999.1641_RF5","doi-asserted-by":"crossref","first-page":"842S","DOI":"10.1093\/ajcn\/63.5.842","volume":"63","author":"Scheinberg","year":"1996","journal-title":"Am. J. Clin. Nutr."},{"key":"10.1006\/abbi.1999.1641_RF6","doi-asserted-by":"crossref","first-page":"327","DOI":"10.1038\/ng1293-327","volume":"5","author":"Bull","year":"1993","journal-title":"Nat. Genet."},{"key":"10.1006\/abbi.1999.1641_RF7","doi-asserted-by":"crossref","first-page":"338","DOI":"10.1038\/ng1293-338","volume":"5","author":"Petrukhin","year":"1993","journal-title":"Nat. Genet."},{"key":"10.1006\/abbi.1999.1641_RF8","doi-asserted-by":"crossref","first-page":"344","DOI":"10.1038\/ng1293-344","volume":"5","author":"Tanzi","year":"1993","journal-title":"Nat. Genet."},{"key":"10.1006\/abbi.1999.1641_RF9","doi-asserted-by":"crossref","first-page":"1858","DOI":"10.1172\/JCI115208","volume":"87","author":"Li","year":"1991","journal-title":"J. Clin. Invest."},{"key":"10.1006\/abbi.1999.1641_RF10","series-title":"The LEC Rats","first-page":"122","author":"Li","year":"1991"},{"key":"10.1006\/abbi.1999.1641_RF11","doi-asserted-by":"crossref","first-page":"512","DOI":"10.1006\/bbrc.1994.1958","volume":"202","author":"Sasaki","year":"1994","journal-title":"Biochem. Biophys. Res. Commun."},{"key":"10.1006\/abbi.1999.1641_RF12","doi-asserted-by":"crossref","first-page":"541","DOI":"10.1038\/ng0894-541","volume":"7","author":"Wu","year":"1994","journal-title":"Nat. Genet."},{"key":"10.1006\/abbi.1999.1641_RF13","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1042\/bj3010001","volume":"301","author":"Yamaguchi","year":"1994","journal-title":"Biochem. J."},{"key":"10.1006\/abbi.1999.1641_RF14","doi-asserted-by":"crossref","first-page":"253","DOI":"10.1203\/00006450-199203000-00011","volume":"31","author":"Okayasu","year":"1992","journal-title":"Pediatr. Res."},{"key":"10.1006\/abbi.1999.1641_RF15","doi-asserted-by":"crossref","first-page":"598","DOI":"10.1203\/00006450-199405000-00012","volume":"35","author":"Suzuki","year":"1994","journal-title":"Pediatr. Res."},{"key":"10.1006\/abbi.1999.1641_RF16","first-page":"221","volume":"89","author":"Suzuki","year":"1995","journal-title":"Res. Commun. Mol. Pathol. Pharmacol."},{"key":"10.1006\/abbi.1999.1641_RF17","doi-asserted-by":"crossref","unstructured":"Ono, T., Abe, S., and Yoshida, M. C.1991inThe LEC Rats (Mori, M., Yoshida, M. C., Takeichi, N., and Taniguchi, N., Eds.), pp. 133\u2013141, Springer-Verlag, Tokyo.","DOI":"10.1007\/978-4-431-68153-3_14"},{"key":"10.1006\/abbi.1999.1641_RF18","doi-asserted-by":"crossref","first-page":"219","DOI":"10.1111\/j.1349-7006.1993.tb02859.x","volume":"84","author":"Kato","year":"1993","journal-title":"Jpn. J. Cancer Res."},{"key":"10.1006\/abbi.1999.1641_RF19","doi-asserted-by":"crossref","first-page":"923","DOI":"10.1172\/JCI118875","volume":"98","author":"Kato","year":"1996","journal-title":"J. Clin. Invest."},{"key":"10.1006\/abbi.1999.1641_RF20","doi-asserted-by":"crossref","first-page":"170","DOI":"10.1111\/j.1753-4887.1995.tb01545.x","volume":"53","author":"Harris","year":"1995","journal-title":"Nutr. Rev."},{"key":"10.1006\/abbi.1999.1641_RF21","doi-asserted-by":"crossref","first-page":"441","DOI":"10.3109\/10715769809066881","volume":"28","author":"Koizumi","year":"1998","journal-title":"Free Radical Res."},{"key":"10.1006\/abbi.1999.1641_RF22","first-page":"200","volume":"144","author":"Mori","year":"1994","journal-title":"Am. J. Pathol."},{"key":"10.1006\/abbi.1999.1641_RF23","doi-asserted-by":"crossref","first-page":"164","DOI":"10.1006\/bbrc.1997.7900","volume":"242","author":"Nakayama","year":"1998","journal-title":"Biochem. Biophys. Res. Commun."},{"key":"10.1006\/abbi.1999.1641_RF24","doi-asserted-by":"crossref","first-page":"865","DOI":"10.1177\/44.8.8756759","volume":"44","author":"Okabe","year":"1996","journal-title":"J. Histochem. Cytochem."},{"key":"10.1006\/abbi.1999.1641_RF25","doi-asserted-by":"crossref","first-page":"1393","DOI":"10.1016\/S0006-291X(05)80037-3","volume":"184","author":"Sakurai","year":"1992","journal-title":"Biochem. Biophys. Res. Commun."},{"key":"10.1006\/abbi.1999.1641_RF26","doi-asserted-by":"crossref","first-page":"548","DOI":"10.1016\/0006-291X(92)91659-E","volume":"185","author":"Sakurai","year":"1992","journal-title":"Biochem. Biophys. Res. Commun."},{"key":"10.1006\/abbi.1999.1641_RF27","doi-asserted-by":"crossref","first-page":"1060","DOI":"10.1007\/BF01923342","volume":"47","author":"Sugawara","year":"1991","journal-title":"Experientia"},{"key":"10.1006\/abbi.1999.1641_RF28","first-page":"353","volume":"72","author":"Sugawara","year":"1991","journal-title":"Res. Commun. Chem. Pathol. Pharmacol."},{"key":"10.1006\/abbi.1999.1641_RF29","doi-asserted-by":"crossref","first-page":"321","DOI":"10.1111\/j.1600-0773.1992.tb00554.x","volume":"71","author":"Sugawara","year":"1992","journal-title":"Pharmacol. Toxicol."},{"key":"10.1006\/abbi.1999.1641_RF30","series-title":"The LEC Rats","first-page":"11","author":"Kasai","year":"1991"},{"key":"10.1006\/abbi.1999.1641_RF31","doi-asserted-by":"crossref","first-page":"302","DOI":"10.1046\/j.1365-2362.1998.00292.x","volume":"28","author":"Klein","year":"1998","journal-title":"Eur. J. Clin. Invest."},{"key":"10.1006\/abbi.1999.1641_RF32","series-title":"The LEC Rats","first-page":"20","author":"Yamazaki","year":"1991"},{"key":"10.1006\/abbi.1999.1641_RF33","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/0003-2697(86)90187-9","volume":"157","author":"Kennedy","year":"1986","journal-title":"Anal. Biochem."},{"key":"10.1006\/abbi.1999.1641_RF34","doi-asserted-by":"crossref","first-page":"1508","DOI":"10.1093\/clinchem\/35.7.1508","volume":"35","author":"Perkins","year":"1989","journal-title":"Clin. Chem."},{"key":"10.1006\/abbi.1999.1641_RF35","doi-asserted-by":"crossref","first-page":"127","DOI":"10.1016\/0378-4347(93)80455-D","volume":"619","author":"Kennedy","year":"1993","journal-title":"J. Chromatogr."},{"key":"10.1006\/abbi.1999.1641_RF36","doi-asserted-by":"crossref","first-page":"464","DOI":"10.1016\/0041-008X(91)90047-I","volume":"110","author":"Woods","year":"1991","journal-title":"Toxicol. Appl. Pharmacol."},{"key":"10.1006\/abbi.1999.1641_RF37","doi-asserted-by":"crossref","first-page":"397","DOI":"10.1093\/clinchem\/27.3.397","volume":"27","author":"Ford","year":"1981","journal-title":"Clin. Chem."},{"key":"10.1006\/abbi.1999.1641_RF38","series-title":"The Porphyrins, III","first-page":"1","author":"Gouterman","year":"1978"},{"key":"10.1006\/abbi.1999.1641_RF39","doi-asserted-by":"crossref","first-page":"229","DOI":"10.1001\/archinte.1966.00290150043009","volume":"118","author":"Zimmerman","year":"1966","journal-title":"Arch. Intern. Med."},{"key":"10.1006\/abbi.1999.1641_RF40","doi-asserted-by":"crossref","first-page":"422","DOI":"10.1007\/BF01705507","volume":"14","author":"Grant","year":"1975","journal-title":"Bull. Environ. Contam. Toxicol."},{"key":"10.1006\/abbi.1999.1641_RF41","doi-asserted-by":"crossref","first-page":"3543","DOI":"10.1016\/0006-2952(82)90573-1","volume":"31","author":"Rizzardini","year":"1982","journal-title":"Biochem. Pharmacol."},{"key":"10.1006\/abbi.1999.1641_RF42","doi-asserted-by":"crossref","first-page":"631","DOI":"10.1093\/carcin\/6.4.631","volume":"6","author":"Smith","year":"1985","journal-title":"Carinogenesis"},{"key":"10.1006\/abbi.1999.1641_RF43","doi-asserted-by":"crossref","first-page":"433","DOI":"10.1016\/0272-0590(91)90194-9","volume":"17","author":"Krishnan","year":"1991","journal-title":"Fundam. Appl. Toxicol."},{"key":"10.1006\/abbi.1999.1641_RF44","doi-asserted-by":"crossref","first-page":"23","DOI":"10.1006\/taap.1997.8157","volume":"145","author":"Mylchreest","year":"1997","journal-title":"Toxicol. Appl. Pharmacol."},{"key":"10.1006\/abbi.1999.1641_RF45","doi-asserted-by":"crossref","first-page":"90","DOI":"10.1159\/000181958","volume":"26","author":"Day","year":"1980","journal-title":"Nephron"},{"key":"10.1006\/abbi.1999.1641_RF46","doi-asserted-by":"crossref","first-page":"22","DOI":"10.1159\/000182426","volume":"30","author":"Day","year":"1982","journal-title":"Nephron"},{"key":"10.1006\/abbi.1999.1641_RF47","doi-asserted-by":"crossref","first-page":"287","DOI":"10.1016\/0006-8993(92)91587-5","volume":"588","author":"Sugawara","year":"1992","journal-title":"Brain Res."},{"key":"10.1006\/abbi.1999.1641_RF48","doi-asserted-by":"crossref","first-page":"97","DOI":"10.1016\/0304-3940(94)90614-9","volume":"171","author":"Sato","year":"1994","journal-title":"Neurosci. Lett."},{"key":"10.1006\/abbi.1999.1641_RF49","doi-asserted-by":"crossref","first-page":"240","DOI":"10.1016\/0006-8993(95)00819-C","volume":"695","author":"Saito","year":"1995","journal-title":"Brain Res."},{"key":"10.1006\/abbi.1999.1641_RF50","first-page":"195","volume":"216","author":"Saito","year":"1996","journal-title":"Neurosci. Lett."},{"key":"10.1006\/abbi.1999.1641_RF51","doi-asserted-by":"crossref","first-page":"383","DOI":"10.1073\/pnas.68.2.383","volume":"68","author":"Feldman","year":"1971","journal-title":"Proc. Natl. Acad. Sci. USA"},{"key":"10.1006\/abbi.1999.1641_RF52","first-page":"94","volume":"5","author":"Bornstein","year":"1979","journal-title":"Neurology"},{"key":"10.1006\/abbi.1999.1641_RF53","doi-asserted-by":"crossref","first-page":"26","DOI":"10.1016\/0005-2736(71)90280-X","volume":"225","author":"Becker","year":"1971","journal-title":"Biochim. Biophys. Acta"},{"key":"10.1006\/abbi.1999.1641_RF54","doi-asserted-by":"crossref","first-page":"521","DOI":"10.1016\/0024-3205(76)90231-9","volume":"19","author":"Nicoll","year":"1976","journal-title":"Life Sci."},{"key":"10.1006\/abbi.1999.1641_RF55","doi-asserted-by":"crossref","first-page":"189","DOI":"10.1016\/0006-8993(77)90229-3","volume":"126","author":"Dichter","year":"1977","journal-title":"Brain Res."},{"key":"10.1006\/abbi.1999.1641_RF56","doi-asserted-by":"crossref","first-page":"1019","DOI":"10.1111\/j.1471-4159.1974.tb10754.x","volume":"23","author":"Becker","year":"1974","journal-title":"J. Neurochem."},{"key":"10.1006\/abbi.1999.1641_RF57","doi-asserted-by":"crossref","first-page":"1009","DOI":"10.1007\/BF00965140","volume":"7","author":"Russell","year":"1982","journal-title":"Neurochem. Res."},{"key":"10.1006\/abbi.1999.1641_RF58","doi-asserted-by":"crossref","first-page":"340","DOI":"10.1002\/ana.410020415","volume":"2","author":"M\u00fcller","year":"1977","journal-title":"Ann. Neurol."},{"key":"10.1006\/abbi.1999.1641_RF59","doi-asserted-by":"crossref","first-page":"1407","DOI":"10.1007\/BF00964997","volume":"8","author":"Russell","year":"1983","journal-title":"Neurochem. Res."},{"key":"10.1006\/abbi.1999.1641_RF60","first-page":"143","volume":"111C","author":"Juknat","year":"1995","journal-title":"Comp. Biochem. Physiol."}],"container-title":["Archives of Biochemistry and Biophysics"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0003986199916417?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0003986199916417?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2021,5,3]],"date-time":"2021-05-03T05:52:28Z","timestamp":1620021148000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0003986199916417"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2000,3]]},"references-count":60,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2000,3]]}},"alternative-id":["S0003986199916417"],"URL":"https:\/\/doi.org\/10.1006\/abbi.1999.1641","relation":{},"ISSN":["0003-9861"],"issn-type":[{"value":"0003-9861","type":"print"}],"subject":[],"published":{"date-parts":[[2000,3]]}}}